Scimitar syndrome: A case report
Scimitar syndrome is a rare vascular malformation characterized by partial or total abnormal flow of the right pulmonary vein into the inferior vena cava, located above or below the diaphragm. Scimitar syndrome is a rare disease has an incidence of approximately 1-3 per 100,000 live births. And it c...
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| Language: | English |
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Elsevier
2025-04-01
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| Series: | Radiology Case Reports |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1930043325000688 |
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| author | Xiang Zhao Junyang Huang Junke Yang Bingkui Cen |
| author_facet | Xiang Zhao Junyang Huang Junke Yang Bingkui Cen |
| author_sort | Xiang Zhao |
| collection | DOAJ |
| description | Scimitar syndrome is a rare vascular malformation characterized by partial or total abnormal flow of the right pulmonary vein into the inferior vena cava, located above or below the diaphragm. Scimitar syndrome is a rare disease has an incidence of approximately 1-3 per 100,000 live births. And it can be divided into infantile type and child/adult type. Infantile patients have more deformities and poor prognosis, so it is urgent to combine multidisciplinary early precision diagnosis and treatment. Most children with childhood/adult forms are asymptomatic or have mild symptoms and can live normally without medical intervention. Here we report a case of a 3 year, 8-month-old girl who was diagnosed with Scimitar syndrome in our hospital. By presenting multiplanar CT images of malformed drainage veins in this patient's lungs and analyzing a series of cardiopulmonary abnormalities resulting from them, we have demonstrated in detail the diagnostic process of this rare disease, Scimitar syndrome. For patients with Scimitar syndrome, whether to take surgical treatment should be determined according to the specific cardiopulmonary function of patients, mild patients can take regular follow-up strategy. For patients with obvious clinical symptoms, surgery can significantly improve the long-term prognosis. |
| format | Article |
| id | doaj-art-386215b1d63e4746bcf00be16bdac994 |
| institution | Kabale University |
| issn | 1930-0433 |
| language | English |
| publishDate | 2025-04-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Radiology Case Reports |
| spelling | doaj-art-386215b1d63e4746bcf00be16bdac9942025-02-06T05:11:29ZengElsevierRadiology Case Reports1930-04332025-04-0120422222226Scimitar syndrome: A case reportXiang Zhao0Junyang Huang1Junke Yang2Bingkui Cen3Corresponding author.; Department of Radiology, Baise People's Hospital, Guangxi, ChinaDepartment of Radiology, Baise People's Hospital, Guangxi, ChinaDepartment of Radiology, Baise People's Hospital, Guangxi, ChinaDepartment of Radiology, Baise People's Hospital, Guangxi, ChinaScimitar syndrome is a rare vascular malformation characterized by partial or total abnormal flow of the right pulmonary vein into the inferior vena cava, located above or below the diaphragm. Scimitar syndrome is a rare disease has an incidence of approximately 1-3 per 100,000 live births. And it can be divided into infantile type and child/adult type. Infantile patients have more deformities and poor prognosis, so it is urgent to combine multidisciplinary early precision diagnosis and treatment. Most children with childhood/adult forms are asymptomatic or have mild symptoms and can live normally without medical intervention. Here we report a case of a 3 year, 8-month-old girl who was diagnosed with Scimitar syndrome in our hospital. By presenting multiplanar CT images of malformed drainage veins in this patient's lungs and analyzing a series of cardiopulmonary abnormalities resulting from them, we have demonstrated in detail the diagnostic process of this rare disease, Scimitar syndrome. For patients with Scimitar syndrome, whether to take surgical treatment should be determined according to the specific cardiopulmonary function of patients, mild patients can take regular follow-up strategy. For patients with obvious clinical symptoms, surgery can significantly improve the long-term prognosis.http://www.sciencedirect.com/science/article/pii/S1930043325000688Scimitar syndromeVascular malformationComputed tomographyAngiography |
| spellingShingle | Xiang Zhao Junyang Huang Junke Yang Bingkui Cen Scimitar syndrome: A case report Radiology Case Reports Scimitar syndrome Vascular malformation Computed tomography Angiography |
| title | Scimitar syndrome: A case report |
| title_full | Scimitar syndrome: A case report |
| title_fullStr | Scimitar syndrome: A case report |
| title_full_unstemmed | Scimitar syndrome: A case report |
| title_short | Scimitar syndrome: A case report |
| title_sort | scimitar syndrome a case report |
| topic | Scimitar syndrome Vascular malformation Computed tomography Angiography |
| url | http://www.sciencedirect.com/science/article/pii/S1930043325000688 |
| work_keys_str_mv | AT xiangzhao scimitarsyndromeacasereport AT junyanghuang scimitarsyndromeacasereport AT junkeyang scimitarsyndromeacasereport AT bingkuicen scimitarsyndromeacasereport |