A case of phosphoglyceride crystal deposition disease in the maxilla

Abstract Background Phosphoglyceride crystal deposition disease (PCDD) is a rare disorder in which phosphoglyceride crystals accumulate in soft tissues and bones. It tends to occur years after surgery, trauma, or repeated injections. Case presentation An 81-year-old woman was referred to our departm...

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Main Authors: Emi Saitou, Takaaki Sano, Mai Seki, Takahiro Yamaguchi, Tetsunari Oyama, Satoshi Yokoo
Format: Article
Language:English
Published: BMC 2025-04-01
Series:Diagnostic Pathology
Subjects:
Online Access:https://doi.org/10.1186/s13000-025-01641-2
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author Emi Saitou
Takaaki Sano
Mai Seki
Takahiro Yamaguchi
Tetsunari Oyama
Satoshi Yokoo
author_facet Emi Saitou
Takaaki Sano
Mai Seki
Takahiro Yamaguchi
Tetsunari Oyama
Satoshi Yokoo
author_sort Emi Saitou
collection DOAJ
description Abstract Background Phosphoglyceride crystal deposition disease (PCDD) is a rare disorder in which phosphoglyceride crystals accumulate in soft tissues and bones. It tends to occur years after surgery, trauma, or repeated injections. Case presentation An 81-year-old woman was referred to our department because of swelling of the left maxillary gingiva. The left maxillary second molar had been extracted more than 10 years earlier. Surgical biopsy was performed, and histopathological findings indicated a foreign body granuloma. The patient underwent tumorectomy, during which we found a yellowish tumor. The pathologic findings were the characteristic crystal deposition, fibril-like crystals, and giant cells around the crystals. Gold hydroxamic acid staining revealed positivity for the crystals. The final pathological diagnosis was PCDD. The patient had no further symptoms and no disease recurrence. Conclusions It is relatively easy to diagnose PCDD from the characteristic histopathological findings; however, it may be overlooked by pathologists who are unaware of the disease. T2-weighted magnetic resonance imaging of PCDD in the jawbone has depicted low intensity, a finding that differs from those of ordinary cancers and odontogenic tumors. The oral cavity often undergoes surgical procedures, and PCDD may form, and grow.
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spelling doaj-art-030b61eb1cd0456fa200c23e7c66b5dc2025-08-20T02:24:26ZengBMCDiagnostic Pathology1746-15962025-04-012011810.1186/s13000-025-01641-2A case of phosphoglyceride crystal deposition disease in the maxillaEmi Saitou0Takaaki Sano1Mai Seki2Takahiro Yamaguchi3Tetsunari Oyama4Satoshi Yokoo5Department of Diagnostic Pathology, Gunma University Graduate School of MedicineDepartment of Diagnostic Pathology, Gunma University Graduate School of MedicineDepartment of Diagnostic Pathology, Gunma University Graduate School of MedicineDepartment of Oral and Maxillofacial Surgery, Gunma University HospitalDepartment of Diagnostic Pathology, Gunma University Graduate School of MedicineDepartment of Oral and Maxillofacial Surgery, and Plastic Surgery, Gunma University Graduate School of MedicineAbstract Background Phosphoglyceride crystal deposition disease (PCDD) is a rare disorder in which phosphoglyceride crystals accumulate in soft tissues and bones. It tends to occur years after surgery, trauma, or repeated injections. Case presentation An 81-year-old woman was referred to our department because of swelling of the left maxillary gingiva. The left maxillary second molar had been extracted more than 10 years earlier. Surgical biopsy was performed, and histopathological findings indicated a foreign body granuloma. The patient underwent tumorectomy, during which we found a yellowish tumor. The pathologic findings were the characteristic crystal deposition, fibril-like crystals, and giant cells around the crystals. Gold hydroxamic acid staining revealed positivity for the crystals. The final pathological diagnosis was PCDD. The patient had no further symptoms and no disease recurrence. Conclusions It is relatively easy to diagnose PCDD from the characteristic histopathological findings; however, it may be overlooked by pathologists who are unaware of the disease. T2-weighted magnetic resonance imaging of PCDD in the jawbone has depicted low intensity, a finding that differs from those of ordinary cancers and odontogenic tumors. The oral cavity often undergoes surgical procedures, and PCDD may form, and grow.https://doi.org/10.1186/s13000-025-01641-2Phosphoglyceride crystal deposition diseaseJawboneHistopathologyMRIForeign body granuloma
spellingShingle Emi Saitou
Takaaki Sano
Mai Seki
Takahiro Yamaguchi
Tetsunari Oyama
Satoshi Yokoo
A case of phosphoglyceride crystal deposition disease in the maxilla
Diagnostic Pathology
Phosphoglyceride crystal deposition disease
Jawbone
Histopathology
MRI
Foreign body granuloma
title A case of phosphoglyceride crystal deposition disease in the maxilla
title_full A case of phosphoglyceride crystal deposition disease in the maxilla
title_fullStr A case of phosphoglyceride crystal deposition disease in the maxilla
title_full_unstemmed A case of phosphoglyceride crystal deposition disease in the maxilla
title_short A case of phosphoglyceride crystal deposition disease in the maxilla
title_sort case of phosphoglyceride crystal deposition disease in the maxilla
topic Phosphoglyceride crystal deposition disease
Jawbone
Histopathology
MRI
Foreign body granuloma
url https://doi.org/10.1186/s13000-025-01641-2
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