A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous Manifestations

Posttransfusion purpura is a serious adverse effect of transfusion due to HPA-antibodies. A young female was diagnosed with acute leukaemia, and treatment commenced. Severe thrombocytopenia ensued. No platelet increment was achieved despite transfusions with buffy coat, HLA-compatible, and HPA-1a ne...

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Main Authors: Jagjit Singh Bhamra, Per Ole Iversen, Thomas Kjenner Titze, Geir Erland Tjønnfjord, Çiğdem Akalın Akkök
Format: Article
Language:English
Published: Wiley 2018-01-01
Series:Case Reports in Hematology
Online Access:http://dx.doi.org/10.1155/2018/8187659
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author Jagjit Singh Bhamra
Per Ole Iversen
Thomas Kjenner Titze
Geir Erland Tjønnfjord
Çiğdem Akalın Akkök
author_facet Jagjit Singh Bhamra
Per Ole Iversen
Thomas Kjenner Titze
Geir Erland Tjønnfjord
Çiğdem Akalın Akkök
author_sort Jagjit Singh Bhamra
collection DOAJ
description Posttransfusion purpura is a serious adverse effect of transfusion due to HPA-antibodies. A young female was diagnosed with acute leukaemia, and treatment commenced. Severe thrombocytopenia ensued. No platelet increment was achieved despite transfusions with buffy coat, HLA-compatible, and HPA-1a negative platelets. The workup indicated the presence of anti-HPA-1a. When the diagnosis of posttransfusion purpura was sufficiently substantiated, she had experienced a fatal intracerebral haemorrhage.
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institution Kabale University
issn 2090-6560
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language English
publishDate 2018-01-01
publisher Wiley
record_format Article
series Case Reports in Hematology
spelling doaj-art-08290d78b91a45afbd93d5f75136537f2025-08-20T03:55:32ZengWileyCase Reports in Hematology2090-65602090-65792018-01-01201810.1155/2018/81876598187659A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous ManifestationsJagjit Singh Bhamra0Per Ole Iversen1Thomas Kjenner Titze2Geir Erland Tjønnfjord3Çiğdem Akalın Akkök4Department of Immunology and Transfusion Medicine, Oslo University Hospital, Oslo, NorwayDepartment of Nutrition, Institute of Basic Medical Sciences, University of Oslo, Oslo, NorwayDepartment of Immunology and Transfusion Medicine, Oslo University Hospital, Oslo, NorwayDepartment of Haematology, Oslo University Hospital, Oslo, NorwayDepartment of Immunology and Transfusion Medicine, Oslo University Hospital, Oslo, NorwayPosttransfusion purpura is a serious adverse effect of transfusion due to HPA-antibodies. A young female was diagnosed with acute leukaemia, and treatment commenced. Severe thrombocytopenia ensued. No platelet increment was achieved despite transfusions with buffy coat, HLA-compatible, and HPA-1a negative platelets. The workup indicated the presence of anti-HPA-1a. When the diagnosis of posttransfusion purpura was sufficiently substantiated, she had experienced a fatal intracerebral haemorrhage.http://dx.doi.org/10.1155/2018/8187659
spellingShingle Jagjit Singh Bhamra
Per Ole Iversen
Thomas Kjenner Titze
Geir Erland Tjønnfjord
Çiğdem Akalın Akkök
A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous Manifestations
Case Reports in Hematology
title A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous Manifestations
title_full A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous Manifestations
title_fullStr A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous Manifestations
title_full_unstemmed A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous Manifestations
title_short A Case of Posttransfusion Purpura with Severe Refractory Thrombocytopenia but No Cutaneous Manifestations
title_sort case of posttransfusion purpura with severe refractory thrombocytopenia but no cutaneous manifestations
url http://dx.doi.org/10.1155/2018/8187659
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