Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?

Background The Creutzfeldt-Jakob disease (CJD) is a spongiform encephalopathy that manifests as a rapidly progressive dementia syndrome. Currently, CJD has no cure, and many patients die within the first year, but some drugs are being studied as options for managing this condition.

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Main Authors: Luiz Henrique Lélis Miranda, André Felipe Pastick de Holanda Oliveira, Davi Mariano de Carvalho, Gustavo Marques Figueredo Souza, João Guilherme Monteiro Magalhães, Joselmo Alberto Cabral Júnior, Pedro Thadeu Mertens Brainer de Queiroz Lima, Renato Melo Aguiar Júnior, Sérgio Pereira Lins Filho, Hugo Moura de Albuquerque Melo
Format: Article
Language:English
Published: Thieme Revinter Publicações 2022-08-01
Series:Arquivos de Neuro-Psiquiatria
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Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0042-1755341
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author Luiz Henrique Lélis Miranda
André Felipe Pastick de Holanda Oliveira
Davi Mariano de Carvalho
Gustavo Marques Figueredo Souza
João Guilherme Monteiro Magalhães
Joselmo Alberto Cabral Júnior
Pedro Thadeu Mertens Brainer de Queiroz Lima
Renato Melo Aguiar Júnior
Sérgio Pereira Lins Filho
Hugo Moura de Albuquerque Melo
author_facet Luiz Henrique Lélis Miranda
André Felipe Pastick de Holanda Oliveira
Davi Mariano de Carvalho
Gustavo Marques Figueredo Souza
João Guilherme Monteiro Magalhães
Joselmo Alberto Cabral Júnior
Pedro Thadeu Mertens Brainer de Queiroz Lima
Renato Melo Aguiar Júnior
Sérgio Pereira Lins Filho
Hugo Moura de Albuquerque Melo
author_sort Luiz Henrique Lélis Miranda
collection DOAJ
description Background The Creutzfeldt-Jakob disease (CJD) is a spongiform encephalopathy that manifests as a rapidly progressive dementia syndrome. Currently, CJD has no cure, and many patients die within the first year, but some drugs are being studied as options for managing this condition.
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publishDate 2022-08-01
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series Arquivos de Neuro-Psiquiatria
spelling doaj-art-35d2b1d75691499ab6c201e28b4094ee2025-08-20T03:18:41ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria0004-282X1678-42272022-08-01800883784410.1055/s-0042-1755341Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?Luiz Henrique Lélis Miranda0https://orcid.org/0000-0003-0527-2753André Felipe Pastick de Holanda Oliveira1https://orcid.org/0000-0002-0655-6769Davi Mariano de Carvalho2https://orcid.org/0000-0002-9275-4920Gustavo Marques Figueredo Souza3https://orcid.org/0000-0002-2777-2241João Guilherme Monteiro Magalhães4https://orcid.org/0000-0001-7354-3039Joselmo Alberto Cabral Júnior5https://orcid.org/0000-0003-3399-0023Pedro Thadeu Mertens Brainer de Queiroz Lima6https://orcid.org/0000-0003-0819-0155Renato Melo Aguiar Júnior7https://orcid.org/0000-0001-8039-5417Sérgio Pereira Lins Filho8https://orcid.org/0000-0002-1751-6674Hugo Moura de Albuquerque Melo9https://orcid.org/0000-0001-8072-337XUniversidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil.Universidade Federal de Pernambuco, Centro de Ciências Médicas, Departamento de Clínica Médica, Recife PE, Brazil. Background The Creutzfeldt-Jakob disease (CJD) is a spongiform encephalopathy that manifests as a rapidly progressive dementia syndrome. Currently, CJD has no cure, and many patients die within the first year, but some drugs are being studied as options for managing this condition.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0042-1755341Creutzfeldt-Jakob SyndromePrion DiseasesTherapeuticsSíndrome de Creutzfeldt-JakobDoenças PriônicasTerapêutica
spellingShingle Luiz Henrique Lélis Miranda
André Felipe Pastick de Holanda Oliveira
Davi Mariano de Carvalho
Gustavo Marques Figueredo Souza
João Guilherme Monteiro Magalhães
Joselmo Alberto Cabral Júnior
Pedro Thadeu Mertens Brainer de Queiroz Lima
Renato Melo Aguiar Júnior
Sérgio Pereira Lins Filho
Hugo Moura de Albuquerque Melo
Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?
Arquivos de Neuro-Psiquiatria
Creutzfeldt-Jakob Syndrome
Prion Diseases
Therapeutics
Síndrome de Creutzfeldt-Jakob
Doenças Priônicas
Terapêutica
title Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?
title_full Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?
title_fullStr Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?
title_full_unstemmed Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?
title_short Systematic review of pharmacological management in Creutzfeldt-Jakob disease: no options so far?
title_sort systematic review of pharmacological management in creutzfeldt jakob disease no options so far
topic Creutzfeldt-Jakob Syndrome
Prion Diseases
Therapeutics
Síndrome de Creutzfeldt-Jakob
Doenças Priônicas
Terapêutica
url http://www.thieme-connect.de/DOI/DOI?10.1055/s-0042-1755341
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