Transcatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgery

Introduction. Transcatheter atrial septal defect (ASD) closure is considered to be a gold standard for patients with the suitable anatomy as compared to cardiac surgery. Reocurrence of ASD after surgical closure is a very rare late complication which can be successfully managed with transca...

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Main Authors: Mangovski Ljupčo, Farkić Mihajlo, Jovović Ljiljana
Format: Article
Language:English
Published: Ministry of Defence of the Republic of Serbia, University of Defence, Belgrade 2015-01-01
Series:Vojnosanitetski Pregled
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Online Access:http://www.doiserbia.nb.rs/img/doi/0042-8450/2015/0042-84501506557M.pdf
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author Mangovski Ljupčo
Farkić Mihajlo
Jovović Ljiljana
author_facet Mangovski Ljupčo
Farkić Mihajlo
Jovović Ljiljana
author_sort Mangovski Ljupčo
collection DOAJ
description Introduction. Transcatheter atrial septal defect (ASD) closure is considered to be a gold standard for patients with the suitable anatomy as compared to cardiac surgery. Reocurrence of ASD after surgical closure is a very rare late complication which can be successfully managed with transcatheter procedure. Case report. We reported a female patient with Noonan syndrome who presented with hemodinamically significant ASD 37 years after the corrective cardiac surgery. Due to numerous comorbidities which included severe kyphoscoliosis, pectus excavatum and multiple surgeries we decided to perform transcatheter closure of ASD. The procedure itself was very challenging due to the patient’s short stature and heart’s orientation in the chest, but was performed successfully. The subsequent follow-up was uneventful and the patient reported improvement in the symptoms. Conclusion. Transcatheter closure of ASD in a patient with Noonan syndrome with the history of surgically corrected ASD can be performed successfully, despite challenging chest anatomy.
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institution Kabale University
issn 0042-8450
language English
publishDate 2015-01-01
publisher Ministry of Defence of the Republic of Serbia, University of Defence, Belgrade
record_format Article
series Vojnosanitetski Pregled
spelling doaj-art-145343d223ad4afda5df91e1b7a5b9d82025-08-20T03:54:33ZengMinistry of Defence of the Republic of Serbia, University of Defence, BelgradeVojnosanitetski Pregled0042-84502015-01-0172655756010.2298/VSP1506557M0042-84501506557MTranscatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgeryMangovski Ljupčo0Farkić Mihajlo1Jovović Ljiljana2"Dedinje" Cardiovascular Institute, Belgrade"Dedinje" Cardiovascular Institute, Belgrade"Dedinje" Cardiovascular Institute, BelgradeIntroduction. Transcatheter atrial septal defect (ASD) closure is considered to be a gold standard for patients with the suitable anatomy as compared to cardiac surgery. Reocurrence of ASD after surgical closure is a very rare late complication which can be successfully managed with transcatheter procedure. Case report. We reported a female patient with Noonan syndrome who presented with hemodinamically significant ASD 37 years after the corrective cardiac surgery. Due to numerous comorbidities which included severe kyphoscoliosis, pectus excavatum and multiple surgeries we decided to perform transcatheter closure of ASD. The procedure itself was very challenging due to the patient’s short stature and heart’s orientation in the chest, but was performed successfully. The subsequent follow-up was uneventful and the patient reported improvement in the symptoms. Conclusion. Transcatheter closure of ASD in a patient with Noonan syndrome with the history of surgically corrected ASD can be performed successfully, despite challenging chest anatomy.http://www.doiserbia.nb.rs/img/doi/0042-8450/2015/0042-84501506557M.pdfNoonan syndromeheart septal defectscongenital abnormalitiescardiovascular surgical procedurestreatment outcome
spellingShingle Mangovski Ljupčo
Farkić Mihajlo
Jovović Ljiljana
Transcatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgery
Vojnosanitetski Pregled
Noonan syndrome
heart septal defects
congenital abnormalities
cardiovascular surgical procedures
treatment outcome
title Transcatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgery
title_full Transcatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgery
title_fullStr Transcatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgery
title_full_unstemmed Transcatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgery
title_short Transcatheter closure of atrial septal defect in a patient with Noonan syndrome after corrective surgery
title_sort transcatheter closure of atrial septal defect in a patient with noonan syndrome after corrective surgery
topic Noonan syndrome
heart septal defects
congenital abnormalities
cardiovascular surgical procedures
treatment outcome
url http://www.doiserbia.nb.rs/img/doi/0042-8450/2015/0042-84501506557M.pdf
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AT farkicmihajlo transcatheterclosureofatrialseptaldefectinapatientwithnoonansyndromeaftercorrectivesurgery
AT jovovicljiljana transcatheterclosureofatrialseptaldefectinapatientwithnoonansyndromeaftercorrectivesurgery