Primary familial brain calcification: a clinical case

Primary familial brain calcification (familial idiopathic basal ganglia calcification, Fahr’s disease) is a rare neurodegenerative syndrome characterised by a symmetrical bilateral calcification in the basal ganglia, dentate nucleus, cerebral cortex, and other regions of the brain. The widespread us...

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Main Authors: Yu. A. Malyshenko, I. V. Soroko, D. V. Kober, R. S. Bogachev, A. E. Mityukov
Format: Article
Language:Russian
Published: Kemerovo State Medical University 2019-09-01
Series:Фундаментальная и клиническая медицина
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Online Access:https://fcm.kemsmu.ru/jour/article/view/170
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author Yu. A. Malyshenko
I. V. Soroko
D. V. Kober
R. S. Bogachev
A. E. Mityukov
author_facet Yu. A. Malyshenko
I. V. Soroko
D. V. Kober
R. S. Bogachev
A. E. Mityukov
author_sort Yu. A. Malyshenko
collection DOAJ
description Primary familial brain calcification (familial idiopathic basal ganglia calcification, Fahr’s disease) is a rare neurodegenerative syndrome characterised by a symmetrical bilateral calcification in the basal ganglia, dentate nucleus, cerebral cortex, and other regions of the brain. The widespread use of multislice computed tomography and magnetic resonance imaging increased the number of diagnosed cases, yet neither causes nor efficient treatment of this disease are known to date. Due to variable symptoms, primary familial brain calcification can resemble multiple neurological, mental, and endocrine disorders. Here we describe a case of a 38-year-old woman where timely multislice computed tomography led to the proper diagnosis and successful treatment.
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institution DOAJ
issn 2500-0764
2542-0941
language Russian
publishDate 2019-09-01
publisher Kemerovo State Medical University
record_format Article
series Фундаментальная и клиническая медицина
spelling doaj-art-1e75499c05c7427982be6ecac0eaa8b22025-08-20T02:49:10ZrusKemerovo State Medical UniversityФундаментальная и клиническая медицина2500-07642542-09412019-09-014312813210.23946/2500-0764-2019-4-3-128-132169Primary familial brain calcification: a clinical caseYu. A. Malyshenko0I. V. Soroko1D. V. Kober2R. S. Bogachev3A. E. Mityukov4Kaliningrad Regional Clinical HospitalKaliningrad Regional Clinical HospitalKaliningrad Regional Clinical HospitalImmanuel Kant Baltic Federal UniversityImmanuel Kant Baltic Federal UniversityPrimary familial brain calcification (familial idiopathic basal ganglia calcification, Fahr’s disease) is a rare neurodegenerative syndrome characterised by a symmetrical bilateral calcification in the basal ganglia, dentate nucleus, cerebral cortex, and other regions of the brain. The widespread use of multislice computed tomography and magnetic resonance imaging increased the number of diagnosed cases, yet neither causes nor efficient treatment of this disease are known to date. Due to variable symptoms, primary familial brain calcification can resemble multiple neurological, mental, and endocrine disorders. Here we describe a case of a 38-year-old woman where timely multislice computed tomography led to the proper diagnosis and successful treatment.https://fcm.kemsmu.ru/jour/article/view/170hypoparathyroidismprimary familial brain calcificationidiopathic calcificationfahr’s diseasecalcification
spellingShingle Yu. A. Malyshenko
I. V. Soroko
D. V. Kober
R. S. Bogachev
A. E. Mityukov
Primary familial brain calcification: a clinical case
Фундаментальная и клиническая медицина
hypoparathyroidism
primary familial brain calcification
idiopathic calcification
fahr’s disease
calcification
title Primary familial brain calcification: a clinical case
title_full Primary familial brain calcification: a clinical case
title_fullStr Primary familial brain calcification: a clinical case
title_full_unstemmed Primary familial brain calcification: a clinical case
title_short Primary familial brain calcification: a clinical case
title_sort primary familial brain calcification a clinical case
topic hypoparathyroidism
primary familial brain calcification
idiopathic calcification
fahr’s disease
calcification
url https://fcm.kemsmu.ru/jour/article/view/170
work_keys_str_mv AT yuamalyshenko primaryfamilialbraincalcificationaclinicalcase
AT ivsoroko primaryfamilialbraincalcificationaclinicalcase
AT dvkober primaryfamilialbraincalcificationaclinicalcase
AT rsbogachev primaryfamilialbraincalcificationaclinicalcase
AT aemityukov primaryfamilialbraincalcificationaclinicalcase