Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the Literature
Behçet's disease (BD) is a multisystem vascular inflammatory disease with several clinical manifestations. Intracranial aneurysms are an extremely rare but nevertheless severe complication of BD. We report a case of a 44-year-old man. The diagnosis of BD was made based on the presence of recurr...
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| Format: | Article |
| Language: | English |
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Wiley
2013-01-01
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| Series: | Case Reports in Neurological Medicine |
| Online Access: | http://dx.doi.org/10.1155/2013/812158 |
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| author | Samia Younes Yosra Cherif Narjes Mokni Olfa Berriche Baha Zantour Amel Boughammoura Mahbouba Frih-Ayed Saida Jerbi Mohamed Habib Sfar |
| author_facet | Samia Younes Yosra Cherif Narjes Mokni Olfa Berriche Baha Zantour Amel Boughammoura Mahbouba Frih-Ayed Saida Jerbi Mohamed Habib Sfar |
| author_sort | Samia Younes |
| collection | DOAJ |
| description | Behçet's disease (BD) is a multisystem vascular inflammatory disease with several clinical manifestations. Intracranial aneurysms are an extremely rare but nevertheless severe complication of BD. We report a case of a 44-year-old man. The diagnosis of BD was made based on the presence of recurrent oral aphthous ulcers and positive human leukocyte antigen (HLA-) B51 in the absence of evidence of other diseases. MRI showed an ancient ischemic right capsulolenticular lesion, subacute white matter hypersignals of the left capsule lenticular region, and multiple arterial aneurysms. The patient underwent two-month systemic high-dose corticosteroids and immunosuppressive therapy associated with severe neurological deficiency upon admission and severe impairment upon discharge. A thorough review of the literature showed 20 case reports of intracranial aneurysms in BD. |
| format | Article |
| id | doaj-art-20acc8163f9b4b22ab09a569cf030a63 |
| institution | Kabale University |
| issn | 2090-6668 2090-6676 |
| language | English |
| publishDate | 2013-01-01 |
| publisher | Wiley |
| record_format | Article |
| series | Case Reports in Neurological Medicine |
| spelling | doaj-art-20acc8163f9b4b22ab09a569cf030a632025-02-03T01:01:12ZengWileyCase Reports in Neurological Medicine2090-66682090-66762013-01-01201310.1155/2013/812158812158Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the LiteratureSamia Younes0Yosra Cherif1Narjes Mokni2Olfa Berriche3Baha Zantour4Amel Boughammoura5Mahbouba Frih-Ayed6Saida Jerbi7Mohamed Habib Sfar8Department of Endocrinology and Internal Medicine, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, TunisiaDepartment of Endocrinology and Internal Medicine, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, TunisiaDepartment of Endocrinology and Internal Medicine, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, TunisiaDepartment of Endocrinology and Internal Medicine, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, TunisiaDepartment of Endocrinology and Internal Medicine, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, TunisiaDepartment of Neurology, Fattouma Bourguiba University Hospital of Monastir, 1st June Street, 5000 Monastir, TunisiaDepartment of Neurology, Fattouma Bourguiba University Hospital of Monastir, 1st June Street, 5000 Monastir, TunisiaDepartment of Medical Imagery, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, TunisiaDepartment of Endocrinology and Internal Medicine, Tahar Sfar University Hospital of Mahdia, Hiboun District, 5100 Mahdia, TunisiaBehçet's disease (BD) is a multisystem vascular inflammatory disease with several clinical manifestations. Intracranial aneurysms are an extremely rare but nevertheless severe complication of BD. We report a case of a 44-year-old man. The diagnosis of BD was made based on the presence of recurrent oral aphthous ulcers and positive human leukocyte antigen (HLA-) B51 in the absence of evidence of other diseases. MRI showed an ancient ischemic right capsulolenticular lesion, subacute white matter hypersignals of the left capsule lenticular region, and multiple arterial aneurysms. The patient underwent two-month systemic high-dose corticosteroids and immunosuppressive therapy associated with severe neurological deficiency upon admission and severe impairment upon discharge. A thorough review of the literature showed 20 case reports of intracranial aneurysms in BD.http://dx.doi.org/10.1155/2013/812158 |
| spellingShingle | Samia Younes Yosra Cherif Narjes Mokni Olfa Berriche Baha Zantour Amel Boughammoura Mahbouba Frih-Ayed Saida Jerbi Mohamed Habib Sfar Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the Literature Case Reports in Neurological Medicine |
| title | Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the Literature |
| title_full | Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the Literature |
| title_fullStr | Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the Literature |
| title_full_unstemmed | Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the Literature |
| title_short | Cerebral Aneurysms: A Rare Feature of Behçet's Disease—A Case Report and Review of the Literature |
| title_sort | cerebral aneurysms a rare feature of behcet s disease a case report and review of the literature |
| url | http://dx.doi.org/10.1155/2013/812158 |
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