Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature
Ewing's sarcoma (EWS) and peripheral primitive neuroectodermal tumor (pPNET) are small round cell malignancies that develop in soft tissue and bone. They very rarely affect newborns. A diagnosis of EWS/pPNET depends mainly on immunohistochemistry and molecular/genetic assays. Since these tumors...
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| Format: | Article |
| Language: | English |
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Elsevier
2016-10-01
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| Series: | Pediatrics and Neonatology |
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| Online Access: | http://www.sciencedirect.com/science/article/pii/S1875957213002349 |
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| _version_ | 1849724139337678848 |
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| author | Shu-Guang Jin Xiao-Ping Jiang Lin Zhong |
| author_facet | Shu-Guang Jin Xiao-Ping Jiang Lin Zhong |
| author_sort | Shu-Guang Jin |
| collection | DOAJ |
| description | Ewing's sarcoma (EWS) and peripheral primitive neuroectodermal tumor (pPNET) are small round cell malignancies that develop in soft tissue and bone. They very rarely affect newborns. A diagnosis of EWS/pPNET depends mainly on immunohistochemistry and molecular/genetic assays. Since these tumors are highly aggressive, patient prognosis is typically very poor, and treatment remains a challenge. Here, we report a 13-day-old newborn diagnosed with congenital EWS/pPNET and describe its treatment. |
| format | Article |
| id | doaj-art-20e570be0f5e4fc496582f810d5f55d2 |
| institution | DOAJ |
| issn | 1875-9572 |
| language | English |
| publishDate | 2016-10-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Pediatrics and Neonatology |
| spelling | doaj-art-20e570be0f5e4fc496582f810d5f55d22025-08-20T03:10:50ZengElsevierPediatrics and Neonatology1875-95722016-10-0157543643910.1016/j.pedneo.2013.11.002Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the LiteratureShu-Guang JinXiao-Ping JiangLin ZhongEwing's sarcoma (EWS) and peripheral primitive neuroectodermal tumor (pPNET) are small round cell malignancies that develop in soft tissue and bone. They very rarely affect newborns. A diagnosis of EWS/pPNET depends mainly on immunohistochemistry and molecular/genetic assays. Since these tumors are highly aggressive, patient prognosis is typically very poor, and treatment remains a challenge. Here, we report a 13-day-old newborn diagnosed with congenital EWS/pPNET and describe its treatment.http://www.sciencedirect.com/science/article/pii/S1875957213002349diagnosisEwing's sarcomanewbornperipheral primitive neuroectodermal tumorprognosistreatment |
| spellingShingle | Shu-Guang Jin Xiao-Ping Jiang Lin Zhong Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature Pediatrics and Neonatology diagnosis Ewing's sarcoma newborn peripheral primitive neuroectodermal tumor prognosis treatment |
| title | Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature |
| title_full | Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature |
| title_fullStr | Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature |
| title_full_unstemmed | Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature |
| title_short | Congenital Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature |
| title_sort | congenital ewing s sarcoma peripheral primitive neuroectodermal tumor a case report and review of the literature |
| topic | diagnosis Ewing's sarcoma newborn peripheral primitive neuroectodermal tumor prognosis treatment |
| url | http://www.sciencedirect.com/science/article/pii/S1875957213002349 |
| work_keys_str_mv | AT shuguangjin congenitalewingssarcomaperipheralprimitiveneuroectodermaltumoracasereportandreviewoftheliterature AT xiaopingjiang congenitalewingssarcomaperipheralprimitiveneuroectodermaltumoracasereportandreviewoftheliterature AT linzhong congenitalewingssarcomaperipheralprimitiveneuroectodermaltumoracasereportandreviewoftheliterature |