Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspective

Objective: In select patients with borderline ventricular hypoplasia, we adopted a strategy of initial single-ventricle palliation followed by staged or direct biventricular conversion by 2 years of age. Methods: Between 2018 and 2023, 14 newborns with borderline hypoplastic heart disease deemed hig...

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Main Authors: Nicholas D. Andersen, MD, Douglas M. Overbey, MD, Neel K. Prabhu, MD, Andrew W. McCrary, MD, MSc, Jennifer I. Sherwin, MD, Veerajalandhar Allareddy, MD, Joseph W. Turek, MD, PhD
Format: Article
Language:English
Published: Elsevier 2024-04-01
Series:JTCVS Techniques
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Online Access:http://www.sciencedirect.com/science/article/pii/S2666250724000610
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author Nicholas D. Andersen, MD
Douglas M. Overbey, MD
Neel K. Prabhu, MD
Andrew W. McCrary, MD, MSc
Jennifer I. Sherwin, MD
Veerajalandhar Allareddy, MD
Joseph W. Turek, MD, PhD
author_facet Nicholas D. Andersen, MD
Douglas M. Overbey, MD
Neel K. Prabhu, MD
Andrew W. McCrary, MD, MSc
Jennifer I. Sherwin, MD
Veerajalandhar Allareddy, MD
Joseph W. Turek, MD, PhD
author_sort Nicholas D. Andersen, MD
collection DOAJ
description Objective: In select patients with borderline ventricular hypoplasia, we adopted a strategy of initial single-ventricle palliation followed by staged or direct biventricular conversion by 2 years of age. Methods: Between 2018 and 2023, 14 newborns with borderline hypoplastic heart disease deemed high risk for primary biventricular repair underwent palliative procedures as a neonate/infant, followed by staged or direct biventricular conversion. Results: Of the 14 patients, 6 had borderline left ventricles and 8 had borderline right ventricles. Index neonatal operations were performed in 12 patients and included the Norwood operation (n = 5), pulmonary artery band (n = 3), ductal stent (n = 3), and hybrid Norwood (n = 1). Five patients underwent direct biventricular conversion, and the remaining 9 patients underwent staged ventricular recruitment operations at a mean age of 6 months (range, 3-11 months). Ventricular recruitment operations included atrial septation with or without ventricular rehabilitation, atrioventricular valve repair, or outflow tract operations. At a mean duration of 8 months (range, 4-10 months) after ventricular recruitment, there was a significant increase in chamber volume, aortic valve, and mitral valve size in patients with borderline left ventricles, and a normalization of the right ventricle:left ventricle end-diastolic volume ratio in patients with borderline right ventricles. To date, 13 of 14 patients have undergone successful biventricular conversion at a mean age of 16 months (range, 4-31 months). Conclusions: In select newborns with borderline hypoplastic heart disease, single-ventricle palliation followed by staged or direct biventricular conversion may increase infant survival while allowing for early attainment of a biventricular circulation.
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spelling doaj-art-3487b08429e24f20a6953d41d8bcb8df2025-08-20T03:36:38ZengElsevierJTCVS Techniques2666-25072024-04-012415016310.1016/j.xjtc.2024.02.006Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspectiveNicholas D. Andersen, MD0Douglas M. Overbey, MD1Neel K. Prabhu, MD2Andrew W. McCrary, MD, MSc3Jennifer I. Sherwin, MD4Veerajalandhar Allareddy, MD5Joseph W. Turek, MD, PhD6Department of Cardiothoracic Surgery, University of Texas Southwestern and Children's Health, Dallas, Tex; Address for reprints: Nicholas D. Andersen, MD, Division of Pediatric Cardiothoracic Surgery, Children's Medical Center Dallas, 1935 Medical District Dr, Dallas, TX 75235.Department of Surgery, Duke Children's Pediatric & Congenital Heart Center, Duke Children's Hospital, Durham, NCDepartment of Surgery, Duke Children's Pediatric & Congenital Heart Center, Duke Children's Hospital, Durham, NCDepartment of Pediatrics, Duke Children's Pediatric & Congenital Heart Center, Duke Children's Hospital, Durham, NCDepartment of Pediatrics, Duke Children's Pediatric & Congenital Heart Center, Duke Children's Hospital, Durham, NCDepartment of Pediatrics, Duke Children's Pediatric & Congenital Heart Center, Duke Children's Hospital, Durham, NCDepartment of Surgery, Duke Children's Pediatric & Congenital Heart Center, Duke Children's Hospital, Durham, NCObjective: In select patients with borderline ventricular hypoplasia, we adopted a strategy of initial single-ventricle palliation followed by staged or direct biventricular conversion by 2 years of age. Methods: Between 2018 and 2023, 14 newborns with borderline hypoplastic heart disease deemed high risk for primary biventricular repair underwent palliative procedures as a neonate/infant, followed by staged or direct biventricular conversion. Results: Of the 14 patients, 6 had borderline left ventricles and 8 had borderline right ventricles. Index neonatal operations were performed in 12 patients and included the Norwood operation (n = 5), pulmonary artery band (n = 3), ductal stent (n = 3), and hybrid Norwood (n = 1). Five patients underwent direct biventricular conversion, and the remaining 9 patients underwent staged ventricular recruitment operations at a mean age of 6 months (range, 3-11 months). Ventricular recruitment operations included atrial septation with or without ventricular rehabilitation, atrioventricular valve repair, or outflow tract operations. At a mean duration of 8 months (range, 4-10 months) after ventricular recruitment, there was a significant increase in chamber volume, aortic valve, and mitral valve size in patients with borderline left ventricles, and a normalization of the right ventricle:left ventricle end-diastolic volume ratio in patients with borderline right ventricles. To date, 13 of 14 patients have undergone successful biventricular conversion at a mean age of 16 months (range, 4-31 months). Conclusions: In select newborns with borderline hypoplastic heart disease, single-ventricle palliation followed by staged or direct biventricular conversion may increase infant survival while allowing for early attainment of a biventricular circulation.http://www.sciencedirect.com/science/article/pii/S2666250724000610atrioventricular septal defectbiventricular conversionborderline ventriclehypoplastic left heart syndromeventricular recruitment
spellingShingle Nicholas D. Andersen, MD
Douglas M. Overbey, MD
Neel K. Prabhu, MD
Andrew W. McCrary, MD, MSc
Jennifer I. Sherwin, MD
Veerajalandhar Allareddy, MD
Joseph W. Turek, MD, PhD
Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspective
JTCVS Techniques
atrioventricular septal defect
biventricular conversion
borderline ventricle
hypoplastic left heart syndrome
ventricular recruitment
title Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspective
title_full Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspective
title_fullStr Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspective
title_full_unstemmed Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspective
title_short Staged repair of borderline hypoplastic heart disease with early biventricular conversionCentral MessagePerspective
title_sort staged repair of borderline hypoplastic heart disease with early biventricular conversioncentral messageperspective
topic atrioventricular septal defect
biventricular conversion
borderline ventricle
hypoplastic left heart syndrome
ventricular recruitment
url http://www.sciencedirect.com/science/article/pii/S2666250724000610
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