On a Rare Cutaneous Metastasis from a Sacrococcygeal Chordoma

Chordomas are rare malignant tumors of notochordal origin and are rare locally aggressive ones with a metastatic potential. The skin rarely is seen as metastatic site. We describe a case of an adult woman with cutaneous metastasis of a primary sacral chordoma excised ten years before, which appeared...

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Main Authors: Alessandro D’Amuri, Matteo Brunelli, Federica Floccari, Francesco De Caro, Giuliana Crisman, Francesca Sanguedolce, Marcello Filotico
Format: Article
Language:English
Published: Wiley 2017-01-01
Series:Case Reports in Pathology
Online Access:http://dx.doi.org/10.1155/2017/5281239
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author Alessandro D’Amuri
Matteo Brunelli
Federica Floccari
Francesco De Caro
Giuliana Crisman
Francesca Sanguedolce
Marcello Filotico
author_facet Alessandro D’Amuri
Matteo Brunelli
Federica Floccari
Francesco De Caro
Giuliana Crisman
Francesca Sanguedolce
Marcello Filotico
author_sort Alessandro D’Amuri
collection DOAJ
description Chordomas are rare malignant tumors of notochordal origin and are rare locally aggressive ones with a metastatic potential. The skin rarely is seen as metastatic site. We describe a case of an adult woman with cutaneous metastasis of a primary sacral chordoma excised ten years before, which appeared as a painless cutaneous mass located in the dorsal region. Once removed, the surgical specimen was formalin fixed and in paraffin embedded. Sections were stained with haematoxylin-eosin, and histochemical and immunohistochemical investigations were performed. Histologically, the neoplasia was characterized by cords or single tumor cells with an abundant myxoid stroma, conspicuous pale vacuolated cytoplasm (the classic “physaliphorous cells”), and mild nuclear atypia. Mitotic activity was scanty. At immunohistochemistry, the tumor cells were diffusely positive for S-100 protein, pan-keratins, EMA, and vimentin. A diagnosis of cutaneous metastasis of chordoma was performed. This case illustrates a diagnostic challenge because of the unusual presentation of an already rare tumor.
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publishDate 2017-01-01
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spelling doaj-art-13fb7ebb270b4b3ca20cf2b10c44edda2025-08-20T02:04:51ZengWileyCase Reports in Pathology2090-67812090-679X2017-01-01201710.1155/2017/52812395281239On a Rare Cutaneous Metastasis from a Sacrococcygeal ChordomaAlessandro D’Amuri0Matteo Brunelli1Federica Floccari2Francesco De Caro3Giuliana Crisman4Francesca Sanguedolce5Marcello Filotico6Anatomic Pathology Unit, Card. G. Panico Hospital, Tricase, ItalyDepartment of Diagnostics and Public Health, Anatomic Pathology, University and Hospital Trust, Verona, ItalyClinic Pathology Unit, Sacro Cuore di Gesù Hospital, Gallipoli, ItalyOrthopaedics and Traumatology Unit, Sacro Cuore di Gesù Hospital, Gallipoli, ItalyPathology Unit, Desenzano del Garda General Hospital, Brescia, ItalyDepartment of Pathology, University and Hospital Trust, Riuniti Hospital, Foggia, ItalyAnatomic Pathology Unit, Card. G. Panico Hospital, Tricase, ItalyChordomas are rare malignant tumors of notochordal origin and are rare locally aggressive ones with a metastatic potential. The skin rarely is seen as metastatic site. We describe a case of an adult woman with cutaneous metastasis of a primary sacral chordoma excised ten years before, which appeared as a painless cutaneous mass located in the dorsal region. Once removed, the surgical specimen was formalin fixed and in paraffin embedded. Sections were stained with haematoxylin-eosin, and histochemical and immunohistochemical investigations were performed. Histologically, the neoplasia was characterized by cords or single tumor cells with an abundant myxoid stroma, conspicuous pale vacuolated cytoplasm (the classic “physaliphorous cells”), and mild nuclear atypia. Mitotic activity was scanty. At immunohistochemistry, the tumor cells were diffusely positive for S-100 protein, pan-keratins, EMA, and vimentin. A diagnosis of cutaneous metastasis of chordoma was performed. This case illustrates a diagnostic challenge because of the unusual presentation of an already rare tumor.http://dx.doi.org/10.1155/2017/5281239
spellingShingle Alessandro D’Amuri
Matteo Brunelli
Federica Floccari
Francesco De Caro
Giuliana Crisman
Francesca Sanguedolce
Marcello Filotico
On a Rare Cutaneous Metastasis from a Sacrococcygeal Chordoma
Case Reports in Pathology
title On a Rare Cutaneous Metastasis from a Sacrococcygeal Chordoma
title_full On a Rare Cutaneous Metastasis from a Sacrococcygeal Chordoma
title_fullStr On a Rare Cutaneous Metastasis from a Sacrococcygeal Chordoma
title_full_unstemmed On a Rare Cutaneous Metastasis from a Sacrococcygeal Chordoma
title_short On a Rare Cutaneous Metastasis from a Sacrococcygeal Chordoma
title_sort on a rare cutaneous metastasis from a sacrococcygeal chordoma
url http://dx.doi.org/10.1155/2017/5281239
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