A Giant Primary Mediastinal Teratocarcinoma in a Male Adult

Germ cell tumors (GCTs) arise along the midline, in which 50-70% of extragonadal GCTs occur in the mediastinum. Malignant GCTs are more common in males, while benign GCTs occur equally in both males and females. This report presents a case of a giant primary mediastinal nonseminomatous GCT resected...

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Main Authors: Muneera Al-Khalifa, Sara Alsaad, Habib Al-Tareef, Zaid Arekat, Abdulla Darwish
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Case Reports in Surgery
Online Access:http://dx.doi.org/10.1155/2019/7123241
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author Muneera Al-Khalifa
Sara Alsaad
Habib Al-Tareef
Zaid Arekat
Abdulla Darwish
author_facet Muneera Al-Khalifa
Sara Alsaad
Habib Al-Tareef
Zaid Arekat
Abdulla Darwish
author_sort Muneera Al-Khalifa
collection DOAJ
description Germ cell tumors (GCTs) arise along the midline, in which 50-70% of extragonadal GCTs occur in the mediastinum. Malignant GCTs are more common in males, while benign GCTs occur equally in both males and females. This report presents a case of a giant primary mediastinal nonseminomatous GCT resected from a 35-year-old male who presented with dyspnoea and tightness in the chest. Thorough investigations including a chest MRI were done. It showed a 21×19×15 cm tumor. Thus, surgical resection of the tumor through a midline sternotomy was done. Histopathological analysis diagnosed the tumor as a primary mediastinal teratocarcinoma with a sarcomatous component. Eighteen-month follow-up showed no tumor recurrence. Mediastinal teratocarcinoma is a rare and life-threatening germ cell tumor. Studies recommend the use of chemotherapy prior to resection as an important step in its management. Close and regular follow-up postsurgical resection is advised.
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institution Kabale University
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publishDate 2019-01-01
publisher Wiley
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series Case Reports in Surgery
spelling doaj-art-143bd65db4094f9487fec079ea70ce3f2025-08-20T03:54:33ZengWileyCase Reports in Surgery2090-69002090-69192019-01-01201910.1155/2019/71232417123241A Giant Primary Mediastinal Teratocarcinoma in a Male AdultMuneera Al-Khalifa0Sara Alsaad1Habib Al-Tareef2Zaid Arekat3Abdulla Darwish4RCSI-MUB, Busaiteen, BahrainDepartment of Pathology, Bahrain Defense Force Hospital, Riffa, BahrainMohammed Bin Khalifa Cardiac Center, Bahrain Defense Force Hospital, Riffa, BahrainMohammed Bin Khalifa Cardiac Center, Bahrain Defense Force Hospital, Riffa, BahrainDepartment of Pathology, Bahrain Defense Force Hospital, Riffa, BahrainGerm cell tumors (GCTs) arise along the midline, in which 50-70% of extragonadal GCTs occur in the mediastinum. Malignant GCTs are more common in males, while benign GCTs occur equally in both males and females. This report presents a case of a giant primary mediastinal nonseminomatous GCT resected from a 35-year-old male who presented with dyspnoea and tightness in the chest. Thorough investigations including a chest MRI were done. It showed a 21×19×15 cm tumor. Thus, surgical resection of the tumor through a midline sternotomy was done. Histopathological analysis diagnosed the tumor as a primary mediastinal teratocarcinoma with a sarcomatous component. Eighteen-month follow-up showed no tumor recurrence. Mediastinal teratocarcinoma is a rare and life-threatening germ cell tumor. Studies recommend the use of chemotherapy prior to resection as an important step in its management. Close and regular follow-up postsurgical resection is advised.http://dx.doi.org/10.1155/2019/7123241
spellingShingle Muneera Al-Khalifa
Sara Alsaad
Habib Al-Tareef
Zaid Arekat
Abdulla Darwish
A Giant Primary Mediastinal Teratocarcinoma in a Male Adult
Case Reports in Surgery
title A Giant Primary Mediastinal Teratocarcinoma in a Male Adult
title_full A Giant Primary Mediastinal Teratocarcinoma in a Male Adult
title_fullStr A Giant Primary Mediastinal Teratocarcinoma in a Male Adult
title_full_unstemmed A Giant Primary Mediastinal Teratocarcinoma in a Male Adult
title_short A Giant Primary Mediastinal Teratocarcinoma in a Male Adult
title_sort giant primary mediastinal teratocarcinoma in a male adult
url http://dx.doi.org/10.1155/2019/7123241
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