A Misleading Orbital Cystic Lesion

Orbital schwannomas are rare and arise from the Schwann cells of sensory nerves. Cystic degeneration has been known to occur with orbital schwannomas but those occurring intra-ocularly have not been reported till date. Authors here report a rare case of a 24 year old woman, blind in the right eye, p...

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Bibliographic Details
Main Authors: Shruthi Tara, Shraddha Shah
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2022-01-01
Series:Delhi Journal of Ophthalmology
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Online Access:https://journals.lww.com/10.7869/djo.742
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Summary:Orbital schwannomas are rare and arise from the Schwann cells of sensory nerves. Cystic degeneration has been known to occur with orbital schwannomas but those occurring intra-ocularly have not been reported till date. Authors here report a rare case of a 24 year old woman, blind in the right eye, presenting with right sided headache and progressive proptosis since four years. Computer tomography (CT) of right eye showed presence of a well-demarcated, retro-orbital cystic lesion with a solid component causing displacement of the globe-like structure and bony remodelling. From the clinical and radiological features a pre-operative diagnosis of a right congenital cystic eyeball and a left microphthalmos with cyst was made. The patient underwent enucleation of the right eye along with the cystic lesion as a whole. Based on histopathology, a final diagnosis of an orbital schwannoma with extensive cystic degeneration and intra-ocular extension was made
ISSN:0972-0200
2454-2784