Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four Cases
Pulmonary atresia with intact ventricular septum suggests a simple congenital heart malformation. However, nothing could be further from the truth. Among the morphological peculiarities of this condition, the presence of congenitally unguarded tricuspid valve orifice is rarely observed. The present...
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| Format: | Article |
| Language: | Spanish |
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Centro Provincial de Información de Ciencias Médicas. Cienfuegos
2013-12-01
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| Series: | Medisur |
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| Online Access: | http://medisur.sld.cu/index.php/medisur/article/view/2411 |
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| author | Adel E. González Morejón Ansia Serrano Sánchez Giselle Serrano Ricardo |
| author_facet | Adel E. González Morejón Ansia Serrano Sánchez Giselle Serrano Ricardo |
| author_sort | Adel E. González Morejón |
| collection | DOAJ |
| description | Pulmonary atresia with intact ventricular septum suggests a simple congenital heart malformation. However, nothing could be further from the truth. Among the morphological peculiarities of this condition, the presence of congenitally unguarded tricuspid valve orifice is rarely observed. The present paper aims at describing a series of four patients with both malformations detected in the William Soler Children’s Heart Center from 1986 through 2012. Echocardiographic diagnosis could be accurately performed in the last two patients; identification of the initial cases was established by the findings at necropsy. All patients underwent Blalock – Taussig shunt as initial palliative treatment, which was associated with balloon atrioseptostomy in two cases. Only one of the last children mentioned survived. Vital prognosis of patients suffering from this association of malformations lies in early echocardiographic detection. |
| format | Article |
| id | doaj-art-2e57390016014dfa93f802c80a113788 |
| institution | Kabale University |
| issn | 1727-897X |
| language | Spanish |
| publishDate | 2013-12-01 |
| publisher | Centro Provincial de Información de Ciencias Médicas. Cienfuegos |
| record_format | Article |
| series | Medisur |
| spelling | doaj-art-2e57390016014dfa93f802c80a1137882025-01-30T21:28:47ZspaCentro Provincial de Información de Ciencias Médicas. CienfuegosMedisur1727-897X2013-12-011166776841037Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four CasesAdel E. González Morejón0Ansia Serrano Sánchez1Giselle Serrano Ricardo2Cardiocentro Pediátrico William Soler. La HabanaHospital Pediátrico Universitario William Soler. La HabanaCardiocentro Pediátrico William Soler. La HabanaPulmonary atresia with intact ventricular septum suggests a simple congenital heart malformation. However, nothing could be further from the truth. Among the morphological peculiarities of this condition, the presence of congenitally unguarded tricuspid valve orifice is rarely observed. The present paper aims at describing a series of four patients with both malformations detected in the William Soler Children’s Heart Center from 1986 through 2012. Echocardiographic diagnosis could be accurately performed in the last two patients; identification of the initial cases was established by the findings at necropsy. All patients underwent Blalock – Taussig shunt as initial palliative treatment, which was associated with balloon atrioseptostomy in two cases. Only one of the last children mentioned survived. Vital prognosis of patients suffering from this association of malformations lies in early echocardiographic detection.http://medisur.sld.cu/index.php/medisur/article/view/2411atresia pulmonartabique interventricularatresia tricúspideniñoinformes de casos |
| spellingShingle | Adel E. González Morejón Ansia Serrano Sánchez Giselle Serrano Ricardo Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four Cases Medisur atresia pulmonar tabique interventricular atresia tricúspide niño informes de casos |
| title | Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four Cases |
| title_full | Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four Cases |
| title_fullStr | Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four Cases |
| title_full_unstemmed | Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four Cases |
| title_short | Pulmonary Atresia with Intact Ventricular Septum and Absence of Tricuspid Valve. A Report of Four Cases |
| title_sort | pulmonary atresia with intact ventricular septum and absence of tricuspid valve a report of four cases |
| topic | atresia pulmonar tabique interventricular atresia tricúspide niño informes de casos |
| url | http://medisur.sld.cu/index.php/medisur/article/view/2411 |
| work_keys_str_mv | AT adelegonzalezmorejon pulmonaryatresiawithintactventricularseptumandabsenceoftricuspidvalveareportoffourcases AT ansiaserranosanchez pulmonaryatresiawithintactventricularseptumandabsenceoftricuspidvalveareportoffourcases AT giselleserranoricardo pulmonaryatresiawithintactventricularseptumandabsenceoftricuspidvalveareportoffourcases |