Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases
Hepatic angiomyolipoma is an extremely rare benign hamartomatous lesion. Situs inversus totalis is a genetic condition occurring in 0.01% of the population. Following the kidney, the liver is the second most common site of angiomyolipoma. No consensus on the treatment of hepatic angiomyolipoma has b...
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| Format: | Article |
| Language: | English |
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Wiley
2016-01-01
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| Series: | Case Reports in Hepatology |
| Online Access: | http://dx.doi.org/10.1155/2016/5060284 |
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| _version_ | 1832550683048411136 |
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| author | Jonathan Mayes Nigel Heaton |
| author_facet | Jonathan Mayes Nigel Heaton |
| author_sort | Jonathan Mayes |
| collection | DOAJ |
| description | Hepatic angiomyolipoma is an extremely rare benign hamartomatous lesion. Situs inversus totalis is a genetic condition occurring in 0.01% of the population. Following the kidney, the liver is the second most common site of angiomyolipoma. No consensus on the treatment of hepatic angiomyolipoma has been reached. However, the majority of these tumours are managed conservatively. Situs inversus totalis presents difficulties for procedures and is most commonly an incidental finding. These two conditions have not previously been reported and no genetic link has been established between them. This paper reports the association of both conditions in a 74-year-old female, reviews the literature, and presents CT imaging of the case. |
| format | Article |
| id | doaj-art-2d3ba325d7f840ddab9ee406cfb501b7 |
| institution | Kabale University |
| issn | 2090-6587 2090-6595 |
| language | English |
| publishDate | 2016-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Hepatology |
| spelling | doaj-art-2d3ba325d7f840ddab9ee406cfb501b72025-02-03T06:06:07ZengWileyCase Reports in Hepatology2090-65872090-65952016-01-01201610.1155/2016/50602845060284Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare DiseasesJonathan Mayes0Nigel Heaton1Newcastle University, Newcastle upon Tyne NE1 7RU, UKInstitute of Liver Studies, King’s Health Partners, King’s College Hospital NHS FT, Denmark Hill, Camberwell, London SE5 9RS, UKHepatic angiomyolipoma is an extremely rare benign hamartomatous lesion. Situs inversus totalis is a genetic condition occurring in 0.01% of the population. Following the kidney, the liver is the second most common site of angiomyolipoma. No consensus on the treatment of hepatic angiomyolipoma has been reached. However, the majority of these tumours are managed conservatively. Situs inversus totalis presents difficulties for procedures and is most commonly an incidental finding. These two conditions have not previously been reported and no genetic link has been established between them. This paper reports the association of both conditions in a 74-year-old female, reviews the literature, and presents CT imaging of the case.http://dx.doi.org/10.1155/2016/5060284 |
| spellingShingle | Jonathan Mayes Nigel Heaton Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases Case Reports in Hepatology |
| title | Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases |
| title_full | Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases |
| title_fullStr | Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases |
| title_full_unstemmed | Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases |
| title_short | Angiomyolipoma in a Patient with Situs Inversus Totalis: Managing Two Rare Diseases |
| title_sort | angiomyolipoma in a patient with situs inversus totalis managing two rare diseases |
| url | http://dx.doi.org/10.1155/2016/5060284 |
| work_keys_str_mv | AT jonathanmayes angiomyolipomainapatientwithsitusinversustotalismanagingtworarediseases AT nigelheaton angiomyolipomainapatientwithsitusinversustotalismanagingtworarediseases |