Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association

Shone’s complex is a rare constellation of multilevel left cardiac obstructive lesions involving both the inflow and outflow. Four primary lesions were included in the initial lesion description. However, other obstruction-causing structural lesions could be infrequently associated. The current repo...

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Main Author: Shaimaa Rakha
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-11-01
Series:Annals of Pediatric Cardiology
Subjects:
Online Access:https://journals.lww.com/10.4103/apc.apc_191_24
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author Shaimaa Rakha
author_facet Shaimaa Rakha
author_sort Shaimaa Rakha
collection DOAJ
description Shone’s complex is a rare constellation of multilevel left cardiac obstructive lesions involving both the inflow and outflow. Four primary lesions were included in the initial lesion description. However, other obstruction-causing structural lesions could be infrequently associated. The current report describes a fetal diagnosis of an unusual association of incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch.
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issn 0974-2069
0974-5149
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publishDate 2024-11-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Annals of Pediatric Cardiology
spelling doaj-art-0aee4efb5cb149d3ab53c4876263f3012025-08-20T02:27:00ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20690974-51492024-11-0117643644010.4103/apc.apc_191_24Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare associationShaimaa RakhaShone’s complex is a rare constellation of multilevel left cardiac obstructive lesions involving both the inflow and outflow. Four primary lesions were included in the initial lesion description. However, other obstruction-causing structural lesions could be infrequently associated. The current report describes a fetal diagnosis of an unusual association of incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch.https://journals.lww.com/10.4103/apc.apc_191_24fetal echocardiographyleft-sided obstructive lesionsparachute-like mitral valvesupramitral ring
spellingShingle Shaimaa Rakha
Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association
Annals of Pediatric Cardiology
fetal echocardiography
left-sided obstructive lesions
parachute-like mitral valve
supramitral ring
title Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association
title_full Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association
title_fullStr Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association
title_full_unstemmed Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association
title_short Incomplete Shone’s complex with cor triatriatum sinister and interrupted aortic arch: Prenatal diagnosis of a rare association
title_sort incomplete shone s complex with cor triatriatum sinister and interrupted aortic arch prenatal diagnosis of a rare association
topic fetal echocardiography
left-sided obstructive lesions
parachute-like mitral valve
supramitral ring
url https://journals.lww.com/10.4103/apc.apc_191_24
work_keys_str_mv AT shaimaarakha incompleteshonescomplexwithcortriatriatumsinisterandinterruptedaorticarchprenataldiagnosisofarareassociation