A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis
A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right...
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Format: | Article |
Language: | English |
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Wiley
2012-01-01
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Series: | Case Reports in Pulmonology |
Online Access: | http://dx.doi.org/10.1155/2012/371490 |
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author | Ghulam Rehman Mohyuddin Fatima Sultan Ghulam Khaleeq |
author_facet | Ghulam Rehman Mohyuddin Fatima Sultan Ghulam Khaleeq |
author_sort | Ghulam Rehman Mohyuddin |
collection | DOAJ |
description | A 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right upper lobe bronchus and right mainstem bronchus and secondary atelectatic changes. Biopsy was consistent with a diagnosis of lymphomatoid granulomatosis Grade 3. She responded well clinically and radiologically to therapy. Lymphomatoid granulomatosis is a rare EBV-associated disorder which is considered a lymphoproliferative disease. The most common radiographic feature is multiple lung nodules. An isolated hilar mass is an exceptionally rare presentation of this rare disease. |
format | Article |
id | doaj-art-0765e50826cb474880986afd25147366 |
institution | Kabale University |
issn | 2090-6846 2090-6854 |
language | English |
publishDate | 2012-01-01 |
publisher | Wiley |
record_format | Article |
series | Case Reports in Pulmonology |
spelling | doaj-art-0765e50826cb474880986afd251473662025-02-03T05:51:22ZengWileyCase Reports in Pulmonology2090-68462090-68542012-01-01201210.1155/2012/371490371490A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid GranulomatosisGhulam Rehman Mohyuddin0Fatima Sultan1Ghulam Khaleeq2Department of Internal Medicine, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USADepartment of Internal Medicine, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USADivision of Pulmonary and Critical Care, Geisinger Medical Center, 100 North Academy Avenue, Danville, PA 17822, USAA 70-year-old female presented with a 4-week history of dry cough and wheezing. Chest radiograph showed a 10.5 cm mass-like density in the anterior mediastinum which had not been previously visualized. Computed tomography scan (CT) of the chest showed a right hilar mass encasing and narrowing right upper lobe bronchus and right mainstem bronchus and secondary atelectatic changes. Biopsy was consistent with a diagnosis of lymphomatoid granulomatosis Grade 3. She responded well clinically and radiologically to therapy. Lymphomatoid granulomatosis is a rare EBV-associated disorder which is considered a lymphoproliferative disease. The most common radiographic feature is multiple lung nodules. An isolated hilar mass is an exceptionally rare presentation of this rare disease.http://dx.doi.org/10.1155/2012/371490 |
spellingShingle | Ghulam Rehman Mohyuddin Fatima Sultan Ghulam Khaleeq A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis Case Reports in Pulmonology |
title | A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis |
title_full | A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis |
title_fullStr | A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis |
title_full_unstemmed | A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis |
title_short | A Rare Presentation of a Rare Disease: Pulmonary Lymphomatoid Granulomatosis |
title_sort | rare presentation of a rare disease pulmonary lymphomatoid granulomatosis |
url | http://dx.doi.org/10.1155/2012/371490 |
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