Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right Ventricle

Pulmonary valve atresia (PVA) is a fatal pediatric cardiac condition and commonly associated with other anomalies such as double outlet right ventricle (DORV). There is a disagreement over the best surgical strategy for treating PVA in conjunction with DORV. Prematurely born neonates are considered...

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Main Authors: Mohammed Rasool Hussein, Maysam Yousif Abed, Nabeeha Najatee Akram
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-12-01
Series:Mustansiriya Medical Journal
Subjects:
Online Access:https://journals.lww.com/10.4103/mj.mj_33_24
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author Mohammed Rasool Hussein
Maysam Yousif Abed
Nabeeha Najatee Akram
author_facet Mohammed Rasool Hussein
Maysam Yousif Abed
Nabeeha Najatee Akram
author_sort Mohammed Rasool Hussein
collection DOAJ
description Pulmonary valve atresia (PVA) is a fatal pediatric cardiac condition and commonly associated with other anomalies such as double outlet right ventricle (DORV). There is a disagreement over the best surgical strategy for treating PVA in conjunction with DORV. Prematurely born neonates are considered high-risk group for early pulmonary artery shunt surgery as the staged repair is found to be associated with higher interstage mortality, while the primary repair may lead to frequent postrepair reinterventions due to the presence of associated developmental anomalies. In this report, we present the successful results of using percutaneous transcatheterization in a high-risk patient; a 6-h premature neonate who had DORV, PVA with other anomalies including situs inversus, levocardia, D-malposed great arteries without patent ductus arteriosus. This rapid interventional catheterization offered to the neonate has an immense advantage of lifesaving and the protection against the remolding effect on the right ventricle that usually develops when waiting for the palliative procedures or surgery to take place.
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issn 2070-1128
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publishDate 2024-12-01
publisher Wolters Kluwer Medknow Publications
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series Mustansiriya Medical Journal
spelling doaj-art-1f95c8956a4f49759cc028b7610557622025-01-14T06:49:04ZengWolters Kluwer Medknow PublicationsMustansiriya Medical Journal2070-11282227-40812024-12-012329810010.4103/mj.mj_33_24Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right VentricleMohammed Rasool HusseinMaysam Yousif AbedNabeeha Najatee AkramPulmonary valve atresia (PVA) is a fatal pediatric cardiac condition and commonly associated with other anomalies such as double outlet right ventricle (DORV). There is a disagreement over the best surgical strategy for treating PVA in conjunction with DORV. Prematurely born neonates are considered high-risk group for early pulmonary artery shunt surgery as the staged repair is found to be associated with higher interstage mortality, while the primary repair may lead to frequent postrepair reinterventions due to the presence of associated developmental anomalies. In this report, we present the successful results of using percutaneous transcatheterization in a high-risk patient; a 6-h premature neonate who had DORV, PVA with other anomalies including situs inversus, levocardia, D-malposed great arteries without patent ductus arteriosus. This rapid interventional catheterization offered to the neonate has an immense advantage of lifesaving and the protection against the remolding effect on the right ventricle that usually develops when waiting for the palliative procedures or surgery to take place.https://journals.lww.com/10.4103/mj.mj_33_24pulmonary valve atresiaright ventricular outflow obstructionstent
spellingShingle Mohammed Rasool Hussein
Maysam Yousif Abed
Nabeeha Najatee Akram
Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right Ventricle
Mustansiriya Medical Journal
pulmonary valve atresia
right ventricular outflow obstruction
stent
title Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right Ventricle
title_full Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right Ventricle
title_fullStr Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right Ventricle
title_full_unstemmed Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right Ventricle
title_short Right Ventricular Outflow Tract Perforation and Stenting for a Premature Neonate with Pulmonary Valve Atresia and Double Outlet Right Ventricle
title_sort right ventricular outflow tract perforation and stenting for a premature neonate with pulmonary valve atresia and double outlet right ventricle
topic pulmonary valve atresia
right ventricular outflow obstruction
stent
url https://journals.lww.com/10.4103/mj.mj_33_24
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AT nabeehanajateeakram rightventricularoutflowtractperforationandstentingforaprematureneonatewithpulmonaryvalveatresiaanddoubleoutletrightventricle