Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantation

Background Evidence on maintenance therapy following frontline induction is sparse in primary light-chain amyloidosis (AL), especially for those who do not undergo autologous haematopoietic stem cell transplantation (ASCT).Methods We enrolled primary AL patients who achieved at least haematologic ve...

Full description

Saved in:
Bibliographic Details
Main Authors: Wenjing Wang, Jing Li, Tianhong Xu, Yang Yang, Chenqi Yu, Pu Wang, Chi Zhou, Peng Liu
Format: Article
Language:English
Published: Taylor & Francis Group 2024-12-01
Series:Annals of Medicine
Subjects:
Online Access:https://www.tandfonline.com/doi/10.1080/07853890.2024.2418339
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850181295848554496
author Wenjing Wang
Jing Li
Tianhong Xu
Yang Yang
Chenqi Yu
Pu Wang
Chi Zhou
Peng Liu
author_facet Wenjing Wang
Jing Li
Tianhong Xu
Yang Yang
Chenqi Yu
Pu Wang
Chi Zhou
Peng Liu
author_sort Wenjing Wang
collection DOAJ
description Background Evidence on maintenance therapy following frontline induction is sparse in primary light-chain amyloidosis (AL), especially for those who do not undergo autologous haematopoietic stem cell transplantation (ASCT).Methods We enrolled primary AL patients who achieved at least haematologic very good partial response (VGPR) by the 4th month at the frontline from December 2008 to June 2023 at Zhongshan Hospital, Fudan University. Those who followed maintenance therapy were identified as the maintenance group (n = 44), whereas those entering the observational phase were classified as the observational group (n = 24).Results After 7.2(interquartile range, 4.7–18.6) months of maintenance therapy, 9(20.5%), 14(31.8%) and 5 (11.4%) patients achieved improvement in haematologic, cardiac and renal response respectively. Five (11.4%) patients had minimal residual disease (MRD) response conversion from positive to negative based on maintenance therapy. In the observation group, none of the patients had haematologic response improvement, with 3(12.5%) and 1(4.2%) patient showing cardiac and renal response improvement during follow-up.Conclusion This study identified the clinical benefits of maintenance therapy in patients with AL who did not undergo ASCT in real-world practice.
format Article
id doaj-art-20d21c08dd2f4e4aaab09c5dd05aa942
institution OA Journals
issn 0785-3890
1365-2060
language English
publishDate 2024-12-01
publisher Taylor & Francis Group
record_format Article
series Annals of Medicine
spelling doaj-art-20d21c08dd2f4e4aaab09c5dd05aa9422025-08-20T02:17:57ZengTaylor & Francis GroupAnnals of Medicine0785-38901365-20602024-12-0156110.1080/07853890.2024.2418339Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantationWenjing Wang0Jing Li1Tianhong Xu2Yang Yang3Chenqi Yu4Pu Wang5Chi Zhou6Peng Liu7Department of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaDepartment of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaDepartment of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaDepartment of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaDepartment of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaDepartment of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaDepartment of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaDepartment of Hematology, Zhongshan Hospital Fudan University, Shanghai, ChinaBackground Evidence on maintenance therapy following frontline induction is sparse in primary light-chain amyloidosis (AL), especially for those who do not undergo autologous haematopoietic stem cell transplantation (ASCT).Methods We enrolled primary AL patients who achieved at least haematologic very good partial response (VGPR) by the 4th month at the frontline from December 2008 to June 2023 at Zhongshan Hospital, Fudan University. Those who followed maintenance therapy were identified as the maintenance group (n = 44), whereas those entering the observational phase were classified as the observational group (n = 24).Results After 7.2(interquartile range, 4.7–18.6) months of maintenance therapy, 9(20.5%), 14(31.8%) and 5 (11.4%) patients achieved improvement in haematologic, cardiac and renal response respectively. Five (11.4%) patients had minimal residual disease (MRD) response conversion from positive to negative based on maintenance therapy. In the observation group, none of the patients had haematologic response improvement, with 3(12.5%) and 1(4.2%) patient showing cardiac and renal response improvement during follow-up.Conclusion This study identified the clinical benefits of maintenance therapy in patients with AL who did not undergo ASCT in real-world practice.https://www.tandfonline.com/doi/10.1080/07853890.2024.2418339Hematologic responselight chain amyloidosismaintenance therapyminimal residual diseaseorgan response
spellingShingle Wenjing Wang
Jing Li
Tianhong Xu
Yang Yang
Chenqi Yu
Pu Wang
Chi Zhou
Peng Liu
Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantation
Annals of Medicine
Hematologic response
light chain amyloidosis
maintenance therapy
minimal residual disease
organ response
title Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantation
title_full Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantation
title_fullStr Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantation
title_full_unstemmed Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantation
title_short Maintenance therapy promotes profound organ and haematologic response in light-chain amyloidosis patients not undergoing autologous stem cell transplantation
title_sort maintenance therapy promotes profound organ and haematologic response in light chain amyloidosis patients not undergoing autologous stem cell transplantation
topic Hematologic response
light chain amyloidosis
maintenance therapy
minimal residual disease
organ response
url https://www.tandfonline.com/doi/10.1080/07853890.2024.2418339
work_keys_str_mv AT wenjingwang maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation
AT jingli maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation
AT tianhongxu maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation
AT yangyang maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation
AT chenqiyu maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation
AT puwang maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation
AT chizhou maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation
AT pengliu maintenancetherapypromotesprofoundorganandhaematologicresponseinlightchainamyloidosispatientsnotundergoingautologousstemcelltransplantation