Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four cases

São relatados os casos de 4 pacientes com síndrome de Dandy-Walker diagnosticada pela pneumencefalografia fracionada e ventriculografia. O tratamento e a patogenia desta malformação são discutidos com base em dados embriológicos.<br>Four cases of Dandy-Walker syndrome diagnosed through encepha...

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Main Authors: Jaderson Costa da Costa, Adão Anicet, Mario Ferreira Coutinho
Format: Article
Language:English
Published: Thieme Revinter Publicações 1973-03-01
Series:Arquivos de Neuro-Psiquiatria
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1973000100007
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author Jaderson Costa da Costa
Adão Anicet
Mario Ferreira Coutinho
author_facet Jaderson Costa da Costa
Adão Anicet
Mario Ferreira Coutinho
author_sort Jaderson Costa da Costa
collection DOAJ
description São relatados os casos de 4 pacientes com síndrome de Dandy-Walker diagnosticada pela pneumencefalografia fracionada e ventriculografia. O tratamento e a patogenia desta malformação são discutidos com base em dados embriológicos.<br>Four cases of Dandy-Walker syndrome diagnosed through encephalography and ventriculography with air are reported. The pathogenesis of this malformation is discussed. Particularly stressed are the radiological aspects of the condition, which are considered to be pathognomonic. The roentgenological findings are quite typical, indicating the extreme dolichocephaly, thinning and bulging of the bones of the posterior cranial fossa, prominent separation of the lambdoid sutures and an abnormal position of the lateral sinuses. Ventriculography shows symmetric hydrocephalus with extremely large cyst -like formation in the posterior fossa. Surgical indications are also considered. The ventricle lateral shunt is the recommended treatment for the DandyWalker malformations which show cerebral subarachnoid agenesis by pneumoencephalography.
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series Arquivos de Neuro-Psiquiatria
spelling doaj-art-177fff0059534a4e9738eb25c67e7bd42025-08-20T02:04:54ZengThieme Revinter PublicaçõesArquivos de Neuro-Psiquiatria0004-282X1678-42271973-03-013114652Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four casesJaderson Costa da CostaAdão AnicetMario Ferreira CoutinhoSão relatados os casos de 4 pacientes com síndrome de Dandy-Walker diagnosticada pela pneumencefalografia fracionada e ventriculografia. O tratamento e a patogenia desta malformação são discutidos com base em dados embriológicos.<br>Four cases of Dandy-Walker syndrome diagnosed through encephalography and ventriculography with air are reported. The pathogenesis of this malformation is discussed. Particularly stressed are the radiological aspects of the condition, which are considered to be pathognomonic. The roentgenological findings are quite typical, indicating the extreme dolichocephaly, thinning and bulging of the bones of the posterior cranial fossa, prominent separation of the lambdoid sutures and an abnormal position of the lateral sinuses. Ventriculography shows symmetric hydrocephalus with extremely large cyst -like formation in the posterior fossa. Surgical indications are also considered. The ventricle lateral shunt is the recommended treatment for the DandyWalker malformations which show cerebral subarachnoid agenesis by pneumoencephalography.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1973000100007
spellingShingle Jaderson Costa da Costa
Adão Anicet
Mario Ferreira Coutinho
Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four cases
Arquivos de Neuro-Psiquiatria
title Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four cases
title_full Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four cases
title_fullStr Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four cases
title_full_unstemmed Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four cases
title_short Síndrome de Dandy-walker The Dandy-Walker syndrome. Report of four cases
title_sort sindrome de dandy walker the dandy walker syndrome report of four cases
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1973000100007
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AT adaoanicet sindromededandywalkerthedandywalkersyndromereportoffourcases
AT marioferreiracoutinho sindromededandywalkerthedandywalkersyndromereportoffourcases