Novel CLCNKB Mutation in Two Siblings With Classic Bartter Syndrome

Conclusions: Bartter syndrome Type III is a genetic disorder that must be identified clinically without delay, as it typically manifests as acute dehydration due to polyuria and vomiting. Hydrocephalus, although cannot be concluded to be a complication of Bartter syndrome, can be associated due to s...

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Main Authors: Navid Roodaki, Leigh Michelle Salinas, Ebner Bon G. Maceda, Jorelyn Frias
Format: Article
Language:English
Published: Wiley 2025-01-01
Series:Case Reports in Genetics
Online Access:http://dx.doi.org/10.1155/crig/8862780
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author Navid Roodaki
Leigh Michelle Salinas
Ebner Bon G. Maceda
Jorelyn Frias
author_facet Navid Roodaki
Leigh Michelle Salinas
Ebner Bon G. Maceda
Jorelyn Frias
author_sort Navid Roodaki
collection DOAJ
description Conclusions: Bartter syndrome Type III is a genetic disorder that must be identified clinically without delay, as it typically manifests as acute dehydration due to polyuria and vomiting. Hydrocephalus, although cannot be concluded to be a complication of Bartter syndrome, can be associated due to several electrolyte imbalances involved in this condition. Genetic testing is essential for identifying unidentified pathogenic variants that will aid future patients diagnosed with this condition. Genetic counseling is of the utmost importance for these families affected by the condition in question.
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spelling doaj-art-30fc48d035ce4ea19d81fc0a5867a10e2025-08-20T02:06:20ZengWileyCase Reports in Genetics2090-65522025-01-01202510.1155/crig/8862780Novel CLCNKB Mutation in Two Siblings With Classic Bartter SyndromeNavid Roodaki0Leigh Michelle Salinas1Ebner Bon G. Maceda2Jorelyn Frias3Department of PediatricsDepartment of PediatricsCenter for Human Genetics ServicesDepartment of PediatricsConclusions: Bartter syndrome Type III is a genetic disorder that must be identified clinically without delay, as it typically manifests as acute dehydration due to polyuria and vomiting. Hydrocephalus, although cannot be concluded to be a complication of Bartter syndrome, can be associated due to several electrolyte imbalances involved in this condition. Genetic testing is essential for identifying unidentified pathogenic variants that will aid future patients diagnosed with this condition. Genetic counseling is of the utmost importance for these families affected by the condition in question.http://dx.doi.org/10.1155/crig/8862780
spellingShingle Navid Roodaki
Leigh Michelle Salinas
Ebner Bon G. Maceda
Jorelyn Frias
Novel CLCNKB Mutation in Two Siblings With Classic Bartter Syndrome
Case Reports in Genetics
title Novel CLCNKB Mutation in Two Siblings With Classic Bartter Syndrome
title_full Novel CLCNKB Mutation in Two Siblings With Classic Bartter Syndrome
title_fullStr Novel CLCNKB Mutation in Two Siblings With Classic Bartter Syndrome
title_full_unstemmed Novel CLCNKB Mutation in Two Siblings With Classic Bartter Syndrome
title_short Novel CLCNKB Mutation in Two Siblings With Classic Bartter Syndrome
title_sort novel clcnkb mutation in two siblings with classic bartter syndrome
url http://dx.doi.org/10.1155/crig/8862780
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AT leighmichellesalinas novelclcnkbmutationintwosiblingswithclassicbarttersyndrome
AT ebnerbongmaceda novelclcnkbmutationintwosiblingswithclassicbarttersyndrome
AT jorelynfrias novelclcnkbmutationintwosiblingswithclassicbarttersyndrome