Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experience

BackgroundDedifferentiated liposarcoma (DDLPS) is one of the most common types of soft tissue sarcoma (STS) characterized by liposarcomatous differentiation and a predilection for the retroperitoneum. Despite the growing number of histology-specific immune checkpoint blockade (ICB) trials in STS, it...

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Main Authors: Madeline B. Torres, Cheuk Hong Leung, Marianne Zoghbi, Rossana Lazcano, Davis Ingram, Khalida Wani, Emily Z. Keung, M. Alejandra Zarzour, Christopher P. Scally, Kelly K. Hunt, Anthony Conley, Andrew J. Bishop, B. Ashleigh Guadagnolo, Ahsan Farooqi, Devarati Mitra, Alison K. Yoder, Michael S. Nakazawa, Dejka Araujo, Andrew Livingston, Ravin Ratan, Shreyaskumar Patel, Vinod Ravi, Alexander J. Lazar, Christina L. Roland, Neeta Somaiah, Elise F. Nassif Haddad
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Language:English
Published: Frontiers Media S.A. 2025-04-01
Series:Frontiers in Immunology
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Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2025.1567736/full
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author Madeline B. Torres
Madeline B. Torres
Cheuk Hong Leung
Marianne Zoghbi
Rossana Lazcano
Davis Ingram
Khalida Wani
Emily Z. Keung
M. Alejandra Zarzour
Christopher P. Scally
Kelly K. Hunt
Anthony Conley
Andrew J. Bishop
B. Ashleigh Guadagnolo
Ahsan Farooqi
Devarati Mitra
Alison K. Yoder
Michael S. Nakazawa
Dejka Araujo
Andrew Livingston
Ravin Ratan
Shreyaskumar Patel
Vinod Ravi
Alexander J. Lazar
Alexander J. Lazar
Christina L. Roland
Neeta Somaiah
Elise F. Nassif Haddad
Elise F. Nassif Haddad
author_facet Madeline B. Torres
Madeline B. Torres
Cheuk Hong Leung
Marianne Zoghbi
Rossana Lazcano
Davis Ingram
Khalida Wani
Emily Z. Keung
M. Alejandra Zarzour
Christopher P. Scally
Kelly K. Hunt
Anthony Conley
Andrew J. Bishop
B. Ashleigh Guadagnolo
Ahsan Farooqi
Devarati Mitra
Alison K. Yoder
Michael S. Nakazawa
Dejka Araujo
Andrew Livingston
Ravin Ratan
Shreyaskumar Patel
Vinod Ravi
Alexander J. Lazar
Alexander J. Lazar
Christina L. Roland
Neeta Somaiah
Elise F. Nassif Haddad
Elise F. Nassif Haddad
author_sort Madeline B. Torres
collection DOAJ
description BackgroundDedifferentiated liposarcoma (DDLPS) is one of the most common types of soft tissue sarcoma (STS) characterized by liposarcomatous differentiation and a predilection for the retroperitoneum. Despite the growing number of histology-specific immune checkpoint blockade (ICB) trials in STS, it is still difficult to identify the radiographic objective response rate (ORR) for DDLPS in the real world setting. This study aimed to evaluate the ORR and survival of patients with DDLPS treated with ICB at a single center.MethodsWe conducted a retrospective study of 31 patients with pathologically confirmed DDLPS treated with ICB at MD Anderson Cancer Center between 2018 and 2023. Patient demographics, disease characteristics, treatment history, and response to ICB were analyzed. Immunohistochemical analysis was performed on tumor samples to assess immune-related markers.ResultsORR by RECIST 1.1 was 3.2% (n=1/31). Among all patients (n=31), 6% achieved partial radiographic response, while 39% had stable disease, and 55% showed progressive disease. Median progression-free survival (PFS) was 3.5 (95%CI:1.9, 4.7) months, and overall survival (OS) after ICB initiation was 19.7 (95%CI: 8.8, not reached) months. Patients without prior systemic therapy demonstrated better OS (p=0.004). Immunohistochemistry revealed no relationship between pre- or post-ICB expression of CD8, CD20, CD21 and PDL-1 and response.ConclusionWhile the response to ICB in DDLPS remains limited, specific immune markers may influence treatment outcomes. CD20/21 post-ICB appear more important for prognosis. Further research is warranted to identify predictive factors for ICB efficacy in DDLPS.
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spelling doaj-art-2aeb74ef38cb4842bef698ed2bb59db32025-08-20T02:28:55ZengFrontiers Media S.A.Frontiers in Immunology1664-32242025-04-011610.3389/fimmu.2025.15677361567736Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experienceMadeline B. Torres0Madeline B. Torres1Cheuk Hong Leung2Marianne Zoghbi3Rossana Lazcano4Davis Ingram5Khalida Wani6Emily Z. Keung7M. Alejandra Zarzour8Christopher P. Scally9Kelly K. Hunt10Anthony Conley11Andrew J. Bishop12B. Ashleigh Guadagnolo13Ahsan Farooqi14Devarati Mitra15Alison K. Yoder16Michael S. Nakazawa17Dejka Araujo18Andrew Livingston19Ravin Ratan20Shreyaskumar Patel21Vinod Ravi22Alexander J. Lazar23Alexander J. Lazar24Christina L. Roland25Neeta Somaiah26Elise F. Nassif Haddad27Elise F. Nassif Haddad28Department of Surgical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Surgery, Cooper University Hospital, Cooper Medical School of Rowan University, Camden, NJ, United StatesDepartment of Biostatistics, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Translational Molecular Pathology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Translational Molecular Pathology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Translational Molecular Pathology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Surgical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Surgical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Surgical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Radiation Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Translational Molecular Pathology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Genomic Medicine, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Surgical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Sarcoma Medical Oncology, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesDepartment of Investigational Cancer Therapeutics, The University of Texas MD Anderson Cancer Center, Houston, TX, United StatesBackgroundDedifferentiated liposarcoma (DDLPS) is one of the most common types of soft tissue sarcoma (STS) characterized by liposarcomatous differentiation and a predilection for the retroperitoneum. Despite the growing number of histology-specific immune checkpoint blockade (ICB) trials in STS, it is still difficult to identify the radiographic objective response rate (ORR) for DDLPS in the real world setting. This study aimed to evaluate the ORR and survival of patients with DDLPS treated with ICB at a single center.MethodsWe conducted a retrospective study of 31 patients with pathologically confirmed DDLPS treated with ICB at MD Anderson Cancer Center between 2018 and 2023. Patient demographics, disease characteristics, treatment history, and response to ICB were analyzed. Immunohistochemical analysis was performed on tumor samples to assess immune-related markers.ResultsORR by RECIST 1.1 was 3.2% (n=1/31). Among all patients (n=31), 6% achieved partial radiographic response, while 39% had stable disease, and 55% showed progressive disease. Median progression-free survival (PFS) was 3.5 (95%CI:1.9, 4.7) months, and overall survival (OS) after ICB initiation was 19.7 (95%CI: 8.8, not reached) months. Patients without prior systemic therapy demonstrated better OS (p=0.004). Immunohistochemistry revealed no relationship between pre- or post-ICB expression of CD8, CD20, CD21 and PDL-1 and response.ConclusionWhile the response to ICB in DDLPS remains limited, specific immune markers may influence treatment outcomes. CD20/21 post-ICB appear more important for prognosis. Further research is warranted to identify predictive factors for ICB efficacy in DDLPS.https://www.frontiersin.org/articles/10.3389/fimmu.2025.1567736/fullsarcomadedifferentiated liposarcomaAnti-PD1immunotherapyimmune-checkpoint inhibitorssurvival
spellingShingle Madeline B. Torres
Madeline B. Torres
Cheuk Hong Leung
Marianne Zoghbi
Rossana Lazcano
Davis Ingram
Khalida Wani
Emily Z. Keung
M. Alejandra Zarzour
Christopher P. Scally
Kelly K. Hunt
Anthony Conley
Andrew J. Bishop
B. Ashleigh Guadagnolo
Ahsan Farooqi
Devarati Mitra
Alison K. Yoder
Michael S. Nakazawa
Dejka Araujo
Andrew Livingston
Ravin Ratan
Shreyaskumar Patel
Vinod Ravi
Alexander J. Lazar
Alexander J. Lazar
Christina L. Roland
Neeta Somaiah
Elise F. Nassif Haddad
Elise F. Nassif Haddad
Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experience
Frontiers in Immunology
sarcoma
dedifferentiated liposarcoma
Anti-PD1
immunotherapy
immune-checkpoint inhibitors
survival
title Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experience
title_full Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experience
title_fullStr Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experience
title_full_unstemmed Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experience
title_short Dedifferentiated liposarcomas treated with immune checkpoint blockade: the MD Anderson experience
title_sort dedifferentiated liposarcomas treated with immune checkpoint blockade the md anderson experience
topic sarcoma
dedifferentiated liposarcoma
Anti-PD1
immunotherapy
immune-checkpoint inhibitors
survival
url https://www.frontiersin.org/articles/10.3389/fimmu.2025.1567736/full
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