Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case report

Abstract Neuromyelitis optica spectrum disorder (NMOSD) is a group of autoimmune disorders characterized by inflammatory involvement of the optic nerve, spinal cord, and central nervous system. NMOSD is often associated with other autoimmune disorders, including Sjogren's syndrome (SS). While N...

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Main Authors: Man‐Min Zhu, Zu‐Cai Xu, Chang‐Yin Yu, Hao Huang
Format: Article
Language:English
Published: Wiley-VCH 2025-06-01
Series:Ibrain
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Online Access:https://doi.org/10.1002/ibra.12175
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author Man‐Min Zhu
Zu‐Cai Xu
Chang‐Yin Yu
Hao Huang
author_facet Man‐Min Zhu
Zu‐Cai Xu
Chang‐Yin Yu
Hao Huang
author_sort Man‐Min Zhu
collection DOAJ
description Abstract Neuromyelitis optica spectrum disorder (NMOSD) is a group of autoimmune disorders characterized by inflammatory involvement of the optic nerve, spinal cord, and central nervous system. NMOSD is often associated with other autoimmune disorders, including Sjogren's syndrome (SS). While NMOSD typically occurs at a peak in young or older individuals, the coexistence of NMOSD and SS in a youngster is rare. Here, we presented a case of a 14‐year‐old girl with NMOSD and SS who responded well to immunosuppressive therapy but experienced a severe relapse after discontinuation of therapy. We described the clinical course of a case over 8 years, underscoring the importance of long‐term treatment for NMOSD and SS. This case, along with the review of relevant literature, will raise awareness of this type of disease and facilitate early diagnosis and treatment to avoid serious sequelae.
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issn 2313-1934
2769-2795
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publishDate 2025-06-01
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series Ibrain
spelling doaj-art-36284746c8c94c8781fa069ce1604c5e2025-08-20T03:31:19ZengWiley-VCHIbrain2313-19342769-27952025-06-0111226827310.1002/ibra.12175Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case reportMan‐Min Zhu0Zu‐Cai Xu1Chang‐Yin Yu2Hao Huang3Department of Neurology Affiliated Hospital of Zunyi Medical University Zunyi ChinaDepartment of Neurology Affiliated Hospital of Zunyi Medical University Zunyi ChinaDepartment of Neurology Affiliated Hospital of Zunyi Medical University Zunyi ChinaDepartment of Neurology Affiliated Hospital of Zunyi Medical University Zunyi ChinaAbstract Neuromyelitis optica spectrum disorder (NMOSD) is a group of autoimmune disorders characterized by inflammatory involvement of the optic nerve, spinal cord, and central nervous system. NMOSD is often associated with other autoimmune disorders, including Sjogren's syndrome (SS). While NMOSD typically occurs at a peak in young or older individuals, the coexistence of NMOSD and SS in a youngster is rare. Here, we presented a case of a 14‐year‐old girl with NMOSD and SS who responded well to immunosuppressive therapy but experienced a severe relapse after discontinuation of therapy. We described the clinical course of a case over 8 years, underscoring the importance of long‐term treatment for NMOSD and SS. This case, along with the review of relevant literature, will raise awareness of this type of disease and facilitate early diagnosis and treatment to avoid serious sequelae.https://doi.org/10.1002/ibra.12175immunosuppressive therapyneuromyelitis optica spectrum disorderrelapse childSjogren's syndrome
spellingShingle Man‐Min Zhu
Zu‐Cai Xu
Chang‐Yin Yu
Hao Huang
Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case report
Ibrain
immunosuppressive therapy
neuromyelitis optica spectrum disorder
relapse child
Sjogren's syndrome
title Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case report
title_full Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case report
title_fullStr Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case report
title_full_unstemmed Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case report
title_short Severe relapse after cessation of immunosuppressive therapy in a patient with co‐occurrence of neuromyelitis optica spectrum disorder and Sjögren's syndrome: A case report
title_sort severe relapse after cessation of immunosuppressive therapy in a patient with co occurrence of neuromyelitis optica spectrum disorder and sjogren s syndrome a case report
topic immunosuppressive therapy
neuromyelitis optica spectrum disorder
relapse child
Sjogren's syndrome
url https://doi.org/10.1002/ibra.12175
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