Severe generalized edema in a premature neonate: A case report and literature review

Key Clinical Message With no family history, and an atypical phenotype, the clinical diagnosing of Noonan syndrome (NS) can be very difficult. The present case emphasized that generalized edema in neonates may be the potential first symptom of NS. Abstract Severe generalized edema is a rare patholog...

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Main Authors: Haifeng Zong, Yingsui Huang, Ying Xiong, Wentao Gong, Bingchun Lin, Chuanzhong Yang
Format: Article
Language:English
Published: Wiley 2024-09-01
Series:Clinical Case Reports
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Online Access:https://doi.org/10.1002/ccr3.9341
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author Haifeng Zong
Yingsui Huang
Ying Xiong
Wentao Gong
Bingchun Lin
Chuanzhong Yang
author_facet Haifeng Zong
Yingsui Huang
Ying Xiong
Wentao Gong
Bingchun Lin
Chuanzhong Yang
author_sort Haifeng Zong
collection DOAJ
description Key Clinical Message With no family history, and an atypical phenotype, the clinical diagnosing of Noonan syndrome (NS) can be very difficult. The present case emphasized that generalized edema in neonates may be the potential first symptom of NS. Abstract Severe generalized edema is a rare pathological condition with high mortality in newborns, in particular the premature infants. It is characterized by the extensive subcutaneous tissue edema and the accumulation of fluid in neonatal body fluid compartments. The etiology and pathogenesis of hydrops in neonates are quite complex. Generally speaking, hydrops can be divided into immune hydrops and non‐immune hydrops according to the etiology. It is still challenging in treating severe neonatal edema. In this study, we presented a preterm newborn with severe generalized edema after birth, which was finally diagnosed with Noonan syndrome (NS). The infant clinically manifested as severe generalized edema alone, without the involvement of multiple organ malformation. Generalized edema in neonates was probably the first symptom of NS. Therefore, differential diagnosis of NS is necessary for infants developing generalized edema.
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spelling doaj-art-05f89c136d7049caa60a3cf07b9882e82025-08-20T01:59:05ZengWileyClinical Case Reports2050-09042024-09-01129n/an/a10.1002/ccr3.9341Severe generalized edema in a premature neonate: A case report and literature reviewHaifeng Zong0Yingsui Huang1Ying Xiong2Wentao Gong3Bingchun Lin4Chuanzhong Yang5Neonatal Intensive Care Unit Shenzhen Maternity and Child Healthcare Hospital Shenzhen ChinaNeonatal Intensive Care Unit Shenzhen Maternity and Child Healthcare Hospital Shenzhen ChinaNeonatal Intensive Care Unit Shenzhen Maternity and Child Healthcare Hospital Shenzhen ChinaNeonatal Intensive Care Unit Shenzhen Maternity and Child Healthcare Hospital Shenzhen ChinaNeonatal Intensive Care Unit Shenzhen Maternity and Child Healthcare Hospital Shenzhen ChinaNeonatal Intensive Care Unit Shenzhen Maternity and Child Healthcare Hospital Shenzhen ChinaKey Clinical Message With no family history, and an atypical phenotype, the clinical diagnosing of Noonan syndrome (NS) can be very difficult. The present case emphasized that generalized edema in neonates may be the potential first symptom of NS. Abstract Severe generalized edema is a rare pathological condition with high mortality in newborns, in particular the premature infants. It is characterized by the extensive subcutaneous tissue edema and the accumulation of fluid in neonatal body fluid compartments. The etiology and pathogenesis of hydrops in neonates are quite complex. Generally speaking, hydrops can be divided into immune hydrops and non‐immune hydrops according to the etiology. It is still challenging in treating severe neonatal edema. In this study, we presented a preterm newborn with severe generalized edema after birth, which was finally diagnosed with Noonan syndrome (NS). The infant clinically manifested as severe generalized edema alone, without the involvement of multiple organ malformation. Generalized edema in neonates was probably the first symptom of NS. Therefore, differential diagnosis of NS is necessary for infants developing generalized edema.https://doi.org/10.1002/ccr3.9341edemahydropsMAPKnewbornNoonan syndromePTPN11
spellingShingle Haifeng Zong
Yingsui Huang
Ying Xiong
Wentao Gong
Bingchun Lin
Chuanzhong Yang
Severe generalized edema in a premature neonate: A case report and literature review
Clinical Case Reports
edema
hydrops
MAPK
newborn
Noonan syndrome
PTPN11
title Severe generalized edema in a premature neonate: A case report and literature review
title_full Severe generalized edema in a premature neonate: A case report and literature review
title_fullStr Severe generalized edema in a premature neonate: A case report and literature review
title_full_unstemmed Severe generalized edema in a premature neonate: A case report and literature review
title_short Severe generalized edema in a premature neonate: A case report and literature review
title_sort severe generalized edema in a premature neonate a case report and literature review
topic edema
hydrops
MAPK
newborn
Noonan syndrome
PTPN11
url https://doi.org/10.1002/ccr3.9341
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AT yingxiong severegeneralizededemainaprematureneonateacasereportandliteraturereview
AT wentaogong severegeneralizededemainaprematureneonateacasereportandliteraturereview
AT bingchunlin severegeneralizededemainaprematureneonateacasereportandliteraturereview
AT chuanzhongyang severegeneralizededemainaprematureneonateacasereportandliteraturereview