Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)

Hutchinson-Gilford Progeria Syndrome (HGPS) is a rare disease with a combination of short stature, bone abnormalities, premature ageing, and skin changes. Though the physical appearance of these patients is characteristic, there is little emphasis on the characteristic radiological features. In this...

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Main Authors: Haji Mohammed Nazir, Akshiitha Ramesh Baabhu, Yuvaraj Muralidharan, Seena Cheppala Rajan
Format: Article
Language:English
Published: Wiley 2017-01-01
Series:Case Reports in Radiology
Online Access:http://dx.doi.org/10.1155/2017/1305360
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author Haji Mohammed Nazir
Akshiitha Ramesh Baabhu
Yuvaraj Muralidharan
Seena Cheppala Rajan
author_facet Haji Mohammed Nazir
Akshiitha Ramesh Baabhu
Yuvaraj Muralidharan
Seena Cheppala Rajan
author_sort Haji Mohammed Nazir
collection DOAJ
description Hutchinson-Gilford Progeria Syndrome (HGPS) is a rare disease with a combination of short stature, bone abnormalities, premature ageing, and skin changes. Though the physical appearance of these patients is characteristic, there is little emphasis on the characteristic radiological features. In this paper, we report a 16-year-old boy with clinical and radiological features of this rare genetic disorder. He had a characteristic facial appearance with a large head, large eyes, thin nose with beaked tip, small chin, protruding ears, prominent scalp veins, and absence of hair.
format Article
id doaj-art-0559bb3e01dd4ac7a09d7da4df7629f8
institution Kabale University
issn 2090-6862
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language English
publishDate 2017-01-01
publisher Wiley
record_format Article
series Case Reports in Radiology
spelling doaj-art-0559bb3e01dd4ac7a09d7da4df7629f82025-08-20T03:54:25ZengWileyCase Reports in Radiology2090-68622090-68702017-01-01201710.1155/2017/13053601305360Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)Haji Mohammed Nazir0Akshiitha Ramesh Baabhu1Yuvaraj Muralidharan2Seena Cheppala Rajan3Saveetha Medical College and Hospital, Saveetha Nagar, Thandalam, Chennai, Tamil Nadu 602105, IndiaSaveetha Medical College and Hospital, Saveetha Nagar, Thandalam, Chennai, Tamil Nadu 602105, IndiaSaveetha Medical College and Hospital, Saveetha Nagar, Thandalam, Chennai, Tamil Nadu 602105, IndiaSaveetha Medical College and Hospital, Saveetha Nagar, Thandalam, Chennai, Tamil Nadu 602105, IndiaHutchinson-Gilford Progeria Syndrome (HGPS) is a rare disease with a combination of short stature, bone abnormalities, premature ageing, and skin changes. Though the physical appearance of these patients is characteristic, there is little emphasis on the characteristic radiological features. In this paper, we report a 16-year-old boy with clinical and radiological features of this rare genetic disorder. He had a characteristic facial appearance with a large head, large eyes, thin nose with beaked tip, small chin, protruding ears, prominent scalp veins, and absence of hair.http://dx.doi.org/10.1155/2017/1305360
spellingShingle Haji Mohammed Nazir
Akshiitha Ramesh Baabhu
Yuvaraj Muralidharan
Seena Cheppala Rajan
Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)
Case Reports in Radiology
title Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)
title_full Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)
title_fullStr Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)
title_full_unstemmed Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)
title_short Radiological Diagnosis of a Rare Premature Aging Genetic Disorder: Progeria (Hutchinson-Gilford Syndrome)
title_sort radiological diagnosis of a rare premature aging genetic disorder progeria hutchinson gilford syndrome
url http://dx.doi.org/10.1155/2017/1305360
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