Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early clues

Vanishing bile duct syndrome is a specific pathologic process characterized by ductopenia and intrahepatic cholestasis, which may be a unique paraneoplastic syndrome of Hodgkin’s lymphoma with an unfavorable prognosis. We report a 34-year-old woman with acute jaundice and lymphadenopathy, which was...

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Main Authors: Shiyu Ma, Dali Cai, Yuan Miao, Baocheng Deng, Xiaojing Yan, Ran Gao
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-05-01
Series:Frontiers in Immunology
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Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2025.1561110/full
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author Shiyu Ma
Dali Cai
Yuan Miao
Baocheng Deng
Xiaojing Yan
Ran Gao
author_facet Shiyu Ma
Dali Cai
Yuan Miao
Baocheng Deng
Xiaojing Yan
Ran Gao
author_sort Shiyu Ma
collection DOAJ
description Vanishing bile duct syndrome is a specific pathologic process characterized by ductopenia and intrahepatic cholestasis, which may be a unique paraneoplastic syndrome of Hodgkin’s lymphoma with an unfavorable prognosis. We report a 34-year-old woman with acute jaundice and lymphadenopathy, which was subsequently confirmed to be Hodgkin’s lymphoma with concurrent vanishing bile duct syndrome based on a liver biopsy. The patient agreed to combination chemotherapy with brentuximab vedotin and achieved a complete response. Liver function recovered within 4 months. This article reviews the literature and provides insight for addressing similar clinical challenges.
format Article
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issn 1664-3224
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publishDate 2025-05-01
publisher Frontiers Media S.A.
record_format Article
series Frontiers in Immunology
spelling doaj-art-1ebcf3acd1964fa6bb3ac28effe3c57f2025-08-20T01:55:27ZengFrontiers Media S.A.Frontiers in Immunology1664-32242025-05-011610.3389/fimmu.2025.15611101561110Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early cluesShiyu Ma0Dali Cai1Yuan Miao2Baocheng Deng3Xiaojing Yan4Ran Gao5Department of Hematology, The First Hospital of China Medical University, Shenyang, Liaoning, ChinaDepartment of Hematology, The First Hospital of China Medical University, Shenyang, Liaoning, ChinaDepartment of Pathology, The First Hospital of China Medical University, Shenyang, Liaoning, ChinaThe Second Department of Infectious Diseases, The First Hospital of China Medical University, Shenyang, Liaoning, ChinaDepartment of Hematology, The First Hospital of China Medical University, Shenyang, Liaoning, ChinaDepartment of Hematology, The First Hospital of China Medical University, Shenyang, Liaoning, ChinaVanishing bile duct syndrome is a specific pathologic process characterized by ductopenia and intrahepatic cholestasis, which may be a unique paraneoplastic syndrome of Hodgkin’s lymphoma with an unfavorable prognosis. We report a 34-year-old woman with acute jaundice and lymphadenopathy, which was subsequently confirmed to be Hodgkin’s lymphoma with concurrent vanishing bile duct syndrome based on a liver biopsy. The patient agreed to combination chemotherapy with brentuximab vedotin and achieved a complete response. Liver function recovered within 4 months. This article reviews the literature and provides insight for addressing similar clinical challenges.https://www.frontiersin.org/articles/10.3389/fimmu.2025.1561110/fulljaundiceHodgkin’s lymphomavanishing bile duct syndromeliver biopsybrentuximab vedotin (BV)
spellingShingle Shiyu Ma
Dali Cai
Yuan Miao
Baocheng Deng
Xiaojing Yan
Ran Gao
Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early clues
Frontiers in Immunology
jaundice
Hodgkin’s lymphoma
vanishing bile duct syndrome
liver biopsy
brentuximab vedotin (BV)
title Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early clues
title_full Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early clues
title_fullStr Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early clues
title_full_unstemmed Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early clues
title_short Case Report: Vanishing bile duct syndrome in Hodgkin’s lymphoma: a case highlighting jaundice and lymphadenopathy as early clues
title_sort case report vanishing bile duct syndrome in hodgkin s lymphoma a case highlighting jaundice and lymphadenopathy as early clues
topic jaundice
Hodgkin’s lymphoma
vanishing bile duct syndrome
liver biopsy
brentuximab vedotin (BV)
url https://www.frontiersin.org/articles/10.3389/fimmu.2025.1561110/full
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