Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature

Primary Biliary Tract Neuroendocrine tumors (NET) are extremely rare tumors with only 77 cases been reported in the literature till now. We describe a case of a left hepatic duct NET and review the literature for this rare malignancy. To the best of our knowledge the present case is the first report...

Full description

Saved in:
Bibliographic Details
Main Authors: Ajay H. Bhandarwar, Taher A. Shaikh, Ashok D. Borisa, Jaydeep H. Palep, Arun S. Patil, Aditya A. Manke
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Surgery
Online Access:http://dx.doi.org/10.1155/2012/786432
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1850235293366484992
author Ajay H. Bhandarwar
Taher A. Shaikh
Ashok D. Borisa
Jaydeep H. Palep
Arun S. Patil
Aditya A. Manke
author_facet Ajay H. Bhandarwar
Taher A. Shaikh
Ashok D. Borisa
Jaydeep H. Palep
Arun S. Patil
Aditya A. Manke
author_sort Ajay H. Bhandarwar
collection DOAJ
description Primary Biliary Tract Neuroendocrine tumors (NET) are extremely rare tumors with only 77 cases been reported in the literature till now. We describe a case of a left hepatic duct NET and review the literature for this rare malignancy. To the best of our knowledge the present case is the first reported case of a left hepatic duct NET in the literature. In spite of availability of advanced diagnostic tools like Computerized Tomography (CT) Scan and Endoscopic Retrograde Cholangio Pancreaticography (ERCP) a definitive diagnosis of these tumors is possible only after an accurate histopathologic diagnosis of operative specimens with immunohistochemistry and electron microscopy. Though surgical excision remains the gold standard treatment for such tumors, patients with unresectable tumors have good survival with newer biologic agents like Octreotride.
format Article
id doaj-art-0f7e14bdbc2b4a34beb73517f1573ba6
institution OA Journals
issn 2090-6900
2090-6919
language English
publishDate 2012-01-01
publisher Wiley
record_format Article
series Case Reports in Surgery
spelling doaj-art-0f7e14bdbc2b4a34beb73517f1573ba62025-08-20T02:02:19ZengWileyCase Reports in Surgery2090-69002090-69192012-01-01201210.1155/2012/786432786432Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the LiteratureAjay H. Bhandarwar0Taher A. Shaikh1Ashok D. Borisa2Jaydeep H. Palep3Arun S. Patil4Aditya A. Manke5Division of GI and HPP Surgery, Department of Surgery, Grant Medical College & Sir JJ Group of Hospitals, Byculla, Mumbai 400008, IndiaDivision of GI and HPP Surgery, Department of Surgery, Grant Medical College & Sir JJ Group of Hospitals, Byculla, Mumbai 400008, IndiaDivision of GI and HPP Surgery, Department of Surgery, Grant Medical College & Sir JJ Group of Hospitals, Byculla, Mumbai 400008, IndiaDivision of GI and HPP Surgery, Department of Surgery, Grant Medical College & Sir JJ Group of Hospitals, Byculla, Mumbai 400008, IndiaDivision of GI and HPP Surgery, Department of Surgery, Grant Medical College & Sir JJ Group of Hospitals, Byculla, Mumbai 400008, IndiaDivision of GI and HPP Surgery, Department of Surgery, Grant Medical College & Sir JJ Group of Hospitals, Byculla, Mumbai 400008, IndiaPrimary Biliary Tract Neuroendocrine tumors (NET) are extremely rare tumors with only 77 cases been reported in the literature till now. We describe a case of a left hepatic duct NET and review the literature for this rare malignancy. To the best of our knowledge the present case is the first reported case of a left hepatic duct NET in the literature. In spite of availability of advanced diagnostic tools like Computerized Tomography (CT) Scan and Endoscopic Retrograde Cholangio Pancreaticography (ERCP) a definitive diagnosis of these tumors is possible only after an accurate histopathologic diagnosis of operative specimens with immunohistochemistry and electron microscopy. Though surgical excision remains the gold standard treatment for such tumors, patients with unresectable tumors have good survival with newer biologic agents like Octreotride.http://dx.doi.org/10.1155/2012/786432
spellingShingle Ajay H. Bhandarwar
Taher A. Shaikh
Ashok D. Borisa
Jaydeep H. Palep
Arun S. Patil
Aditya A. Manke
Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature
Case Reports in Surgery
title Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature
title_full Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature
title_fullStr Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature
title_full_unstemmed Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature
title_short Primary Neuroendocrine Tumor of the Left Hepatic Duct: A Case Report with Review of the Literature
title_sort primary neuroendocrine tumor of the left hepatic duct a case report with review of the literature
url http://dx.doi.org/10.1155/2012/786432
work_keys_str_mv AT ajayhbhandarwar primaryneuroendocrinetumorofthelefthepaticductacasereportwithreviewoftheliterature
AT taherashaikh primaryneuroendocrinetumorofthelefthepaticductacasereportwithreviewoftheliterature
AT ashokdborisa primaryneuroendocrinetumorofthelefthepaticductacasereportwithreviewoftheliterature
AT jaydeephpalep primaryneuroendocrinetumorofthelefthepaticductacasereportwithreviewoftheliterature
AT arunspatil primaryneuroendocrinetumorofthelefthepaticductacasereportwithreviewoftheliterature
AT adityaamanke primaryneuroendocrinetumorofthelefthepaticductacasereportwithreviewoftheliterature