Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory Disorders

Treatment of monogenic autoinflammatory disorders, an expanding group of hereditary diseases characterized by apparently unprovoked recurrent episodes of inflammation, without high-titre autoantibodies or antigen-specific T cells, has been revolutionized by the discovery that several of these condit...

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Main Authors: Antonio Vitale, Donato Rigante, Orso Maria Lucherini, Francesco Caso, Isabella Muscari, Flora Magnotti, Maria Giuseppina Brizi, Susanna Guerrini, Maria Patti, Leonardo Punzi, Mauro Galeazzi, Luca Cantarini
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Mediators of Inflammation
Online Access:http://dx.doi.org/10.1155/2013/939847
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author Antonio Vitale
Donato Rigante
Orso Maria Lucherini
Francesco Caso
Isabella Muscari
Flora Magnotti
Maria Giuseppina Brizi
Susanna Guerrini
Maria Patti
Leonardo Punzi
Mauro Galeazzi
Luca Cantarini
author_facet Antonio Vitale
Donato Rigante
Orso Maria Lucherini
Francesco Caso
Isabella Muscari
Flora Magnotti
Maria Giuseppina Brizi
Susanna Guerrini
Maria Patti
Leonardo Punzi
Mauro Galeazzi
Luca Cantarini
author_sort Antonio Vitale
collection DOAJ
description Treatment of monogenic autoinflammatory disorders, an expanding group of hereditary diseases characterized by apparently unprovoked recurrent episodes of inflammation, without high-titre autoantibodies or antigen-specific T cells, has been revolutionized by the discovery that several of these conditions are caused by mutations in proteins involved in the mechanisms of innate immune response, including components of the inflammasome, cytokine receptors, receptor antagonists, and oversecretion of a network of proinflammatory molecules. Aim of this review is to synthesize the current experience and the most recent evidences about the therapeutic approach with biologic drugs in pediatric and adult patients with monogenic autoinflammatory disorders.
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id doaj-art-06b43fea8a5c4944a4e41bf05b646e51
institution OA Journals
issn 0962-9351
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publishDate 2013-01-01
publisher Wiley
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series Mediators of Inflammation
spelling doaj-art-06b43fea8a5c4944a4e41bf05b646e512025-08-20T02:02:48ZengWileyMediators of Inflammation0962-93511466-18612013-01-01201310.1155/2013/939847939847Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory DisordersAntonio Vitale0Donato Rigante1Orso Maria Lucherini2Francesco Caso3Isabella Muscari4Flora Magnotti5Maria Giuseppina Brizi6Susanna Guerrini7Maria Patti8Leonardo Punzi9Mauro Galeazzi10Luca Cantarini11Research Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyInstitute of Pediatrics, Università Cattolica Sacro Cuore, Policlinico A. Gemelli, Largo A. Gemelli 8, 00168 Rome, ItalyResearch Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyRheumatology Unit, Department of Clinical and Experimental Medicine, University of Padova, Via Giustiniani 2, 35128 Padova, ItalyResearch Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyResearch Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyResearch Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyResearch Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyInstitute of Pediatrics, Università Cattolica Sacro Cuore, Policlinico A. Gemelli, Largo A. Gemelli 8, 00168 Rome, ItalyRheumatology Unit, Department of Clinical and Experimental Medicine, University of Padova, Via Giustiniani 2, 35128 Padova, ItalyResearch Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyResearch Center of Systemic Autoimmune and Autoinflammatory Diseases, Rheumatology Unit, Policlinico Le Scotte, University of Siena, Viale Bracci 1, 53100 Siena, ItalyTreatment of monogenic autoinflammatory disorders, an expanding group of hereditary diseases characterized by apparently unprovoked recurrent episodes of inflammation, without high-titre autoantibodies or antigen-specific T cells, has been revolutionized by the discovery that several of these conditions are caused by mutations in proteins involved in the mechanisms of innate immune response, including components of the inflammasome, cytokine receptors, receptor antagonists, and oversecretion of a network of proinflammatory molecules. Aim of this review is to synthesize the current experience and the most recent evidences about the therapeutic approach with biologic drugs in pediatric and adult patients with monogenic autoinflammatory disorders.http://dx.doi.org/10.1155/2013/939847
spellingShingle Antonio Vitale
Donato Rigante
Orso Maria Lucherini
Francesco Caso
Isabella Muscari
Flora Magnotti
Maria Giuseppina Brizi
Susanna Guerrini
Maria Patti
Leonardo Punzi
Mauro Galeazzi
Luca Cantarini
Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory Disorders
Mediators of Inflammation
title Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory Disorders
title_full Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory Disorders
title_fullStr Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory Disorders
title_full_unstemmed Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory Disorders
title_short Biological Treatments: New Weapons in the Management of Monogenic Autoinflammatory Disorders
title_sort biological treatments new weapons in the management of monogenic autoinflammatory disorders
url http://dx.doi.org/10.1155/2013/939847
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