Syringocystadenocarcinoma Papilliferum in a Fifteen-Year-Old Girl: A Case Report and Review of the Literature

Syringocystadenocarcinoma papilliferum (SCACP) is a rare malignant neoplasm arising from adnexal tissues and is the malignant complement to the benign neoplasm syringocystadenoma papilliferum (SCAP). SCACP lesions appear as raised nodules or inflammatory plaques and can be associated with SCAP or ne...

Full description

Saved in:
Bibliographic Details
Main Authors: Jordan N. Halsey, Esteban Fernandez Faith, Suzanna J. Logan, Archana Shenoy, Kathleen M. Schieffer, Catherine E. Cottrell, Anna P. Lillis, Jennifer H. Aldrink, Bhuvana A. Setty, Gregory D. Pearson
Format: Article
Language:English
Published: Wiley 2022-01-01
Series:Case Reports in Dermatological Medicine
Online Access:http://dx.doi.org/10.1155/2022/8076649
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:Syringocystadenocarcinoma papilliferum (SCACP) is a rare malignant neoplasm arising from adnexal tissues and is the malignant complement to the benign neoplasm syringocystadenoma papilliferum (SCAP). SCACP lesions appear as raised nodules or inflammatory plaques and can be associated with SCAP or nevus sebaceous. There have been fewer than 100 described cases of this neoplasm in the literature, and all previously published cases have been described in adults, with the majority occurring in the elderly. We present a case of an adolescent female with a syringocystadenocarcinoma papilliferum arising from a large thigh mass harboring an in-frame alteration in MAP2K1 along with a brief review of the literature.
ISSN:2090-6471