Aortic atresia with complex aortic arch collateralization through the subclavian arteries

A term newborn boy was diagnosed with aortic atresia and ventricular septal defect with duplicated subclavian arteries bilaterally. Computed tomography angiography demonstrated highly unusual aortic arch vasculature. A diminutive aortic arch and complex head vessel anatomy precluded standard surgica...

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Main Authors: Saumya Kapoor, Thomas Knapp, Peace Madueme, Katherine T. Braley, Peter D. Wearden, Jennifer S. Nelson
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-11-01
Series:Annals of Pediatric Cardiology
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Online Access:https://journals.lww.com/10.4103/apc.apc_179_24
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author Saumya Kapoor
Thomas Knapp
Peace Madueme
Katherine T. Braley
Peter D. Wearden
Jennifer S. Nelson
author_facet Saumya Kapoor
Thomas Knapp
Peace Madueme
Katherine T. Braley
Peter D. Wearden
Jennifer S. Nelson
author_sort Saumya Kapoor
collection DOAJ
description A term newborn boy was diagnosed with aortic atresia and ventricular septal defect with duplicated subclavian arteries bilaterally. Computed tomography angiography demonstrated highly unusual aortic arch vasculature. A diminutive aortic arch and complex head vessel anatomy precluded standard surgical palliation with a Damus–Kaye–Stansel, arch reconstruction, and systemic to pulmonary artery shunt. Instead, the patient underwent placement of bilateral pulmonary artery bands and stenting of the patent arterial duct (PDA). At 2 months of age, the patient underwent PDA stent dilation. At 4 months of age, he underwent balloon angioplasty of pulmonary artery bands with transverse aortic stenting. At the most recent follow-up at 15 months of age, there was no significant growth of the aortic arch, and the patient was mildly hypertensive but otherwise hemodynamically stable. He is currently being evaluated for heart transplantation due to his complex vascular anatomy.
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institution Kabale University
issn 0974-2069
0974-5149
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publishDate 2024-11-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Annals of Pediatric Cardiology
spelling doaj-art-1eb3535148174946affb5b30bd4591d22025-08-20T03:48:46ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20690974-51492024-11-0117644144310.4103/apc.apc_179_24Aortic atresia with complex aortic arch collateralization through the subclavian arteriesSaumya KapoorThomas KnappPeace MaduemeKatherine T. BraleyPeter D. WeardenJennifer S. NelsonA term newborn boy was diagnosed with aortic atresia and ventricular septal defect with duplicated subclavian arteries bilaterally. Computed tomography angiography demonstrated highly unusual aortic arch vasculature. A diminutive aortic arch and complex head vessel anatomy precluded standard surgical palliation with a Damus–Kaye–Stansel, arch reconstruction, and systemic to pulmonary artery shunt. Instead, the patient underwent placement of bilateral pulmonary artery bands and stenting of the patent arterial duct (PDA). At 2 months of age, the patient underwent PDA stent dilation. At 4 months of age, he underwent balloon angioplasty of pulmonary artery bands with transverse aortic stenting. At the most recent follow-up at 15 months of age, there was no significant growth of the aortic arch, and the patient was mildly hypertensive but otherwise hemodynamically stable. He is currently being evaluated for heart transplantation due to his complex vascular anatomy.https://journals.lww.com/10.4103/apc.apc_179_24aortic valve atresiacomplex congenital heart diseaseinterventional palliation
spellingShingle Saumya Kapoor
Thomas Knapp
Peace Madueme
Katherine T. Braley
Peter D. Wearden
Jennifer S. Nelson
Aortic atresia with complex aortic arch collateralization through the subclavian arteries
Annals of Pediatric Cardiology
aortic valve atresia
complex congenital heart disease
interventional palliation
title Aortic atresia with complex aortic arch collateralization through the subclavian arteries
title_full Aortic atresia with complex aortic arch collateralization through the subclavian arteries
title_fullStr Aortic atresia with complex aortic arch collateralization through the subclavian arteries
title_full_unstemmed Aortic atresia with complex aortic arch collateralization through the subclavian arteries
title_short Aortic atresia with complex aortic arch collateralization through the subclavian arteries
title_sort aortic atresia with complex aortic arch collateralization through the subclavian arteries
topic aortic valve atresia
complex congenital heart disease
interventional palliation
url https://journals.lww.com/10.4103/apc.apc_179_24
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