Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case report

ObjectiveTo report the clinical characteristics of a case of Autosomal recessive woolly hair/ hypotrichosis(ARWH/HT, OMIM:278150/604379) in a child, analyze and identify the causative gene and mutation site. A review of related research at home and abroad was conducted to summarize the current progr...

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Main Authors: Ying Xie, Sha Luo, Yumei Yang, Xin Zou, Shuying Lv, Meijiao Du, Yonglong Xu, Xiaojuan Song, Changjie Qi, Nuo Li, Dingquan Yang
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-07-01
Series:Frontiers in Medicine
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Online Access:https://www.frontiersin.org/articles/10.3389/fmed.2025.1563299/full
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author Ying Xie
Ying Xie
Sha Luo
Yumei Yang
Xin Zou
Shuying Lv
Meijiao Du
Meijiao Du
Yonglong Xu
Yonglong Xu
Xiaojuan Song
Changjie Qi
Nuo Li
Dingquan Yang
author_facet Ying Xie
Ying Xie
Sha Luo
Yumei Yang
Xin Zou
Shuying Lv
Meijiao Du
Meijiao Du
Yonglong Xu
Yonglong Xu
Xiaojuan Song
Changjie Qi
Nuo Li
Dingquan Yang
author_sort Ying Xie
collection DOAJ
description ObjectiveTo report the clinical characteristics of a case of Autosomal recessive woolly hair/ hypotrichosis(ARWH/HT, OMIM:278150/604379) in a child, analyze and identify the causative gene and mutation site. A review of related research at home and abroad was conducted to summarize the current progress in the diagnosis and treatment of ARWH.MethodsClinical data were collected, and exome sequencing was performed on blood samples from the patient and parents to screen for mutations. Sanger sequencing validated suspected pathogenic variants. A summary analysis of previously published woolly hair cases was also conducted.ResultsThe family was found to have mutations in the LIPH gene, with the patient’s sample showing two heterozygous mutations: c.1101del (maternal) and c.736 T > A (paternal). These compound heterozygous mutations are responsible for the ARWH phenotype.ConclusionThe compound heterozygous mutations c.1101del and c.736 T > A in the LIPH gene are the pathogenic mutations causing the clinical phenotype of autosomal recessive woolly hair in the child. The c.1101del mutation is a newly discovered frameshift mutation, enriching the mutation spectrum of LIPH-associated autosomal recessive woolly hair with hypotrichosis.
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institution Kabale University
issn 2296-858X
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publisher Frontiers Media S.A.
record_format Article
series Frontiers in Medicine
spelling doaj-art-12a3354ad71f4e3b80a77376cc3190532025-08-21T12:37:30ZengFrontiers Media S.A.Frontiers in Medicine2296-858X2025-07-011210.3389/fmed.2025.15632991563299Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case reportYing Xie0Ying Xie1Sha Luo2Yumei Yang3Xin Zou4Shuying Lv5Meijiao Du6Meijiao Du7Yonglong Xu8Yonglong Xu9Xiaojuan Song10Changjie Qi11Nuo Li12Dingquan Yang13Beijing University of Chinese Medicine, Beijing, ChinaDepartment of Dermatology, The National Center for the Integration of Traditional Chinese and Western Medicine, China-Japan Friendship Hospital, Beijing, ChinaDepartment of Dermatology, The First Affiliated Hospital of Hunan University of Chinese Medicine, Changsha, ChinaBeijing University of Chinese Medicine, Beijing, ChinaSchool of Senior Translation College, Dalian University of Foreign Languages, Dalian, ChinaCapital Medical University, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaDepartment of Dermatology, The National Center for the Integration of Traditional Chinese and Western Medicine, China-Japan Friendship Hospital, Beijing, ChinaBeijing University of Chinese Medicine, Beijing, ChinaDepartment of Dermatology, The National Center for the Integration of Traditional Chinese and Western Medicine, China-Japan Friendship Hospital, Beijing, ChinaDepartment of Rehabilitation Medicine, The Eighth Medical Center, PLA General Hospital, Beijing, ChinaDepartment of Rehabilitation Medicine, The Eighth Medical Center, PLA General Hospital, Beijing, ChinaDepartment of Dermatology, The National Center for the Integration of Traditional Chinese and Western Medicine, China-Japan Friendship Hospital, Beijing, ChinaDepartment of Dermatology, The National Center for the Integration of Traditional Chinese and Western Medicine, China-Japan Friendship Hospital, Beijing, ChinaObjectiveTo report the clinical characteristics of a case of Autosomal recessive woolly hair/ hypotrichosis(ARWH/HT, OMIM:278150/604379) in a child, analyze and identify the causative gene and mutation site. A review of related research at home and abroad was conducted to summarize the current progress in the diagnosis and treatment of ARWH.MethodsClinical data were collected, and exome sequencing was performed on blood samples from the patient and parents to screen for mutations. Sanger sequencing validated suspected pathogenic variants. A summary analysis of previously published woolly hair cases was also conducted.ResultsThe family was found to have mutations in the LIPH gene, with the patient’s sample showing two heterozygous mutations: c.1101del (maternal) and c.736 T > A (paternal). These compound heterozygous mutations are responsible for the ARWH phenotype.ConclusionThe compound heterozygous mutations c.1101del and c.736 T > A in the LIPH gene are the pathogenic mutations causing the clinical phenotype of autosomal recessive woolly hair in the child. The c.1101del mutation is a newly discovered frameshift mutation, enriching the mutation spectrum of LIPH-associated autosomal recessive woolly hair with hypotrichosis.https://www.frontiersin.org/articles/10.3389/fmed.2025.1563299/fullwoolly hairautosomal recessiveLIPH genemutationcase report
spellingShingle Ying Xie
Ying Xie
Sha Luo
Yumei Yang
Xin Zou
Shuying Lv
Meijiao Du
Meijiao Du
Yonglong Xu
Yonglong Xu
Xiaojuan Song
Changjie Qi
Nuo Li
Dingquan Yang
Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case report
Frontiers in Medicine
woolly hair
autosomal recessive
LIPH gene
mutation
case report
title Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case report
title_full Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case report
title_fullStr Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case report
title_full_unstemmed Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case report
title_short Autosomal recessive woolly hair/hypotrichosis caused by LIPH mutations: a case report
title_sort autosomal recessive woolly hair hypotrichosis caused by liph mutations a case report
topic woolly hair
autosomal recessive
LIPH gene
mutation
case report
url https://www.frontiersin.org/articles/10.3389/fmed.2025.1563299/full
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