Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.

Imprinting is an epigenetic mechanism that restrains the expression of about 100 genes to one allele depending on its parental origin. Several imprinted genes are implicated in neurodevelopmental brain disorders, such as autism, Angelman, and Prader-Willi syndromes. However, how expression of these...

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Main Authors: Julie Seibt, Olivier Armant, Anne Le Digarcher, Diogo Castro, Vidya Ramesh, Laurent Journot, François Guillemot, Pierre Vanderhaeghen, Tristan Bouschet
Format: Article
Language:English
Published: Public Library of Science (PLoS) 2012-01-01
Series:PLoS ONE
Online Access:https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0048675&type=printable
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author Julie Seibt
Olivier Armant
Anne Le Digarcher
Diogo Castro
Vidya Ramesh
Laurent Journot
François Guillemot
Pierre Vanderhaeghen
Tristan Bouschet
author_facet Julie Seibt
Olivier Armant
Anne Le Digarcher
Diogo Castro
Vidya Ramesh
Laurent Journot
François Guillemot
Pierre Vanderhaeghen
Tristan Bouschet
author_sort Julie Seibt
collection DOAJ
description Imprinting is an epigenetic mechanism that restrains the expression of about 100 genes to one allele depending on its parental origin. Several imprinted genes are implicated in neurodevelopmental brain disorders, such as autism, Angelman, and Prader-Willi syndromes. However, how expression of these imprinted genes is regulated during neural development is poorly understood. Here, using single and double KO animals for the transcription factors Neurogenin2 (Ngn2) and Achaete-scute homolog 1 (Ascl1), we found that the expression of a specific subset of imprinted genes is controlled by these proneural genes. Using in situ hybridization and quantitative PCR, we determined that five imprinted transcripts situated at the Dlk1-Gtl2 locus (Dlk1, Gtl2, Mirg, Rian, Rtl1) are upregulated in the dorsal telencephalon of Ngn2 KO mice. This suggests that Ngn2 influences the expression of the entire Dlk1-Gtl2 locus, independently of the parental origin of the transcripts. Interestingly 14 other imprinted genes situated at other imprinted loci were not affected by the loss of Ngn2. Finally, using Ngn2/Ascl1 double KO mice, we show that the upregulation of genes at the Dlk1-Gtl2 locus in Ngn2 KO animals requires a functional copy of Ascl1. Our data suggest a complex interplay between proneural genes in the developing forebrain that control the level of expression at the imprinted Dlk1-Gtl2 locus (but not of other imprinted genes). This raises the possibility that the transcripts of this selective locus participate in the biological effects of proneural genes in the developing telencephalon.
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spelling doaj-art-11a74fbaaed240cb9bcaebc6c3dae7802025-08-20T02:30:56ZengPublic Library of Science (PLoS)PLoS ONE1932-62032012-01-01711e4867510.1371/journal.pone.0048675Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.Julie SeibtOlivier ArmantAnne Le DigarcherDiogo CastroVidya RameshLaurent JournotFrançois GuillemotPierre VanderhaeghenTristan BouschetImprinting is an epigenetic mechanism that restrains the expression of about 100 genes to one allele depending on its parental origin. Several imprinted genes are implicated in neurodevelopmental brain disorders, such as autism, Angelman, and Prader-Willi syndromes. However, how expression of these imprinted genes is regulated during neural development is poorly understood. Here, using single and double KO animals for the transcription factors Neurogenin2 (Ngn2) and Achaete-scute homolog 1 (Ascl1), we found that the expression of a specific subset of imprinted genes is controlled by these proneural genes. Using in situ hybridization and quantitative PCR, we determined that five imprinted transcripts situated at the Dlk1-Gtl2 locus (Dlk1, Gtl2, Mirg, Rian, Rtl1) are upregulated in the dorsal telencephalon of Ngn2 KO mice. This suggests that Ngn2 influences the expression of the entire Dlk1-Gtl2 locus, independently of the parental origin of the transcripts. Interestingly 14 other imprinted genes situated at other imprinted loci were not affected by the loss of Ngn2. Finally, using Ngn2/Ascl1 double KO mice, we show that the upregulation of genes at the Dlk1-Gtl2 locus in Ngn2 KO animals requires a functional copy of Ascl1. Our data suggest a complex interplay between proneural genes in the developing forebrain that control the level of expression at the imprinted Dlk1-Gtl2 locus (but not of other imprinted genes). This raises the possibility that the transcripts of this selective locus participate in the biological effects of proneural genes in the developing telencephalon.https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0048675&type=printable
spellingShingle Julie Seibt
Olivier Armant
Anne Le Digarcher
Diogo Castro
Vidya Ramesh
Laurent Journot
François Guillemot
Pierre Vanderhaeghen
Tristan Bouschet
Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.
PLoS ONE
title Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.
title_full Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.
title_fullStr Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.
title_full_unstemmed Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.
title_short Expression at the imprinted dlk1-gtl2 locus is regulated by proneural genes in the developing telencephalon.
title_sort expression at the imprinted dlk1 gtl2 locus is regulated by proneural genes in the developing telencephalon
url https://journals.plos.org/plosone/article/file?id=10.1371/journal.pone.0048675&type=printable
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