Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review
Extra-axial ependymomas are rare tumours, and myxopapillary ependymoma (MPE) is the most common subtype in children, often misdiagnosed as other sacral lesions. MPEs are considered low-grade tumours, but relapse with distant metastasis is frequent. Therefore, therefore a proper diagnosis and subsequ...
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| Format: | Article |
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Frontiers Media S.A.
2025-01-01
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| Series: | Frontiers in Oncology |
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| Online Access: | https://www.frontiersin.org/articles/10.3389/fonc.2025.1519842/full |
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| author | Roberto Lo Piccolo Roberto Lo Piccolo Maria Chiara Cianci Iacopo Sardi Marco Di Nicola Anna M. Buccoliero Chiara Caporalini Antonino Morabito Antonino Morabito |
| author_facet | Roberto Lo Piccolo Roberto Lo Piccolo Maria Chiara Cianci Iacopo Sardi Marco Di Nicola Anna M. Buccoliero Chiara Caporalini Antonino Morabito Antonino Morabito |
| author_sort | Roberto Lo Piccolo |
| collection | DOAJ |
| description | Extra-axial ependymomas are rare tumours, and myxopapillary ependymoma (MPE) is the most common subtype in children, often misdiagnosed as other sacral lesions. MPEs are considered low-grade tumours, but relapse with distant metastasis is frequent. Therefore, therefore a proper diagnosis and subsequent follow-up are warranted. The current report presents a case of extra-axial MPE in a paediatric patient who presented with an indolent sacral mass and underwent surgical resection, along with a review of the literature. The aim was to highlight the importance of diagnostic suspicion in differential diagnosis of sacral soft-tissue masses |
| format | Article |
| id | doaj-art-175bfee2303440819d0cb423c81e8880 |
| institution | Kabale University |
| issn | 2234-943X |
| language | English |
| publishDate | 2025-01-01 |
| publisher | Frontiers Media S.A. |
| record_format | Article |
| series | Frontiers in Oncology |
| spelling | doaj-art-175bfee2303440819d0cb423c81e88802025-01-30T06:22:20ZengFrontiers Media S.A.Frontiers in Oncology2234-943X2025-01-011510.3389/fonc.2025.15198421519842Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature reviewRoberto Lo Piccolo0Roberto Lo Piccolo1Maria Chiara Cianci2Iacopo Sardi3Marco Di Nicola4Anna M. Buccoliero5Chiara Caporalini6Antonino Morabito7Antonino Morabito8Azienda Ospedaliera Universitaria Meyer Istituto di Ricerca e Cura a carattere Scientifico (IRCCS) - Firenze, Florence, ItalyDepartment of Pediatric Surgery, Istituto di Ricerca e Cura a carattere Scientifico (IRCCS) Meyer Children’s Hospital, Florence, ItalyDepartment of Pediatric Surgery, Istituto di Ricerca e Cura a carattere Scientifico (IRCCS) Meyer Children’s Hospital, Florence, ItalyNeuro-Oncology Unit, Meyer Children’s Hospital, Florence, ItalyNeuro-Oncology Unit, Meyer Children’s Hospital, Florence, ItalyPathology Unit, Meyer Children’s Hospital, Florence, ItalyPathology Unit, Meyer Children’s Hospital, Florence, ItalyDepartment of Pediatric Surgery, Istituto di Ricerca e Cura a carattere Scientifico (IRCCS) Meyer Children’s Hospital, Florence, ItalyDepartment of Neuroscience, Psychology, Drugs and Child Health Area, School of Psychology, University of Florence, Florence, ItalyExtra-axial ependymomas are rare tumours, and myxopapillary ependymoma (MPE) is the most common subtype in children, often misdiagnosed as other sacral lesions. MPEs are considered low-grade tumours, but relapse with distant metastasis is frequent. Therefore, therefore a proper diagnosis and subsequent follow-up are warranted. The current report presents a case of extra-axial MPE in a paediatric patient who presented with an indolent sacral mass and underwent surgical resection, along with a review of the literature. The aim was to highlight the importance of diagnostic suspicion in differential diagnosis of sacral soft-tissue masseshttps://www.frontiersin.org/articles/10.3389/fonc.2025.1519842/fullpaediatricsacral soft tissue lesioncase reportmyxopapillary ependymomaextra-axial ependymomas |
| spellingShingle | Roberto Lo Piccolo Roberto Lo Piccolo Maria Chiara Cianci Iacopo Sardi Marco Di Nicola Anna M. Buccoliero Chiara Caporalini Antonino Morabito Antonino Morabito Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review Frontiers in Oncology paediatric sacral soft tissue lesion case report myxopapillary ependymoma extra-axial ependymomas |
| title | Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review |
| title_full | Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review |
| title_fullStr | Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review |
| title_full_unstemmed | Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review |
| title_short | Paediatric extra-axial myxopapillary ependymoma: what to expect? Case report and literature review |
| title_sort | paediatric extra axial myxopapillary ependymoma what to expect case report and literature review |
| topic | paediatric sacral soft tissue lesion case report myxopapillary ependymoma extra-axial ependymomas |
| url | https://www.frontiersin.org/articles/10.3389/fonc.2025.1519842/full |
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