Adult-onset Renal Neuroblastoma: Case Report and Literature Review
Neuroblastoma is an extremely rare neoplasm in adults, with a poorer prognosis compared to pediatric neuroblastoma. Due to its rarity, there are no specific treatment guidelines for adult neuroblastoma. Here, we report a case of adult renal neuroblastoma presenting initially with painless and gross...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2024-12-01
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Series: | Journal of Cancer Research and Practice |
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Online Access: | https://journals.lww.com/10.4103/ejcrp.eJCRP-D-24-00017 |
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author | Yao-Ren Yang Cih-En Huang |
author_facet | Yao-Ren Yang Cih-En Huang |
author_sort | Yao-Ren Yang |
collection | DOAJ |
description | Neuroblastoma is an extremely rare neoplasm in adults, with a poorer prognosis compared to pediatric neuroblastoma. Due to its rarity, there are no specific treatment guidelines for adult neuroblastoma. Here, we report a case of adult renal neuroblastoma presenting initially with painless and gross hematuria. Enhanced computed tomography revealed an infiltrative, heterogeneously enhanced renal mass at the lower pole of the right kidney, accompanied by regional lymphadenopathies. The initial impression was renal cell carcinoma, and a right nephroureterectomy with regional lymph node dissection was performed. Pathologic examination confirmed the diagnosis of primary renal neuroblastoma with a differentiating subtype. The patient was classified as having International Neuroblastoma Staging System stage 2B or International Neuroblastoma Risk Group Staging System stage L2. The patient underwent six courses of adjuvant chemotherapy, and no disease recurrence was observed during a 7-year follow-up period. |
format | Article |
id | doaj-art-219dc0687d8646408f4b24c6236dbbf5 |
institution | Kabale University |
issn | 2311-3006 |
language | English |
publishDate | 2024-12-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Journal of Cancer Research and Practice |
spelling | doaj-art-219dc0687d8646408f4b24c6236dbbf52025-01-10T12:26:49ZengWolters Kluwer Medknow PublicationsJournal of Cancer Research and Practice2311-30062024-12-0111415515810.4103/ejcrp.eJCRP-D-24-00017Adult-onset Renal Neuroblastoma: Case Report and Literature ReviewYao-Ren YangCih-En HuangNeuroblastoma is an extremely rare neoplasm in adults, with a poorer prognosis compared to pediatric neuroblastoma. Due to its rarity, there are no specific treatment guidelines for adult neuroblastoma. Here, we report a case of adult renal neuroblastoma presenting initially with painless and gross hematuria. Enhanced computed tomography revealed an infiltrative, heterogeneously enhanced renal mass at the lower pole of the right kidney, accompanied by regional lymphadenopathies. The initial impression was renal cell carcinoma, and a right nephroureterectomy with regional lymph node dissection was performed. Pathologic examination confirmed the diagnosis of primary renal neuroblastoma with a differentiating subtype. The patient was classified as having International Neuroblastoma Staging System stage 2B or International Neuroblastoma Risk Group Staging System stage L2. The patient underwent six courses of adjuvant chemotherapy, and no disease recurrence was observed during a 7-year follow-up period.https://journals.lww.com/10.4103/ejcrp.eJCRP-D-24-00017adultchemotherapykidneynephrectomyneuroblastoma |
spellingShingle | Yao-Ren Yang Cih-En Huang Adult-onset Renal Neuroblastoma: Case Report and Literature Review Journal of Cancer Research and Practice adult chemotherapy kidney nephrectomy neuroblastoma |
title | Adult-onset Renal Neuroblastoma: Case Report and Literature Review |
title_full | Adult-onset Renal Neuroblastoma: Case Report and Literature Review |
title_fullStr | Adult-onset Renal Neuroblastoma: Case Report and Literature Review |
title_full_unstemmed | Adult-onset Renal Neuroblastoma: Case Report and Literature Review |
title_short | Adult-onset Renal Neuroblastoma: Case Report and Literature Review |
title_sort | adult onset renal neuroblastoma case report and literature review |
topic | adult chemotherapy kidney nephrectomy neuroblastoma |
url | https://journals.lww.com/10.4103/ejcrp.eJCRP-D-24-00017 |
work_keys_str_mv | AT yaorenyang adultonsetrenalneuroblastomacasereportandliteraturereview AT cihenhuang adultonsetrenalneuroblastomacasereportandliteraturereview |