BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3

Objective: Spinal muscular atrophy is a lower motor neuron disease, but other parts of the body could be affected. This study compared bone mineral density with bone metabolism and physical growth rates in patients diagnosed with spinal muscular atrophy type 2 and type 3. Material and Methods: Twent...

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Main Authors: Osman Kipoğlu, Esin Karakılıç Özturan, Orhan Coşkun, Ayşe Pınar Öztürk, Edibe Pembegül Yıldız, Firdevs Baş, Nur Aydınlı, Meliha Mine Çalışkan
Format: Article
Language:English
Published: Istanbul University Press 2022-01-01
Series:İstanbul Tıp Fakültesi Dergisi
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Online Access:https://cdn.istanbul.edu.tr/file/JTA6CLJ8T5/31AFCE436E5A4CBDB6AFECF5F5EAC501
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author Osman Kipoğlu
Esin Karakılıç Özturan
Orhan Coşkun
Ayşe Pınar Öztürk
Edibe Pembegül Yıldız
Firdevs Baş
Nur Aydınlı
Meliha Mine Çalışkan
author_facet Osman Kipoğlu
Esin Karakılıç Özturan
Orhan Coşkun
Ayşe Pınar Öztürk
Edibe Pembegül Yıldız
Firdevs Baş
Nur Aydınlı
Meliha Mine Çalışkan
author_sort Osman Kipoğlu
collection DOAJ
description Objective: Spinal muscular atrophy is a lower motor neuron disease, but other parts of the body could be affected. This study compared bone mineral density with bone metabolism and physical growth rates in patients diagnosed with spinal muscular atrophy type 2 and type 3. Material and Methods: Twenty-six patients with spinal muscular atrophy were included in the study (15 patients for type 2 and 11 for type 3). Weights and heights of patients were measured, standard deviation scores were determined, and the body-mass index was calculated. Motor function and pubertal assessment were performed. Serum calcium, phosphorus, alkaline phosphatase, parathormone, and 25-hydroxyvitamin vitamin D levels were compared. Spine radiography for scoliosis and bone densitometry for bone mineral density were performed, and volumetric bone mineral density was calculated for age and sex. Results: Medians of height standard deviation scores were significantly lower in type 2 patients. There was no difference between the two groups in terms of serum calcium, phosphorus, alkaline phosphatase, parathormone, and 25-hydroxyvitamin D levels. The ratio of scoliosis was higher in type 2 patients as was its severity, but Z-scores of volumetric bone mineral density was lower in the same group. Conclusion: This study showed that bone mineralization and growth rates were significantly lower in spinal muscular atrophy, mainly in type 2. Further studies are needed to evaluate bone health in spinal muscular atrophy patients.
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issn 1305-6441
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publisher Istanbul University Press
record_format Article
series İstanbul Tıp Fakültesi Dergisi
spelling doaj-art-2f451df2cfc34ed08236af032bfdb5ff2025-08-20T02:15:19ZengIstanbul University Pressİstanbul Tıp Fakültesi Dergisi1305-64412022-01-01851222810.26650/IUITFD.884235123456BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3Osman Kipoğlu0https://orcid.org/0000-0001-9208-6697Esin Karakılıç Özturan1https://orcid.org/0000-0002-8842-1752Orhan Coşkun2https://orcid.org/0000-0001-9229-404XAyşe Pınar Öztürk3https://orcid.org/0000-0003-3466-2857Edibe Pembegül Yıldız4https://orcid.org/0000-0002-8016-0404Firdevs Baş5https://orcid.org/0000-0001-9689-4464Nur Aydınlı6https://orcid.org/0000-0003-0492-3411Meliha Mine Çalışkan7https://orcid.org/0000-0002-6869-3937İstanbul Üniversitesi, İstanbul, Türkiyeİstanbul Üniversitesi, İstanbul, Türkiyeİstanbul Üniversitesi, İstanbul, Türkiyeİstanbul Üniversitesi, İstanbul, Türkiyeİstanbul Üniversitesi, İstanbul, Türkiyeİstanbul Üniversitesi, İstanbul, Türkiyeİstanbul Üniversitesi, İstanbul, Türkiyeİstanbul Üniversitesi, İstanbul, TürkiyeObjective: Spinal muscular atrophy is a lower motor neuron disease, but other parts of the body could be affected. This study compared bone mineral density with bone metabolism and physical growth rates in patients diagnosed with spinal muscular atrophy type 2 and type 3. Material and Methods: Twenty-six patients with spinal muscular atrophy were included in the study (15 patients for type 2 and 11 for type 3). Weights and heights of patients were measured, standard deviation scores were determined, and the body-mass index was calculated. Motor function and pubertal assessment were performed. Serum calcium, phosphorus, alkaline phosphatase, parathormone, and 25-hydroxyvitamin vitamin D levels were compared. Spine radiography for scoliosis and bone densitometry for bone mineral density were performed, and volumetric bone mineral density was calculated for age and sex. Results: Medians of height standard deviation scores were significantly lower in type 2 patients. There was no difference between the two groups in terms of serum calcium, phosphorus, alkaline phosphatase, parathormone, and 25-hydroxyvitamin D levels. The ratio of scoliosis was higher in type 2 patients as was its severity, but Z-scores of volumetric bone mineral density was lower in the same group. Conclusion: This study showed that bone mineralization and growth rates were significantly lower in spinal muscular atrophy, mainly in type 2. Further studies are needed to evaluate bone health in spinal muscular atrophy patients.https://cdn.istanbul.edu.tr/file/JTA6CLJ8T5/31AFCE436E5A4CBDB6AFECF5F5EAC501spinal muscular atrophybone mineral densitybone health
spellingShingle Osman Kipoğlu
Esin Karakılıç Özturan
Orhan Coşkun
Ayşe Pınar Öztürk
Edibe Pembegül Yıldız
Firdevs Baş
Nur Aydınlı
Meliha Mine Çalışkan
BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3
İstanbul Tıp Fakültesi Dergisi
spinal muscular atrophy
bone mineral density
bone health
title BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3
title_full BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3
title_fullStr BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3
title_full_unstemmed BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3
title_short BONE HEALTH AND GROWTH IN SPINAL MUSCULAR ATROPHY TYPE 2 AND 3
title_sort bone health and growth in spinal muscular atrophy type 2 and 3
topic spinal muscular atrophy
bone mineral density
bone health
url https://cdn.istanbul.edu.tr/file/JTA6CLJ8T5/31AFCE436E5A4CBDB6AFECF5F5EAC501
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AT aysepınarozturk bonehealthandgrowthinspinalmuscularatrophytype2and3
AT edibepembegulyıldız bonehealthandgrowthinspinalmuscularatrophytype2and3
AT firdevsbas bonehealthandgrowthinspinalmuscularatrophytype2and3
AT nuraydınlı bonehealthandgrowthinspinalmuscularatrophytype2and3
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