Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome
Genital ulcers are challenging to any clinician and causes transcend many specialties. Skin ulceration in patients with primary Sjögren’s syndrome is infrequent but an established feature of cutaneous involvement. Although gynecological symptoms, such as vulvovaginal dryness, dyspareunia, and prurit...
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| Format: | Article |
| Language: | English |
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Wiley
2018-01-01
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| Series: | Case Reports in Obstetrics and Gynecology |
| Online Access: | http://dx.doi.org/10.1155/2018/3507484 |
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| author | Filipa de Castro Coelho Maria Amaral Lúcia Correia Maria João Nunes Campos Tereza Paula Augusta Borges Jorge Borrego |
| author_facet | Filipa de Castro Coelho Maria Amaral Lúcia Correia Maria João Nunes Campos Tereza Paula Augusta Borges Jorge Borrego |
| author_sort | Filipa de Castro Coelho |
| collection | DOAJ |
| description | Genital ulcers are challenging to any clinician and causes transcend many specialties. Skin ulceration in patients with primary Sjögren’s syndrome is infrequent but an established feature of cutaneous involvement. Although gynecological symptoms, such as vulvovaginal dryness, dyspareunia, and pruritus, are common in women with primary Sjögren’s syndrome, patients affected by vulvar ulcers are unknown. We describe an exceptional case of necrotic aphthous-type vulvar ulceration as initial presentation of primary Sjögren’s syndrome that was possibly triggered by an infectious agent. Successful healing was achieved with oral corticosteroids, despite some loss of labia minora and labia majora as sequelae of the necrotizing process. Reactive acute genital ulcers (Lipschütz ulcers) should be considered as a possible manifestation of many autoimmune/inflammatory disorders, beyond the classic associations such as Behçet’s syndrome or Crohn’s disease. |
| format | Article |
| id | doaj-art-2da6c0320d2d49df88308cc95f872184 |
| institution | Kabale University |
| issn | 2090-6684 2090-6692 |
| language | English |
| publishDate | 2018-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Obstetrics and Gynecology |
| spelling | doaj-art-2da6c0320d2d49df88308cc95f8721842025-02-03T01:04:51ZengWileyCase Reports in Obstetrics and Gynecology2090-66842090-66922018-01-01201810.1155/2018/35074843507484Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s SyndromeFilipa de Castro Coelho0Maria Amaral1Lúcia Correia2Maria João Nunes Campos3Tereza Paula4Augusta Borges5Jorge Borrego6Gynecology Department, Hospital Dr. Nélio Mendonça, Serviço de Saúde da Região Autónoma da Madeira, EPE, Funchal, PortugalInternal Medicine Department, Maternidade Dr. Alfredo da Costa, Centro Hospitalar Lisboa Central, Lisboa, PortugalGynecology Department, Instituto Português de Oncologia de Lisboa Francisco Gentil, EPE, Lisboa, PortugalGynecology Department, Maternidade Dr. Alfredo da Costa, Centro Hospitalar Lisboa Central, Lisboa, PortugalGynecology Department, Maternidade Dr. Alfredo da Costa, Centro Hospitalar Lisboa Central, Lisboa, PortugalInternal Medicine Department, Maternidade Dr. Alfredo da Costa, Centro Hospitalar Lisboa Central, Lisboa, PortugalGynecology Department, Maternidade Dr. Alfredo da Costa, Centro Hospitalar Lisboa Central, Lisboa, PortugalGenital ulcers are challenging to any clinician and causes transcend many specialties. Skin ulceration in patients with primary Sjögren’s syndrome is infrequent but an established feature of cutaneous involvement. Although gynecological symptoms, such as vulvovaginal dryness, dyspareunia, and pruritus, are common in women with primary Sjögren’s syndrome, patients affected by vulvar ulcers are unknown. We describe an exceptional case of necrotic aphthous-type vulvar ulceration as initial presentation of primary Sjögren’s syndrome that was possibly triggered by an infectious agent. Successful healing was achieved with oral corticosteroids, despite some loss of labia minora and labia majora as sequelae of the necrotizing process. Reactive acute genital ulcers (Lipschütz ulcers) should be considered as a possible manifestation of many autoimmune/inflammatory disorders, beyond the classic associations such as Behçet’s syndrome or Crohn’s disease.http://dx.doi.org/10.1155/2018/3507484 |
| spellingShingle | Filipa de Castro Coelho Maria Amaral Lúcia Correia Maria João Nunes Campos Tereza Paula Augusta Borges Jorge Borrego Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome Case Reports in Obstetrics and Gynecology |
| title | Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome |
| title_full | Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome |
| title_fullStr | Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome |
| title_full_unstemmed | Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome |
| title_short | Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome |
| title_sort | lipschutz genital ulceration as initial manifestation of primary sjogren s syndrome |
| url | http://dx.doi.org/10.1155/2018/3507484 |
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