NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTS

Neuroendocrine tumours of the appendix (aNET) are slow-growing, indolent tumours that have an excellent prognosis and rarely show regional nodal metastases. They account for 0.1% of malignant tumours in children. The treatment and follow-up of aNET in children is not standardised. Appendectomy alone...

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Main Authors: Neža Salobir, Janez Jazbec, Jože Maučec
Format: Article
Language:Slovenian
Published: The Society for Children with Metabolic Disorders 2024-12-01
Series:Slovenska pediatrija
Subjects:
Online Access: http://www.slovenskapediatrija.si/Portals/0/Clanki/2024/Slovpediatr-2024-4-01en.pdf
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author Neža Salobir
Janez Jazbec
Jože Maučec
author_facet Neža Salobir
Janez Jazbec
Jože Maučec
author_sort Neža Salobir
collection DOAJ
description Neuroendocrine tumours of the appendix (aNET) are slow-growing, indolent tumours that have an excellent prognosis and rarely show regional nodal metastases. They account for 0.1% of malignant tumours in children. The treatment and follow-up of aNET in children is not standardised. Appendectomy alone is considered curative in most patients, while a more aggressive surgical approach is warranted for incompletely removed tumours or tumours larger than 2 cm. In the last 11.5 years, 23 children and adolescents were diagnosed with aNET in Slovenia.
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issn 1318-4423
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language Slovenian
publishDate 2024-12-01
publisher The Society for Children with Metabolic Disorders
record_format Article
series Slovenska pediatrija
spelling doaj-art-26ce28b2d6f44cbba09d80be266b9cf02025-08-20T02:52:26ZslvThe Society for Children with Metabolic DisordersSlovenska pediatrija1318-44232712-39602024-12-0131417417910.38031/slovpediatr-2024-4-01en13184423NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTSNeža Salobir0Janez Jazbec1Jože Maučec2 Zdravstveni dom Ljubljana, Ljubljana, Slovenija Klinični oddelek za otroško hematologijo in onkologijo, Pediatrična klinika, Univerzitetni klinični center Ljubljana, Ljubljana, Slovenija in Katedra za pediatrijo, Medicinska fakulteta, Univerza v Ljubljani, Ljubljana, Slovenija Klinični oddelek za otroško kirurgijo, Kirurška klinika, Univerzitetni klinični center Ljubljana, Ljubljana, Slovenija Neuroendocrine tumours of the appendix (aNET) are slow-growing, indolent tumours that have an excellent prognosis and rarely show regional nodal metastases. They account for 0.1% of malignant tumours in children. The treatment and follow-up of aNET in children is not standardised. Appendectomy alone is considered curative in most patients, while a more aggressive surgical approach is warranted for incompletely removed tumours or tumours larger than 2 cm. In the last 11.5 years, 23 children and adolescents were diagnosed with aNET in Slovenia. http://www.slovenskapediatrija.si/Portals/0/Clanki/2024/Slovpediatr-2024-4-01en.pdf appendixneuroendocrine tumourcarcinoidchild
spellingShingle Neža Salobir
Janez Jazbec
Jože Maučec
NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTS
Slovenska pediatrija
appendix
neuroendocrine tumour
carcinoid
child
title NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTS
title_full NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTS
title_fullStr NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTS
title_full_unstemmed NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTS
title_short NEUROENDOCRINE TUMOURS OF THE APPENDIX IN CHILDREN AND ADOLESCENTS
title_sort neuroendocrine tumours of the appendix in children and adolescents
topic appendix
neuroendocrine tumour
carcinoid
child
url http://www.slovenskapediatrija.si/Portals/0/Clanki/2024/Slovpediatr-2024-4-01en.pdf
work_keys_str_mv AT nezasalobir neuroendocrinetumoursoftheappendixinchildrenandadolescents
AT janezjazbec neuroendocrinetumoursoftheappendixinchildrenandadolescents
AT jozemaucec neuroendocrinetumoursoftheappendixinchildrenandadolescents