A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature Review

A 22-year-old female presented with back pain and was discovered to have a right-sided abdominal mass. Computed tomography (CT) scan revealed a 9 cm enhancing right upper pole renal mass with suspicion for tumor thrombus into the right renal vein and possibly the inferior vena cava (IVC). Magnetic r...

Full description

Saved in:
Bibliographic Details
Main Authors: Campbell Grant, John M. Lacy, Stephen E. Strup
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Case Reports in Urology
Online Access:http://dx.doi.org/10.1155/2013/730369
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850217708734382080
author Campbell Grant
John M. Lacy
Stephen E. Strup
author_facet Campbell Grant
John M. Lacy
Stephen E. Strup
author_sort Campbell Grant
collection DOAJ
description A 22-year-old female presented with back pain and was discovered to have a right-sided abdominal mass. Computed tomography (CT) scan revealed a 9 cm enhancing right upper pole renal mass with suspicion for tumor thrombus into the right renal vein and possibly the inferior vena cava (IVC). Magnetic resonance imaging (MRI) confirmed tumor thrombus into the inferior vena cava approximately 3 cm below the hepatic venous confluence. Open right radical nephrectomy with inferior vena cava thrombectomy was performed with removal of right kidney and tumor thrombus en bloc. Pathology revealed malignant epithelioid angiomyolipoma (EAML or PEComa). Epithelioid angiomyolipoma is a rare tumor of mesenchymal tissue that has the potential for local invasion and disease progression. Diagnosis of EAML was confirmed by pathology and immunohistochemistry. She was referred to medical oncology for discussion of surveillance versus potential adjuvant therapy and ultimately opted for close surveillance.
format Article
id doaj-art-382b056fd88c48e5831a892d6ba03280
institution OA Journals
issn 2090-696X
2090-6978
language English
publishDate 2013-01-01
publisher Wiley
record_format Article
series Case Reports in Urology
spelling doaj-art-382b056fd88c48e5831a892d6ba032802025-08-20T02:07:59ZengWileyCase Reports in Urology2090-696X2090-69782013-01-01201310.1155/2013/730369730369A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature ReviewCampbell Grant0John M. Lacy1Stephen E. Strup2University of Kentucky College of Medicine, Lexington, KY 40536, USADivision of Urology, Department of Surgery, University of Kentucky College of Medicine, Lexington, KY 40536, USADivision of Urology, Department of Surgery, University of Kentucky College of Medicine, Lexington, KY 40536, USAA 22-year-old female presented with back pain and was discovered to have a right-sided abdominal mass. Computed tomography (CT) scan revealed a 9 cm enhancing right upper pole renal mass with suspicion for tumor thrombus into the right renal vein and possibly the inferior vena cava (IVC). Magnetic resonance imaging (MRI) confirmed tumor thrombus into the inferior vena cava approximately 3 cm below the hepatic venous confluence. Open right radical nephrectomy with inferior vena cava thrombectomy was performed with removal of right kidney and tumor thrombus en bloc. Pathology revealed malignant epithelioid angiomyolipoma (EAML or PEComa). Epithelioid angiomyolipoma is a rare tumor of mesenchymal tissue that has the potential for local invasion and disease progression. Diagnosis of EAML was confirmed by pathology and immunohistochemistry. She was referred to medical oncology for discussion of surveillance versus potential adjuvant therapy and ultimately opted for close surveillance.http://dx.doi.org/10.1155/2013/730369
spellingShingle Campbell Grant
John M. Lacy
Stephen E. Strup
A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature Review
Case Reports in Urology
title A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature Review
title_full A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature Review
title_fullStr A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature Review
title_full_unstemmed A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature Review
title_short A 22-Year-Old Female with Invasive Epithelioid Angiomyolipoma and Tumor Thrombus into the Inferior Vena Cava: Case Report and Literature Review
title_sort 22 year old female with invasive epithelioid angiomyolipoma and tumor thrombus into the inferior vena cava case report and literature review
url http://dx.doi.org/10.1155/2013/730369
work_keys_str_mv AT campbellgrant a22yearoldfemalewithinvasiveepithelioidangiomyolipomaandtumorthrombusintotheinferiorvenacavacasereportandliteraturereview
AT johnmlacy a22yearoldfemalewithinvasiveepithelioidangiomyolipomaandtumorthrombusintotheinferiorvenacavacasereportandliteraturereview
AT stephenestrup a22yearoldfemalewithinvasiveepithelioidangiomyolipomaandtumorthrombusintotheinferiorvenacavacasereportandliteraturereview
AT campbellgrant 22yearoldfemalewithinvasiveepithelioidangiomyolipomaandtumorthrombusintotheinferiorvenacavacasereportandliteraturereview
AT johnmlacy 22yearoldfemalewithinvasiveepithelioidangiomyolipomaandtumorthrombusintotheinferiorvenacavacasereportandliteraturereview
AT stephenestrup 22yearoldfemalewithinvasiveepithelioidangiomyolipomaandtumorthrombusintotheinferiorvenacavacasereportandliteraturereview