Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology

Abstract Lung development begins during week 4 of pregnancy and continues through fetal development until early infancy. Various malformations can develop during the fetal period. There is histology overlap in several of them and partly joint etiology has been suggested as the cause of malformation....

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Main Authors: Susanna Nuutinen, Elisa Lappi-Blanco, Eveliina Ronkainen, Teija Dunder, Terttu Harju, Willy Serlo, Jaakko Sinikumpu
Format: Article
Language:English
Published: Nature Portfolio 2025-04-01
Series:Scientific Reports
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Online Access:https://doi.org/10.1038/s41598-025-98743-0
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author Susanna Nuutinen
Elisa Lappi-Blanco
Eveliina Ronkainen
Teija Dunder
Terttu Harju
Willy Serlo
Jaakko Sinikumpu
author_facet Susanna Nuutinen
Elisa Lappi-Blanco
Eveliina Ronkainen
Teija Dunder
Terttu Harju
Willy Serlo
Jaakko Sinikumpu
author_sort Susanna Nuutinen
collection DOAJ
description Abstract Lung development begins during week 4 of pregnancy and continues through fetal development until early infancy. Various malformations can develop during the fetal period. There is histology overlap in several of them and partly joint etiology has been suggested as the cause of malformation. Early surgery has been supported after the diagnosis of a local pulmonary malformation due to potential malignancy risk and an increased lung infection risk. However, the evidence supporting surgery for asymptomatic patients is scarce. This comprehensive single-center study in a tertiary children’s hospital included all 45 surgically treated patients at any age between 1986 and 2015. The study population consisted of 45 patients. Histology, preoperative symptoms, and radiological and operative findings were systematically reevaluated. Small cyst type congenital pulmonary airway malformation (CPAM) was the most common type of detected congenital lung malformation. There were no malignant or premalignant findings. Of all the patients, 23 (48.9%) were asymptomatic at the time of surgery. However, histology showed that four out of them (18%) had ongoing inflammation. Overall, one third of patients (n = 15, 34%) presented to have inflammation histologically. While chronic inflammation results in alveolar fibrosis, a high reported inflammation rate (34%) supports early malformation excision, regardless of the symptoms.
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spelling doaj-art-383281d24a204a26b2cf8d9d9d3cf7b52025-08-20T03:13:57ZengNature PortfolioScientific Reports2045-23222025-04-011511610.1038/s41598-025-98743-0Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatologySusanna Nuutinen0Elisa Lappi-Blanco1Eveliina Ronkainen2Teija Dunder3Terttu Harju4Willy Serlo5Jaakko Sinikumpu6Research Unit of Clinical Medicine, University of OuluDepartment of Pathology, Oulu University HospitalResearch Unit of Clinical Medicine, University of OuluResearch Unit of Clinical Medicine, University of OuluMedical Research Center, Oulu University HospitalResearch Unit of Clinical Medicine, University of OuluResearch Unit of Clinical Medicine, University of OuluAbstract Lung development begins during week 4 of pregnancy and continues through fetal development until early infancy. Various malformations can develop during the fetal period. There is histology overlap in several of them and partly joint etiology has been suggested as the cause of malformation. Early surgery has been supported after the diagnosis of a local pulmonary malformation due to potential malignancy risk and an increased lung infection risk. However, the evidence supporting surgery for asymptomatic patients is scarce. This comprehensive single-center study in a tertiary children’s hospital included all 45 surgically treated patients at any age between 1986 and 2015. The study population consisted of 45 patients. Histology, preoperative symptoms, and radiological and operative findings were systematically reevaluated. Small cyst type congenital pulmonary airway malformation (CPAM) was the most common type of detected congenital lung malformation. There were no malignant or premalignant findings. Of all the patients, 23 (48.9%) were asymptomatic at the time of surgery. However, histology showed that four out of them (18%) had ongoing inflammation. Overall, one third of patients (n = 15, 34%) presented to have inflammation histologically. While chronic inflammation results in alveolar fibrosis, a high reported inflammation rate (34%) supports early malformation excision, regardless of the symptoms.https://doi.org/10.1038/s41598-025-98743-0CongenitalSurgeryPulmonary malformation
spellingShingle Susanna Nuutinen
Elisa Lappi-Blanco
Eveliina Ronkainen
Teija Dunder
Terttu Harju
Willy Serlo
Jaakko Sinikumpu
Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology
Scientific Reports
Congenital
Surgery
Pulmonary malformation
title Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology
title_full Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology
title_fullStr Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology
title_full_unstemmed Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology
title_short Characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology
title_sort characterization of 45 cases of congenital lung malformation and association of inflammation with symptomatology
topic Congenital
Surgery
Pulmonary malformation
url https://doi.org/10.1038/s41598-025-98743-0
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