Pigmentary Mosaicism: An Overview

ABSTRACT Mosaicism refers to an individual who developed from a single fertilised egg but has two or more populations of cells with a different genotype as a result of a postzygotic mutation. Pigmentary mosaicism is reflected by a patterned hypo‐, hyperpigmentation, or both combined in cutis tricolo...

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Main Authors: C. Colmant, E. Legius, N. Cattaert, M.‐A. Morren
Format: Article
Language:English
Published: Wiley 2025-09-01
Series:JEADV Clinical Practice
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Online Access:https://doi.org/10.1002/jvc2.70048
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author C. Colmant
E. Legius
N. Cattaert
M.‐A. Morren
author_facet C. Colmant
E. Legius
N. Cattaert
M.‐A. Morren
author_sort C. Colmant
collection DOAJ
description ABSTRACT Mosaicism refers to an individual who developed from a single fertilised egg but has two or more populations of cells with a different genotype as a result of a postzygotic mutation. Pigmentary mosaicism is reflected by a patterned hypo‐, hyperpigmentation, or both combined in cutis tricolour. Pigmentary mosaicism can be associated with extracutaneous features (mainly neurological, musculoskeletal or ophthalmological). Three main mechanisms are involved in the development of pigmentary mosaicism: mosaicism for a chromosomal abnormality, mosaicism for an intragenic pathogenic variant and epigenetic mosaicism (X‐linked due to X‐chromosome inactivation). Recently, different new disease entities have been described with a specific genotype, most of them with characteristic extra‐cutaneous features.
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spelling doaj-art-16d59bf2a1514fd3b6773ff8d76f19ec2025-08-20T02:56:29ZengWileyJEADV Clinical Practice2768-65662025-09-014368168910.1002/jvc2.70048Pigmentary Mosaicism: An OverviewC. Colmant0E. Legius1N. Cattaert2M.‐A. Morren3Department of Dermatology University Hospital Leuven Leuven BelgiumDepartment of Human Genetics University Hospital Leuven Leuven BelgiumDepartment of Dermatology Heilig Hart Ziekenhuis Lier BelgiumPediatric Dermatology Unit, Dept of Pediatrics and Dermatology Lausanne University Hospital and University of Lausanne Lausanne SwitzerlandABSTRACT Mosaicism refers to an individual who developed from a single fertilised egg but has two or more populations of cells with a different genotype as a result of a postzygotic mutation. Pigmentary mosaicism is reflected by a patterned hypo‐, hyperpigmentation, or both combined in cutis tricolour. Pigmentary mosaicism can be associated with extracutaneous features (mainly neurological, musculoskeletal or ophthalmological). Three main mechanisms are involved in the development of pigmentary mosaicism: mosaicism for a chromosomal abnormality, mosaicism for an intragenic pathogenic variant and epigenetic mosaicism (X‐linked due to X‐chromosome inactivation). Recently, different new disease entities have been described with a specific genotype, most of them with characteristic extra‐cutaneous features.https://doi.org/10.1002/jvc2.70048hypomelanosis of Itolinear hypermelanosispigmentary mosaicisme
spellingShingle C. Colmant
E. Legius
N. Cattaert
M.‐A. Morren
Pigmentary Mosaicism: An Overview
JEADV Clinical Practice
hypomelanosis of Ito
linear hypermelanosis
pigmentary mosaicisme
title Pigmentary Mosaicism: An Overview
title_full Pigmentary Mosaicism: An Overview
title_fullStr Pigmentary Mosaicism: An Overview
title_full_unstemmed Pigmentary Mosaicism: An Overview
title_short Pigmentary Mosaicism: An Overview
title_sort pigmentary mosaicism an overview
topic hypomelanosis of Ito
linear hypermelanosis
pigmentary mosaicisme
url https://doi.org/10.1002/jvc2.70048
work_keys_str_mv AT ccolmant pigmentarymosaicismanoverview
AT elegius pigmentarymosaicismanoverview
AT ncattaert pigmentarymosaicismanoverview
AT mamorren pigmentarymosaicismanoverview