Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents
ABSTRACT The development of alloantibodies or autoantibodies is a complication observed in sickle cell disease. Autoimmunization occurs in 7.6-12% of chronically or intermittently transfused patients with sickle cell disease; however, the clinical implications of autoAbs are unclear. Few studies hav...
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| Format: | Article |
| Language: | English |
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Instituto Israelita de Ensino e Pesquisa Albert Einstein
2024-11-01
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| Series: | Einstein (São Paulo) |
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| Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082024000100508&lng=en&tlng=en |
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| _version_ | 1850114967202693120 |
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| author | Vinícius Reis Soares Bruna Paccola Blanco Carla Luana Dinardo Marlene Pereira Garanito |
| author_facet | Vinícius Reis Soares Bruna Paccola Blanco Carla Luana Dinardo Marlene Pereira Garanito |
| author_sort | Vinícius Reis Soares |
| collection | DOAJ |
| description | ABSTRACT The development of alloantibodies or autoantibodies is a complication observed in sickle cell disease. Autoimmunization occurs in 7.6-12% of chronically or intermittently transfused patients with sickle cell disease; however, the clinical implications of autoAbs are unclear. Few studies have focused on pediatric sickle cell disease and autoimmune hemolytic anemia. Herein, we present the coexistence of sickle cell disease and autoimmune hemolytic anemia in two adolescent patients, focusing on their pathophysiology, diagnosis, clinical management, and outcomes. |
| format | Article |
| id | doaj-art-04eb1cdc52584d1c843e6565df1d82e7 |
| institution | OA Journals |
| issn | 2317-6385 |
| language | English |
| publishDate | 2024-11-01 |
| publisher | Instituto Israelita de Ensino e Pesquisa Albert Einstein |
| record_format | Article |
| series | Einstein (São Paulo) |
| spelling | doaj-art-04eb1cdc52584d1c843e6565df1d82e72025-08-20T02:36:42ZengInstituto Israelita de Ensino e Pesquisa Albert EinsteinEinstein (São Paulo)2317-63852024-11-012210.31744/einstein_journal/2024rc1105Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescentsVinícius Reis Soareshttps://orcid.org/0000-0003-2777-3516Bruna Paccola Blancohttps://orcid.org/0000-0001-8587-2868Carla Luana Dinardohttps://orcid.org/0000-0002-0453-7863Marlene Pereira Garanitohttps://orcid.org/0000-0002-9109-9522ABSTRACT The development of alloantibodies or autoantibodies is a complication observed in sickle cell disease. Autoimmunization occurs in 7.6-12% of chronically or intermittently transfused patients with sickle cell disease; however, the clinical implications of autoAbs are unclear. Few studies have focused on pediatric sickle cell disease and autoimmune hemolytic anemia. Herein, we present the coexistence of sickle cell disease and autoimmune hemolytic anemia in two adolescent patients, focusing on their pathophysiology, diagnosis, clinical management, and outcomes.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082024000100508&lng=en&tlng=enAnemia,hemolytic,autoimmuneAdolescentAnemia,sickle cellAutoantibodiesAutoimmunity |
| spellingShingle | Vinícius Reis Soares Bruna Paccola Blanco Carla Luana Dinardo Marlene Pereira Garanito Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents Einstein (São Paulo) Anemia,hemolytic,autoimmune Adolescent Anemia,sickle cell Autoantibodies Autoimmunity |
| title | Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents |
| title_full | Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents |
| title_fullStr | Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents |
| title_full_unstemmed | Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents |
| title_short | Coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents |
| title_sort | coexistent sickle cell anemia and autoimmune hemolytic anemia in two adolescents |
| topic | Anemia,hemolytic,autoimmune Adolescent Anemia,sickle cell Autoantibodies Autoimmunity |
| url | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082024000100508&lng=en&tlng=en |
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