CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION

Idiopathic pulmonary arterial hypertension (IPAH) is a rare cardiovascular disease of unknown etiology, characterized by pulmonary vascular resistance (PVR) and pulmonary artery pressure (PAP) increase due to pronounced remodeling of small pulmonary arteries and arterioles, with progressive deterior...

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Main Authors: T. V. Martynyuk, M. A. Saidova, N. M. Danilov, V. K. Lazutkina, I. Ye. Chazova
Format: Article
Language:Russian
Published: InterMedservice 2015-12-01
Series:Евразийский Кардиологический Журнал
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Online Access:https://www.heartj.asia/jour/article/view/5655
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author T. V. Martynyuk
M. A. Saidova
N. M. Danilov
V. K. Lazutkina
I. Ye. Chazova
author_facet T. V. Martynyuk
M. A. Saidova
N. M. Danilov
V. K. Lazutkina
I. Ye. Chazova
author_sort T. V. Martynyuk
collection DOAJ
description Idiopathic pulmonary arterial hypertension (IPAH) is a rare cardiovascular disease of unknown etiology, characterized by pulmonary vascular resistance (PVR) and pulmonary artery pressure (PAP) increase due to pronounced remodeling of small pulmonary arteries and arterioles, with progressive deterioration and the rapid development of right ventricle failure. The key pathogenetic feature is the endothelial dysfunction, which leads to the development of vasoconstriction, thrombosis in situ, proliferative and inflammatory changes in the lung microvasculature. Optimization of drug therapy is associated with the clinical implementation of highly effective pathogenetic drugs which act on the main disease targets - activation of endothelin-1 (ET-1) system, the lack of endogenous prostacyclin and nitric oxide. The role of ET-1 as a powerful vasoconstrictor that induces cell proliferation and differentiation, production of cytokines, growth factors, biologically active substances. Endothelin receptor antagonists (ERA) represents the important class of PAH-specific therapy, including two non-selective ERAs-nonselective bosentan and selective ambrizentan. Presented clinical case demonstrates the long-term reliable efficacy and safety of ambrizentan for 10 years in the IPAH patient with the baseline functional class III (WHO).
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publishDate 2015-12-01
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series Евразийский Кардиологический Журнал
spelling doaj-art-259fc0a6110245f3a135f9cb18ea29ef2025-08-20T03:59:12ZrusInterMedserviceЕвразийский Кардиологический Журнал2225-16852305-07482015-12-0104485510.38109/2225-1685-2015-4-48-555652CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSIONT. V. Martynyuk0M. A. Saidova1N. M. Danilov2V. K. Lazutkina3I. Ye. Chazova4Russian cardiological research and production complex Ministry of HealthRussian cardiological research and production complex Ministry of HealthRussian cardiological research and production complex Ministry of HealthRussian cardiological research and production complex Ministry of HealthRussian cardiological research and production complex Ministry of HealthIdiopathic pulmonary arterial hypertension (IPAH) is a rare cardiovascular disease of unknown etiology, characterized by pulmonary vascular resistance (PVR) and pulmonary artery pressure (PAP) increase due to pronounced remodeling of small pulmonary arteries and arterioles, with progressive deterioration and the rapid development of right ventricle failure. The key pathogenetic feature is the endothelial dysfunction, which leads to the development of vasoconstriction, thrombosis in situ, proliferative and inflammatory changes in the lung microvasculature. Optimization of drug therapy is associated with the clinical implementation of highly effective pathogenetic drugs which act on the main disease targets - activation of endothelin-1 (ET-1) system, the lack of endogenous prostacyclin and nitric oxide. The role of ET-1 as a powerful vasoconstrictor that induces cell proliferation and differentiation, production of cytokines, growth factors, biologically active substances. Endothelin receptor antagonists (ERA) represents the important class of PAH-specific therapy, including two non-selective ERAs-nonselective bosentan and selective ambrizentan. Presented clinical case demonstrates the long-term reliable efficacy and safety of ambrizentan for 10 years in the IPAH patient with the baseline functional class III (WHO).https://www.heartj.asia/jour/article/view/5655idiopathic pulmonary hypertensionendothelin-1endothelin receptor antagonistsambrisentanидиопатическая лёгочная гипертензияэндотелин-1антагонисты рецепторов эндотелинаамбризентан
spellingShingle T. V. Martynyuk
M. A. Saidova
N. M. Danilov
V. K. Lazutkina
I. Ye. Chazova
CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION
Евразийский Кардиологический Журнал
idiopathic pulmonary hypertension
endothelin-1
endothelin receptor antagonists
ambrisentan
идиопатическая лёгочная гипертензия
эндотелин-1
антагонисты рецепторов эндотелина
амбризентан
title CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION
title_full CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION
title_fullStr CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION
title_full_unstemmed CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION
title_short CLINICAL CASE OF SUCCESSFUL 10-YEAR AMBRIZENTAN TREATMENT OF THE PATIENT WITH IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION
title_sort clinical case of successful 10 year ambrizentan treatment of the patient with idiopathic pulmonary arterial hypertension
topic idiopathic pulmonary hypertension
endothelin-1
endothelin receptor antagonists
ambrisentan
идиопатическая лёгочная гипертензия
эндотелин-1
антагонисты рецепторов эндотелина
амбризентан
url https://www.heartj.asia/jour/article/view/5655
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