A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia

Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) is a rare clinical condition with only about 100 cases reported in the literature. It is characterized by primary hyperplasia of pulmonary neuroendocrine cells (PNECs) which are specialized epithelial cells located throughout the...

Full description

Saved in:
Bibliographic Details
Main Authors: Godwin Ofikwu, Vishnu R. Mani, Ajai Rajabalan, Albert Adu, Leaque Ahmed, Dennis Vega
Format: Article
Language:English
Published: Wiley 2015-01-01
Series:Case Reports in Surgery
Online Access:http://dx.doi.org/10.1155/2015/318175
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850229881508462592
author Godwin Ofikwu
Vishnu R. Mani
Ajai Rajabalan
Albert Adu
Leaque Ahmed
Dennis Vega
author_facet Godwin Ofikwu
Vishnu R. Mani
Ajai Rajabalan
Albert Adu
Leaque Ahmed
Dennis Vega
author_sort Godwin Ofikwu
collection DOAJ
description Diffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) is a rare clinical condition with only about 100 cases reported in the literature. It is characterized by primary hyperplasia of pulmonary neuroendocrine cells (PNECs) which are specialized epithelial cells located throughout the entire respiratory tract, from the trachea to the terminal airways. DIPNECH appears in various forms that include diffuse proliferation of scattered neuroendocrine cells, small nodules, or a linear proliferation. It is usually seen in middle-aged, nonsmoking women with symptoms of cough, dyspnea, and wheezing. We present a 45-year-old, nonsmoking woman who presented with symptoms of DIPNECH associated with bilateral pulmonary nodules and left hilar adenopathy. Of interest, DIPNECH in our patient was associated with metastatic pulmonary carcinoids, papillary carcinoma of the left breast, oncocytoma and angiomyolipoma of her left kidney, and cortical nodules suggestive of tuberous sclerosis. She had video assisted thoracoscopic surgery (VATS), modified radical mastectomy with reconstruction, and radical nephrectomy. She is currently symptom-free most of the time with over two years of follow-up.
format Article
id doaj-art-2a5dd76e2c8e4796be6ffb05120f1fbd
institution OA Journals
issn 2090-6900
2090-6919
language English
publishDate 2015-01-01
publisher Wiley
record_format Article
series Case Reports in Surgery
spelling doaj-art-2a5dd76e2c8e4796be6ffb05120f1fbd2025-08-20T02:04:02ZengWileyCase Reports in Surgery2090-69002090-69192015-01-01201510.1155/2015/318175318175A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell HyperplasiaGodwin Ofikwu0Vishnu R. Mani1Ajai Rajabalan2Albert Adu3Leaque Ahmed4Dennis Vega5Department of Surgery, Columbia University College of Physicians and Surgeons at Harlem Hospital, New York, NY 10037, USADepartment of Surgery, New York University School of Medicine, New York, NY 10016, USADepartment of Surgery, Columbia University College of Physicians and Surgeons at Harlem Hospital, New York, NY 10037, USADepartment of Surgery, Columbia University College of Physicians and Surgeons at Harlem Hospital, New York, NY 10037, USADepartment of Surgery, Columbia University College of Physicians and Surgeons at Harlem Hospital, New York, NY 10037, USADepartment of Cardiothoracic Surgery, Harlem Hospital Center, New York, NY 10037, USADiffuse idiopathic pulmonary neuroendocrine cell hyperplasia (DIPNECH) is a rare clinical condition with only about 100 cases reported in the literature. It is characterized by primary hyperplasia of pulmonary neuroendocrine cells (PNECs) which are specialized epithelial cells located throughout the entire respiratory tract, from the trachea to the terminal airways. DIPNECH appears in various forms that include diffuse proliferation of scattered neuroendocrine cells, small nodules, or a linear proliferation. It is usually seen in middle-aged, nonsmoking women with symptoms of cough, dyspnea, and wheezing. We present a 45-year-old, nonsmoking woman who presented with symptoms of DIPNECH associated with bilateral pulmonary nodules and left hilar adenopathy. Of interest, DIPNECH in our patient was associated with metastatic pulmonary carcinoids, papillary carcinoma of the left breast, oncocytoma and angiomyolipoma of her left kidney, and cortical nodules suggestive of tuberous sclerosis. She had video assisted thoracoscopic surgery (VATS), modified radical mastectomy with reconstruction, and radical nephrectomy. She is currently symptom-free most of the time with over two years of follow-up.http://dx.doi.org/10.1155/2015/318175
spellingShingle Godwin Ofikwu
Vishnu R. Mani
Ajai Rajabalan
Albert Adu
Leaque Ahmed
Dennis Vega
A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
Case Reports in Surgery
title A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
title_full A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
title_fullStr A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
title_full_unstemmed A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
title_short A Rare Case of Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
title_sort rare case of diffuse idiopathic pulmonary neuroendocrine cell hyperplasia
url http://dx.doi.org/10.1155/2015/318175
work_keys_str_mv AT godwinofikwu ararecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT vishnurmani ararecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT ajairajabalan ararecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT albertadu ararecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT leaqueahmed ararecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT dennisvega ararecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT godwinofikwu rarecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT vishnurmani rarecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT ajairajabalan rarecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT albertadu rarecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT leaqueahmed rarecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia
AT dennisvega rarecaseofdiffuseidiopathicpulmonaryneuroendocrinecellhyperplasia