A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.

Endoplasmic reticulum-associated degradation (ERAD) is a protein quality control pathway of fundamental importance to cellular homeostasis. Although multiple ERAD pathways exist for targeting topologically distinct substrates, all pathways require substrate ubiquitination. Here, we characterize a ke...

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Main Authors: Christopher E Smith, Yien Che Tsai, Yu-He Liang, Domarin Khago, Jennifer Mariano, Jess Li, Sergey G Tarasov, Emma Gergel, Borong Tsai, Matthew Villaneuva, Michelle E Clapp, Valentin Magidson, Raj Chari, R Andrew Byrd, Xinhua Ji, Allan M Weissman
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2021-12-01
Series:PLoS Biology
Online Access:https://journals.plos.org/plosbiology/article/file?id=10.1371/journal.pbio.3001474&type=printable
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author Christopher E Smith
Yien Che Tsai
Yu-He Liang
Domarin Khago
Jennifer Mariano
Jess Li
Sergey G Tarasov
Emma Gergel
Borong Tsai
Matthew Villaneuva
Michelle E Clapp
Valentin Magidson
Raj Chari
R Andrew Byrd
Xinhua Ji
Allan M Weissman
author_facet Christopher E Smith
Yien Che Tsai
Yu-He Liang
Domarin Khago
Jennifer Mariano
Jess Li
Sergey G Tarasov
Emma Gergel
Borong Tsai
Matthew Villaneuva
Michelle E Clapp
Valentin Magidson
Raj Chari
R Andrew Byrd
Xinhua Ji
Allan M Weissman
author_sort Christopher E Smith
collection DOAJ
description Endoplasmic reticulum-associated degradation (ERAD) is a protein quality control pathway of fundamental importance to cellular homeostasis. Although multiple ERAD pathways exist for targeting topologically distinct substrates, all pathways require substrate ubiquitination. Here, we characterize a key role for the UBE2G2 Binding Region (G2BR) of the ERAD accessory protein ancient ubiquitous protein 1 (AUP1) in ERAD pathways. This 27-amino acid (aa) region of AUP1 binds with high specificity and low nanomolar affinity to the backside of the ERAD ubiquitin-conjugating enzyme (E2) UBE2G2. The structure of the AUP1 G2BR (G2BRAUP1) in complex with UBE2G2 reveals an interface that includes a network of salt bridges, hydrogen bonds, and hydrophobic interactions essential for AUP1 function in cells. The G2BRAUP1 shares significant structural conservation with the G2BR found in the E3 ubiquitin ligase gp78 and in vitro can similarly allosterically activate ubiquitination in conjunction with ERAD E3s. In cells, AUP1 is uniquely required to maintain normal levels of UBE2G2; this is due to G2BRAUP1 binding to the E2 and preventing its rapid degradation. In addition, the G2BRAUP1 is required for both ER membrane recruitment of UBE2G2 and for its activation at the ER membrane. Thus, by binding to the backside of a critical ERAD E2, G2BRAUP1 plays multiple critical roles in ERAD.
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institution Kabale University
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publishDate 2021-12-01
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spelling doaj-art-1d1767c146ff4ca2be2d36cff2726f112025-08-20T03:44:40ZengPublic Library of Science (PLoS)PLoS Biology1544-91731545-78852021-12-011912e300147410.1371/journal.pbio.3001474A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.Christopher E SmithYien Che TsaiYu-He LiangDomarin KhagoJennifer MarianoJess LiSergey G TarasovEmma GergelBorong TsaiMatthew VillaneuvaMichelle E ClappValentin MagidsonRaj ChariR Andrew ByrdXinhua JiAllan M WeissmanEndoplasmic reticulum-associated degradation (ERAD) is a protein quality control pathway of fundamental importance to cellular homeostasis. Although multiple ERAD pathways exist for targeting topologically distinct substrates, all pathways require substrate ubiquitination. Here, we characterize a key role for the UBE2G2 Binding Region (G2BR) of the ERAD accessory protein ancient ubiquitous protein 1 (AUP1) in ERAD pathways. This 27-amino acid (aa) region of AUP1 binds with high specificity and low nanomolar affinity to the backside of the ERAD ubiquitin-conjugating enzyme (E2) UBE2G2. The structure of the AUP1 G2BR (G2BRAUP1) in complex with UBE2G2 reveals an interface that includes a network of salt bridges, hydrogen bonds, and hydrophobic interactions essential for AUP1 function in cells. The G2BRAUP1 shares significant structural conservation with the G2BR found in the E3 ubiquitin ligase gp78 and in vitro can similarly allosterically activate ubiquitination in conjunction with ERAD E3s. In cells, AUP1 is uniquely required to maintain normal levels of UBE2G2; this is due to G2BRAUP1 binding to the E2 and preventing its rapid degradation. In addition, the G2BRAUP1 is required for both ER membrane recruitment of UBE2G2 and for its activation at the ER membrane. Thus, by binding to the backside of a critical ERAD E2, G2BRAUP1 plays multiple critical roles in ERAD.https://journals.plos.org/plosbiology/article/file?id=10.1371/journal.pbio.3001474&type=printable
spellingShingle Christopher E Smith
Yien Che Tsai
Yu-He Liang
Domarin Khago
Jennifer Mariano
Jess Li
Sergey G Tarasov
Emma Gergel
Borong Tsai
Matthew Villaneuva
Michelle E Clapp
Valentin Magidson
Raj Chari
R Andrew Byrd
Xinhua Ji
Allan M Weissman
A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.
PLoS Biology
title A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.
title_full A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.
title_fullStr A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.
title_full_unstemmed A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.
title_short A structurally conserved site in AUP1 binds the E2 enzyme UBE2G2 and is essential for ER-associated degradation.
title_sort structurally conserved site in aup1 binds the e2 enzyme ube2g2 and is essential for er associated degradation
url https://journals.plos.org/plosbiology/article/file?id=10.1371/journal.pbio.3001474&type=printable
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