Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous Resolution

Subcutaneous panniculitis-like T-cell lymphomas (SPTLs) α/β are rare in childhood. The present report refers to a case of a 7-year-old male child presenting an extensive skin lesion that began when he was 5 years of age. Two biopsies were evaluated using the CD3, CD4, CD8, CD56, βF1, and TIA markers...

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Main Authors: Achiléa L. Bittencourt, Maria das Graças Silva Vieira, Eny Guimarães Carvalho, Celeste Cunha, Iguaracyra Araujo
Format: Article
Language:English
Published: Wiley 2011-01-01
Series:Case Reports in Oncological Medicine
Online Access:http://dx.doi.org/10.1155/2011/639240
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author Achiléa L. Bittencourt
Maria das Graças Silva Vieira
Eny Guimarães Carvalho
Celeste Cunha
Iguaracyra Araujo
author_facet Achiléa L. Bittencourt
Maria das Graças Silva Vieira
Eny Guimarães Carvalho
Celeste Cunha
Iguaracyra Araujo
author_sort Achiléa L. Bittencourt
collection DOAJ
description Subcutaneous panniculitis-like T-cell lymphomas (SPTLs) α/β are rare in childhood. The present report refers to a case of a 7-year-old male child presenting an extensive skin lesion that began when he was 5 years of age. Two biopsies were evaluated using the CD3, CD4, CD8, CD56, βF1, and TIA markers. A dense infiltrate of CD3+, CD4−, CD8+, CD56−, βF1+, and TIA+ pleomorphic lymphocytes was found in the subcutis. The previous biopsy showed cytophagic histiocytic panniculitis with a small focus on CD8+ and βF1+ malignant cells. The lesion regressed spontaneously. This case shows that prognosis may be excellent in SPTL (α/β). On the other hand, it also serves as an alert that a biopsy performed in an area of cytophagic panniculitis may lead to misdiagnosis.
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language English
publishDate 2011-01-01
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series Case Reports in Oncological Medicine
spelling doaj-art-1774e91e1d5d4709b974cdbe6da5054e2025-08-20T03:54:20ZengWileyCase Reports in Oncological Medicine2090-67062090-67142011-01-01201110.1155/2011/639240639240Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous ResolutionAchiléa L. Bittencourt0Maria das Graças Silva Vieira1Eny Guimarães Carvalho2Celeste Cunha3Iguaracyra Araujo4Department of Pathology, Complexo Hospitalar Universitário Prof. Edgard Santos, Federal University of Bahia, Salvador, BA, BrazilDepartment of Pathology, Complexo Hospitalar Universitário Prof. Edgard Santos, Federal University of Bahia, Salvador, BA, BrazilOncology Department, Pediatric Hospital Martagão Gesteira, Liga Baiana Contra a Mortalidade Infantil, Salvador, BA, BrazilOncology Department, Pediatric Hospital Martagão Gesteira, Liga Baiana Contra a Mortalidade Infantil, Salvador, BA, BrazilDepartment of Pathology, Complexo Hospitalar Universitário Prof. Edgard Santos, Federal University of Bahia, Salvador, BA, BrazilSubcutaneous panniculitis-like T-cell lymphomas (SPTLs) α/β are rare in childhood. The present report refers to a case of a 7-year-old male child presenting an extensive skin lesion that began when he was 5 years of age. Two biopsies were evaluated using the CD3, CD4, CD8, CD56, βF1, and TIA markers. A dense infiltrate of CD3+, CD4−, CD8+, CD56−, βF1+, and TIA+ pleomorphic lymphocytes was found in the subcutis. The previous biopsy showed cytophagic histiocytic panniculitis with a small focus on CD8+ and βF1+ malignant cells. The lesion regressed spontaneously. This case shows that prognosis may be excellent in SPTL (α/β). On the other hand, it also serves as an alert that a biopsy performed in an area of cytophagic panniculitis may lead to misdiagnosis.http://dx.doi.org/10.1155/2011/639240
spellingShingle Achiléa L. Bittencourt
Maria das Graças Silva Vieira
Eny Guimarães Carvalho
Celeste Cunha
Iguaracyra Araujo
Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous Resolution
Case Reports in Oncological Medicine
title Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous Resolution
title_full Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous Resolution
title_fullStr Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous Resolution
title_full_unstemmed Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous Resolution
title_short Subcutaneous Panniculitis-Like T-Cell Lymphoma (SPTL) in a Child with Spontaneous Resolution
title_sort subcutaneous panniculitis like t cell lymphoma sptl in a child with spontaneous resolution
url http://dx.doi.org/10.1155/2011/639240
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