Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case report

Objective To analyze the clinical outcomes of a patient with thrombotic thrombocytopenic purpura(TTP) as the starting performance who was considered as systemic lupus erythematosus(SLE) under multiple abnormal autoantibodies, and summarize the treatment experience through the clinical outcomes of pl...

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Main Authors: LI Xu, LIU Fangjiu, YANG Hong
Format: Article
Language:zho
Published: Institute of Blood Transfusion of Chinese Academy of Medical Sciences 2024-10-01
Series:Zhongguo shuxue zazhi
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Online Access:https://www.cjbt.cn/thesisDetails#10.13303/j.cjbt.issn.1004-549x.2024.10.018&lang=en
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author LI Xu
LIU Fangjiu
YANG Hong
author_facet LI Xu
LIU Fangjiu
YANG Hong
author_sort LI Xu
collection DOAJ
description Objective To analyze the clinical outcomes of a patient with thrombotic thrombocytopenic purpura(TTP) as the starting performance who was considered as systemic lupus erythematosus(SLE) under multiple abnormal autoantibodies, and summarize the treatment experience through the clinical outcomes of plasma exchange combined with high-does steroid pulse therapy. Methods A middle-aged female patient presented with initial symptoms of fever, bleeding and hemolytic thrombocytopenia. Laboratory tests showed decreased activity of thrombospondin type 1 motif no.13(ADAMT13) and abnormal autoantibodies. The diagnosis was considered SLE with TTP, and the patient underwent continuous plasma exchange combined with high-dose steroid pulse therapy. The patient's platelet recovery was dynamically observed. Results The patient responded well to plasma exchange combined with high-does steroid pulse therapy, with platelet count raising to normal in a short period of time and hormone gradually decreasing. There was no recurrence during the follow-up period. Conclusion TTP combined with lupus is not common, but when both occur simultaneously, plasma exchange combined with high-does steroid pulse therapy may effectively alleviate symptoms. This treatment approach can serve as a valuable reference for similar clinical cases.
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spelling doaj-art-1577ed7dbc8f432f99b0fe7380e6c10b2025-08-20T02:12:11ZzhoInstitute of Blood Transfusion of Chinese Academy of Medical SciencesZhongguo shuxue zazhi1004-549X2024-10-0137101189119210.13303/j.cjbt.issn.1004-549x.2024.10.0181004-549X(2024)10-1189-04Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case reportLI Xu0LIU Fangjiu1YANG Hong2Suining Central Hospital, Suining 629000, ChinaSuining Central Hospital, Suining 629000, ChinaSuining Central Hospital, Suining 629000, ChinaObjective To analyze the clinical outcomes of a patient with thrombotic thrombocytopenic purpura(TTP) as the starting performance who was considered as systemic lupus erythematosus(SLE) under multiple abnormal autoantibodies, and summarize the treatment experience through the clinical outcomes of plasma exchange combined with high-does steroid pulse therapy. Methods A middle-aged female patient presented with initial symptoms of fever, bleeding and hemolytic thrombocytopenia. Laboratory tests showed decreased activity of thrombospondin type 1 motif no.13(ADAMT13) and abnormal autoantibodies. The diagnosis was considered SLE with TTP, and the patient underwent continuous plasma exchange combined with high-dose steroid pulse therapy. The patient's platelet recovery was dynamically observed. Results The patient responded well to plasma exchange combined with high-does steroid pulse therapy, with platelet count raising to normal in a short period of time and hormone gradually decreasing. There was no recurrence during the follow-up period. Conclusion TTP combined with lupus is not common, but when both occur simultaneously, plasma exchange combined with high-does steroid pulse therapy may effectively alleviate symptoms. This treatment approach can serve as a valuable reference for similar clinical cases.https://www.cjbt.cn/thesisDetails#10.13303/j.cjbt.issn.1004-549x.2024.10.018&lang=enplasma exchangehigh-dose steroid pulsesystemic lupus erythematosus(sle)thrombotic thrombocytopenic purpura(ttp)
spellingShingle LI Xu
LIU Fangjiu
YANG Hong
Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case report
Zhongguo shuxue zazhi
plasma exchange
high-dose steroid pulse
systemic lupus erythematosus(sle)
thrombotic thrombocytopenic purpura(ttp)
title Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case report
title_full Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case report
title_fullStr Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case report
title_full_unstemmed Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case report
title_short Systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high-dose steroid pulse therapy: a case report
title_sort systemic lupus erythematosus induced thrombotic thrombocytopenic purpura treated with plasma exchange combined with high dose steroid pulse therapy a case report
topic plasma exchange
high-dose steroid pulse
systemic lupus erythematosus(sle)
thrombotic thrombocytopenic purpura(ttp)
url https://www.cjbt.cn/thesisDetails#10.13303/j.cjbt.issn.1004-549x.2024.10.018&lang=en
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AT liufangjiu systemiclupuserythematosusinducedthromboticthrombocytopenicpurpuratreatedwithplasmaexchangecombinedwithhighdosesteroidpulsetherapyacasereport
AT yanghong systemiclupuserythematosusinducedthromboticthrombocytopenicpurpuratreatedwithplasmaexchangecombinedwithhighdosesteroidpulsetherapyacasereport