Modern Approaches in Management of Children with Cystic fibrosis
The problem of timely diagnosis and proper management of patients with cystic fibrosis is crucial not only in our country, but throughout the world. Experts of the Union of Pediatricians of Russia have considered various issues of etiology, pathogenesis, epidemiology, diagnosis, and treatment of thi...
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| Format: | Article |
| Language: | Russian |
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Union of pediatricians of Russia
2022-05-01
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| Series: | Педиатрическая фармакология |
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| Online Access: | https://www.pedpharma.ru/jour/article/view/2169 |
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| author | Alexander A. Baranov Leyla S. Namazova-Baranova Sergey I. Kutsev Sergey N. Avdeev Elena V. Polevichenko Andrey S. Belevskiy Elena I. Kondratyeva Olga I. Simonova Nataliya Yu. Kashirskaya Victoria D. Sherman Anna Yu. Voronkova Evgeniya L. Amelina Tatyana E. Gembitskaya Stanislav A. Krasovskiy Alexey G. Chermenskiy Tatyana A. Stepanenko Liliia R. Selimzyanova Elena A. Vishneva Yulia V. Gorinova Elena A. Roslavtseva Irina K. Asherova Natalya A. Ilyenkova Sergey K. Zyryanov Niso D. Odinayeva Tatyana Yu. Maksimycheva Alexander V. Orlov Sergey Yu. Semykin Marina Yu. Chernukha Igor A. Shaginyan Lusine R. Avetisyan Galina L. Shumkova Natalya A. Krylova Ivan A. Dronov Maria N. Kostyleva Ludmila A. Zhelenina Nikolay N. Klimko Yuliya V. Borzova Natalya V. Vasilyeva Tatyana S. Bogomolova Anna A. Speranskaya Irina A. Baranova Evgeny G. Furman Vera V. Shadrina Nikolay F. Shchapov Nika V. Petrova Ivan V. Pashkov Olga M. Tsirulnikova Dmitriy P. Polyakov Valeriy M. Svistushkin Eduard V. Sin'kov Vyacheslav B. Chernykh Svetlana A. Repina Dmitriy A. Blagovidov Mikhail P. Kostinov Olga V. Kondratenko Artem V. Lyamin Svetlana V. Polikarpova Alexander V. Polyakov Tagui A. Adyan Dmitry V. Goldshtein Tatiana B. Bukharova Anna S. Efremova Elena S. Ovsyankina Ludmila V. Panova Irina V. Cherkashina |
| author_facet | Alexander A. Baranov Leyla S. Namazova-Baranova Sergey I. Kutsev Sergey N. Avdeev Elena V. Polevichenko Andrey S. Belevskiy Elena I. Kondratyeva Olga I. Simonova Nataliya Yu. Kashirskaya Victoria D. Sherman Anna Yu. Voronkova Evgeniya L. Amelina Tatyana E. Gembitskaya Stanislav A. Krasovskiy Alexey G. Chermenskiy Tatyana A. Stepanenko Liliia R. Selimzyanova Elena A. Vishneva Yulia V. Gorinova Elena A. Roslavtseva Irina K. Asherova Natalya A. Ilyenkova Sergey K. Zyryanov Niso D. Odinayeva Tatyana Yu. Maksimycheva Alexander V. Orlov Sergey Yu. Semykin Marina Yu. Chernukha Igor A. Shaginyan Lusine R. Avetisyan Galina L. Shumkova Natalya A. Krylova Ivan A. Dronov Maria N. Kostyleva Ludmila A. Zhelenina Nikolay N. Klimko Yuliya V. Borzova Natalya V. Vasilyeva Tatyana S. Bogomolova Anna A. Speranskaya Irina A. Baranova Evgeny G. Furman Vera V. Shadrina Nikolay F. Shchapov Nika V. Petrova Ivan V. Pashkov Olga M. Tsirulnikova Dmitriy P. Polyakov Valeriy M. Svistushkin Eduard V. Sin'kov Vyacheslav B. Chernykh Svetlana A. Repina Dmitriy A. Blagovidov Mikhail P. Kostinov Olga V. Kondratenko Artem V. Lyamin Svetlana V. Polikarpova Alexander V. Polyakov Tagui A. Adyan Dmitry V. Goldshtein Tatiana B. Bukharova Anna S. Efremova Elena S. Ovsyankina Ludmila V. Panova Irina V. Cherkashina |
| author_sort | Alexander A. Baranov |
| collection | DOAJ |
| description | The problem of timely diagnosis and proper management of patients with cystic fibrosis is crucial not only in our country, but throughout the world. Experts of the Union of Pediatricians of Russia have considered various issues of etiology, pathogenesis, epidemiology, diagnosis, and treatment of this genetic disease in a modern light. Particular attention was paid to screening methods for early diagnosis of cystic fibrosis. The principles of complex therapy were justified, including rational use of antibacterial and mucolytic drugs and enzyme replacement therapy that significantly determine the disease prognosis. |
| format | Article |
| id | doaj-art-143f4fcbf4674dee93deee9bc716f441 |
| institution | DOAJ |
| issn | 1727-5776 2500-3089 |
| language | Russian |
| publishDate | 2022-05-01 |
| publisher | Union of pediatricians of Russia |
| record_format | Article |
| series | Педиатрическая фармакология |
| spelling | doaj-art-143f4fcbf4674dee93deee9bc716f4412025-08-20T03:19:39ZrusUnion of pediatricians of RussiaПедиатрическая фармакология1727-57762500-30892022-05-0119215319510.15690/pf.v19i2.24171904Modern Approaches in Management of Children with Cystic fibrosisAlexander A. Baranov0Leyla S. Namazova-Baranova1Sergey I. Kutsev2Sergey N. Avdeev3Elena V. Polevichenko4Andrey S. Belevskiy5Elena I. Kondratyeva6Olga I. Simonova7Nataliya Yu. Kashirskaya8Victoria D. Sherman9Anna Yu. Voronkova10Evgeniya L. Amelina11Tatyana E. Gembitskaya12Stanislav A. Krasovskiy13Alexey G. Chermenskiy14Tatyana A. Stepanenko15Liliia R. Selimzyanova16Elena A. Vishneva17Yulia V. Gorinova18Elena A. Roslavtseva19Irina K. Asherova20Natalya A. Ilyenkova21Sergey K. Zyryanov22Niso D. Odinayeva23Tatyana Yu. Maksimycheva24Alexander V. Orlov25Sergey Yu. Semykin26Marina Yu. Chernukha27Igor A. Shaginyan28Lusine R. Avetisyan29Galina L. Shumkova30Natalya A. Krylova31Ivan A. Dronov32Maria N. Kostyleva33Ludmila A. Zhelenina34Nikolay N. Klimko35Yuliya V. Borzova36Natalya V. Vasilyeva37Tatyana S. Bogomolova38Anna A. Speranskaya39Irina A. Baranova40Evgeny G. Furman41Vera V. Shadrina42Nikolay F. Shchapov43Nika V. Petrova44Ivan V. Pashkov45Olga M. Tsirulnikova46Dmitriy P. Polyakov47Valeriy M. Svistushkin48Eduard V. Sin'kov49Vyacheslav B. Chernykh50Svetlana A. Repina51Dmitriy A. Blagovidov52Mikhail P. Kostinov53Olga V. Kondratenko54Artem V. Lyamin55Svetlana V. Polikarpova56Alexander V. Polyakov57Tagui A. Adyan58Dmitry V. Goldshtein59Tatiana B. Bukharova60Anna S. Efremova61Elena S. Ovsyankina62Ludmila V. Panova63Irina V. Cherkashina64Research Institute of Pediatrics and Children’s Health in Petrovsky National Research Centre of Surgery; Sechenov First Moscow State Medical UniversityResearch Institute of Pediatrics and Children’s Health in Petrovsky National Research Centre of Surgery; Pirogov Russian National Research Medical University; Belgorod National Research UniversityResearch Centre for Medical GeneticsSechenov First Moscow State Medical University; Pulmonology Research Institute of Federal Medico-Biological Agency of RussiaSechenov First Moscow State Medical UniversityPirogov Russian National Research Medical UniversityResearch Centre for Medical Genetics; Research Clinical Institute of Childhood of the Ministry of Health of Moscow RegionSechenov First Moscow State Medical University; National Medical Research Center of Children’s Health; Morozov Children’s City HospitalResearch Centre for Medical GeneticsResearch Centre for Medical GeneticsResearch Centre for Medical GeneticsResearch Centre for Medical Genetics; Pulmonology Research Institute of Federal Medico-Biological Agency of RussiaPavlov First Saint Petersburg State Medical UniversityResearch Centre for Medical Genetics; Pulmonology Research Institute of Federal Medico-Biological Agency of RussiaPavlov First Saint Petersburg State Medical UniversityCity Multidisciplinary Hospital № 2Research Institute of Pediatrics and Children’s Health in Petrovsky National Research Centre of Surgery; Sechenov First Moscow State Medical UniversityResearch Institute of Pediatrics and Children’s Health in Petrovsky National Research Centre of Surgery; Pirogov Russian National Research Medical UniversityNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthCentral Clinical HospitalKrasnoyarsk State Medical University named after prof. V.F. Voino-YasenetskyRUDN UniversityResearch Clinical Institute of Childhood of the Ministry of Health of Moscow RegionResearch Centre for Medical GeneticsNorth-Western State Medical University named after I.I. Mechnikov; St. Olga Children’s City HospitalRussian Children’s Clinical HospitalNational Research Center for Epidemiology and Microbiology named after Honorary Academician N.F. GamaleyaNational Research Center for Epidemiology and Microbiology named after Honorary Academician N.F. GamaleyaNational Research Center for Epidemiology and Microbiology named after Honorary Academician N.F. GamaleyaPulmonology Research Institute of Federal Medico-Biological Agency of RussiaPulmonology Research Institute of Federal Medico-Biological Agency of RussiaSechenov First Moscow State Medical University; Research Clinical Institute of Childhood of the Ministry of Health of Moscow RegionPirogov Russian National Research Medical University; Russian Children’s Clinical HospitalSaint Petersburg State Pediatric Medical UniversityNorth-Western State Medical University named after I.I. MechnikovNorth-Western State Medical University named after I.I. MechnikovNorth-Western State Medical University named after I.I. Mechnikov; Kashkin Research Institute of Medical MycologyNorth-Western State Medical University named after I.I. MechnikovPavlov First Saint Petersburg State Medical UniversityPirogov Russian National Research Medical UniversityPerm State Medical University named after academician E.A. WagnerPerm State Medical University named after academician E.A. WagnerMoscow Regional Center for Maternity and Childhood ProtectionResearch Centre for Medical GeneticsV.I. Shumakov National Medical Research Center of Transplantology and Artificial Organs of the Ministry of Healthcare of Russian FederationSechenov First Moscow State Medical UniversityPirogov Russian National Research Medical University; National Medical Research Center for Otorhinolaryngology of Federal Medico-Biological Agency of RussiaSechenov First Moscow State Medical UniversitySechenov First Moscow State Medical UniversityResearch Centre for Medical GeneticsResearch Centre for Medical GeneticsPirogov Russian National Research Medical University; I.I. Mechnikov Research Institute of Vaccines and SeraI.I. Mechnikov Research Institute of Vaccines and SeraSamara State Medical UniversitySamara State Medical UniversityCity Clinical Hospital № 15 named after O.M. FilatovResearch Centre for Medical GeneticsPirogov Russian National Research Medical University; Research Centre for Medical GeneticsResearch Centre for Medical GeneticsResearch Centre for Medical GeneticsResearch Centre for Medical GeneticsCentral Research Institute of TuberculosisCentral Research Institute of TuberculosisChildren’s Research and Clinical Center for Infectious Diseases of Federal Medico-Biological Agency of RussiaThe problem of timely diagnosis and proper management of patients with cystic fibrosis is crucial not only in our country, but throughout the world. Experts of the Union of Pediatricians of Russia have considered various issues of etiology, pathogenesis, epidemiology, diagnosis, and treatment of this genetic disease in a modern light. Particular attention was paid to screening methods for early diagnosis of cystic fibrosis. The principles of complex therapy were justified, including rational use of antibacterial and mucolytic drugs and enzyme replacement therapy that significantly determine the disease prognosis.https://www.pedpharma.ru/jour/article/view/2169cystic fibrosisdiagnosistreatmentkinesitherapyenzyme replacement therapychildren |
| spellingShingle | Alexander A. Baranov Leyla S. Namazova-Baranova Sergey I. Kutsev Sergey N. Avdeev Elena V. Polevichenko Andrey S. Belevskiy Elena I. Kondratyeva Olga I. Simonova Nataliya Yu. Kashirskaya Victoria D. Sherman Anna Yu. Voronkova Evgeniya L. Amelina Tatyana E. Gembitskaya Stanislav A. Krasovskiy Alexey G. Chermenskiy Tatyana A. Stepanenko Liliia R. Selimzyanova Elena A. Vishneva Yulia V. Gorinova Elena A. Roslavtseva Irina K. Asherova Natalya A. Ilyenkova Sergey K. Zyryanov Niso D. Odinayeva Tatyana Yu. Maksimycheva Alexander V. Orlov Sergey Yu. Semykin Marina Yu. Chernukha Igor A. Shaginyan Lusine R. Avetisyan Galina L. Shumkova Natalya A. Krylova Ivan A. Dronov Maria N. Kostyleva Ludmila A. Zhelenina Nikolay N. Klimko Yuliya V. Borzova Natalya V. Vasilyeva Tatyana S. Bogomolova Anna A. Speranskaya Irina A. Baranova Evgeny G. Furman Vera V. Shadrina Nikolay F. Shchapov Nika V. Petrova Ivan V. Pashkov Olga M. Tsirulnikova Dmitriy P. Polyakov Valeriy M. Svistushkin Eduard V. Sin'kov Vyacheslav B. Chernykh Svetlana A. Repina Dmitriy A. Blagovidov Mikhail P. Kostinov Olga V. Kondratenko Artem V. Lyamin Svetlana V. Polikarpova Alexander V. Polyakov Tagui A. Adyan Dmitry V. Goldshtein Tatiana B. Bukharova Anna S. Efremova Elena S. Ovsyankina Ludmila V. Panova Irina V. Cherkashina Modern Approaches in Management of Children with Cystic fibrosis Педиатрическая фармакология cystic fibrosis diagnosis treatment kinesitherapy enzyme replacement therapy children |
| title | Modern Approaches in Management of Children with Cystic fibrosis |
| title_full | Modern Approaches in Management of Children with Cystic fibrosis |
| title_fullStr | Modern Approaches in Management of Children with Cystic fibrosis |
| title_full_unstemmed | Modern Approaches in Management of Children with Cystic fibrosis |
| title_short | Modern Approaches in Management of Children with Cystic fibrosis |
| title_sort | modern approaches in management of children with cystic fibrosis |
| topic | cystic fibrosis diagnosis treatment kinesitherapy enzyme replacement therapy children |
| url | https://www.pedpharma.ru/jour/article/view/2169 |
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