Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report
Biliary atresia (BA) is the most common cause of the obstructive type of neonatal cholestasis that requires prompt surgical intervention. About 10% of neonates with BA have other congenital anomalies, of which splenic malformation (BASM) is a well-known distinct sub-group. There is sparse literature...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2024-12-01
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| Series: | Indian Journal of Pathology and Microbiology |
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| Online Access: | https://journals.lww.com/10.4103/ijpm.ijpm_182_23 |
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| author | Raktim Mukherjee Aniket Halder Suman Kumar Das Suchandra Mukherjee Uttara Chatterjee |
| author_facet | Raktim Mukherjee Aniket Halder Suman Kumar Das Suchandra Mukherjee Uttara Chatterjee |
| author_sort | Raktim Mukherjee |
| collection | DOAJ |
| description | Biliary atresia (BA) is the most common cause of the obstructive type of neonatal cholestasis that requires prompt surgical intervention. About 10% of neonates with BA have other congenital anomalies, of which splenic malformation (BASM) is a well-known distinct sub-group. There is sparse literature on the association of duodenal atresia and ductal plate malformation (DPM) in patients of BASM. We describe a BASM associated with DPM and duodenal atresia in a 35-day-old infant, who succumbed at 40 days, before portoenterostomy could be performed. Duodenal atresia can be one of the associated malformations associated with BASM and ductal plate abnormalities. In our case, the child did not survive. |
| format | Article |
| id | doaj-art-1816264a5e7f49c3b160b0fd5bf74d9b |
| institution | Kabale University |
| issn | 0377-4929 0974-5130 |
| language | English |
| publishDate | 2024-12-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Pathology and Microbiology |
| spelling | doaj-art-1816264a5e7f49c3b160b0fd5bf74d9b2025-01-10T10:26:17ZengWolters Kluwer Medknow PublicationsIndian Journal of Pathology and Microbiology0377-49290974-51302024-12-0167488188310.4103/ijpm.ijpm_182_23Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case reportRaktim MukherjeeAniket HalderSuman Kumar DasSuchandra MukherjeeUttara ChatterjeeBiliary atresia (BA) is the most common cause of the obstructive type of neonatal cholestasis that requires prompt surgical intervention. About 10% of neonates with BA have other congenital anomalies, of which splenic malformation (BASM) is a well-known distinct sub-group. There is sparse literature on the association of duodenal atresia and ductal plate malformation (DPM) in patients of BASM. We describe a BASM associated with DPM and duodenal atresia in a 35-day-old infant, who succumbed at 40 days, before portoenterostomy could be performed. Duodenal atresia can be one of the associated malformations associated with BASM and ductal plate abnormalities. In our case, the child did not survive.https://journals.lww.com/10.4103/ijpm.ijpm_182_23ba with splenic malformationbiliary atresiaductal plate malformation |
| spellingShingle | Raktim Mukherjee Aniket Halder Suman Kumar Das Suchandra Mukherjee Uttara Chatterjee Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report Indian Journal of Pathology and Microbiology ba with splenic malformation biliary atresia ductal plate malformation |
| title | Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report |
| title_full | Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report |
| title_fullStr | Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report |
| title_full_unstemmed | Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report |
| title_short | Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report |
| title_sort | biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia a case report |
| topic | ba with splenic malformation biliary atresia ductal plate malformation |
| url | https://journals.lww.com/10.4103/ijpm.ijpm_182_23 |
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