Congenital acute megakaryocytic leukemia

Congenital leukemia (CL) is an extremely rare disorder in the newborn, significant proportion of which is of myeloid origin, primarily of M4 or M5 morphology. As compared to pediatric leukemia, CL is a more aggressive disease. Acute myeloid leukemia (AML-M7) or acute megakaryocytic leukemia is a rar...

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Main Authors: N B Mathur, Neha Joshi, T Singh, Meeta Singh
Format: Article
Language:English
Published: Thieme Medical and Scientific Publishers Pvt. Ltd. 2011-01-01
Series:Indian Journal of Medical and Paediatric Oncology
Subjects:
Online Access:http://www.ijmpo.org/article.asp?issn=0971-5851;year=2011;volume=32;issue=3;spage=165;epage=167;aulast=Mathur
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author N B Mathur
Neha Joshi
T Singh
Meeta Singh
author_facet N B Mathur
Neha Joshi
T Singh
Meeta Singh
author_sort N B Mathur
collection DOAJ
description Congenital leukemia (CL) is an extremely rare disorder in the newborn, significant proportion of which is of myeloid origin, primarily of M4 or M5 morphology. As compared to pediatric leukemia, CL is a more aggressive disease. Acute myeloid leukemia (AML-M7) or acute megakaryocytic leukemia is a rare type of AML with an incidence of 0.5 per million per year. Median age of presentation is 6 years, and children may present with a broad variety of symptoms including low-grade fever, diarrhea, easy bruising, failure to gain weight and life-threatening conditions.
format Article
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institution DOAJ
issn 0971-5851
language English
publishDate 2011-01-01
publisher Thieme Medical and Scientific Publishers Pvt. Ltd.
record_format Article
series Indian Journal of Medical and Paediatric Oncology
spelling doaj-art-06a05dd2d8fe44e3aaf7d1516d8327bc2025-08-20T03:06:12ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Medical and Paediatric Oncology0971-58512011-01-0132316516710.4103/0971-5851.92821Congenital acute megakaryocytic leukemiaN B MathurNeha JoshiT SinghMeeta SinghCongenital leukemia (CL) is an extremely rare disorder in the newborn, significant proportion of which is of myeloid origin, primarily of M4 or M5 morphology. As compared to pediatric leukemia, CL is a more aggressive disease. Acute myeloid leukemia (AML-M7) or acute megakaryocytic leukemia is a rare type of AML with an incidence of 0.5 per million per year. Median age of presentation is 6 years, and children may present with a broad variety of symptoms including low-grade fever, diarrhea, easy bruising, failure to gain weight and life-threatening conditions.http://www.ijmpo.org/article.asp?issn=0971-5851;year=2011;volume=32;issue=3;spage=165;epage=167;aulast=MathurCongenital megakaryocytic leukemianeonatesepsis
spellingShingle N B Mathur
Neha Joshi
T Singh
Meeta Singh
Congenital acute megakaryocytic leukemia
Indian Journal of Medical and Paediatric Oncology
Congenital megakaryocytic leukemia
neonate
sepsis
title Congenital acute megakaryocytic leukemia
title_full Congenital acute megakaryocytic leukemia
title_fullStr Congenital acute megakaryocytic leukemia
title_full_unstemmed Congenital acute megakaryocytic leukemia
title_short Congenital acute megakaryocytic leukemia
title_sort congenital acute megakaryocytic leukemia
topic Congenital megakaryocytic leukemia
neonate
sepsis
url http://www.ijmpo.org/article.asp?issn=0971-5851;year=2011;volume=32;issue=3;spage=165;epage=167;aulast=Mathur
work_keys_str_mv AT nbmathur congenitalacutemegakaryocyticleukemia
AT nehajoshi congenitalacutemegakaryocyticleukemia
AT tsingh congenitalacutemegakaryocyticleukemia
AT meetasingh congenitalacutemegakaryocyticleukemia