A novel mutation leading to a deletion in the SH3 domain of Bruton's tyrosine kinase

X-linked agammaglobulinemia (XLA) is a primary B cell immunodeficiency disorder, caused by a defect in the Bruton tyrosine kinase (BTK) gene. Here, we describe a novel four base pair mutation (838delGAGT) in intron 9 of the BTK gene leading to the skipping of exon 9 in a 2.5-year-old boy with...

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Bibliographic Details
Main Authors: Lütfiye Mesci, Hilal Ozdag, Tuba Turul, Fügen Ersoy, Ilhan Tezcan, Ozden Sanal
Format: Article
Language:English
Published: Hacettepe University Institute of Child Health 2006-10-01
Series:The Turkish Journal of Pediatrics
Online Access:https://turkjpediatr.org/article/view/2661
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Summary:X-linked agammaglobulinemia (XLA) is a primary B cell immunodeficiency disorder, caused by a defect in the Bruton tyrosine kinase (BTK) gene. Here, we describe a novel four base pair mutation (838delGAGT) in intron 9 of the BTK gene leading to the skipping of exon 9 in a 2.5-year-old boy with this disorder.
ISSN:0041-4301
2791-6421