Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic Fibrosis
Nephrogenic systemic fibrosis (NSF), previously known as nephrogenic fibrosing dermopathy, is a rare complication of exposure to gadolinium-based contrast agents in patients who have significantly decreased renal function. Manifestations include fibrosis of the skin and other tissues. Effective ther...
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Format: | Article |
Language: | English |
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Wiley
2017-01-01
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Series: | Case Reports in Dermatological Medicine |
Online Access: | http://dx.doi.org/10.1155/2017/3240287 |
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author | Ranran Zhang William Nicholas Rose |
author_facet | Ranran Zhang William Nicholas Rose |
author_sort | Ranran Zhang |
collection | DOAJ |
description | Nephrogenic systemic fibrosis (NSF), previously known as nephrogenic fibrosing dermopathy, is a rare complication of exposure to gadolinium-based contrast agents in patients who have significantly decreased renal function. Manifestations include fibrosis of the skin and other tissues. Effective therapies are lacking. Photopheresis has been tried with variable rates of improvement, and small numbers of cases (20 as of 2016) have been reported of NSF patients treated with photopheresis. We report a case of patient with nephrogenic systemic fibrosis who was treated with photopheresis and demonstrated significant lasting improvements. |
format | Article |
id | doaj-art-1211ba18473d44c9a49d8430ef16f916 |
institution | Kabale University |
issn | 2090-6463 2090-6471 |
language | English |
publishDate | 2017-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Dermatological Medicine |
spelling | doaj-art-1211ba18473d44c9a49d8430ef16f9162025-02-03T01:01:47ZengWileyCase Reports in Dermatological Medicine2090-64632090-64712017-01-01201710.1155/2017/32402873240287Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic FibrosisRanran Zhang0William Nicholas Rose1Department of Pathology and Laboratory Medicine, University of Wisconsin, Madison, WI, USADepartment of Pathology and Laboratory Medicine, University of Wisconsin, Madison, WI, USANephrogenic systemic fibrosis (NSF), previously known as nephrogenic fibrosing dermopathy, is a rare complication of exposure to gadolinium-based contrast agents in patients who have significantly decreased renal function. Manifestations include fibrosis of the skin and other tissues. Effective therapies are lacking. Photopheresis has been tried with variable rates of improvement, and small numbers of cases (20 as of 2016) have been reported of NSF patients treated with photopheresis. We report a case of patient with nephrogenic systemic fibrosis who was treated with photopheresis and demonstrated significant lasting improvements.http://dx.doi.org/10.1155/2017/3240287 |
spellingShingle | Ranran Zhang William Nicholas Rose Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic Fibrosis Case Reports in Dermatological Medicine |
title | Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic Fibrosis |
title_full | Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic Fibrosis |
title_fullStr | Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic Fibrosis |
title_full_unstemmed | Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic Fibrosis |
title_short | Photopheresis Provides Significant Long-Lasting Benefit in Nephrogenic Systemic Fibrosis |
title_sort | photopheresis provides significant long lasting benefit in nephrogenic systemic fibrosis |
url | http://dx.doi.org/10.1155/2017/3240287 |
work_keys_str_mv | AT ranranzhang photopheresisprovidessignificantlonglastingbenefitinnephrogenicsystemicfibrosis AT williamnicholasrose photopheresisprovidessignificantlonglastingbenefitinnephrogenicsystemicfibrosis |